Pediatric Pulmonary Vascular Disease

Case Report: Selexipag in pediatric pulmonary hypertension: Initiation, transition, and titration

Jenna M. Faircloth, Neelam D. Bhatt, Corey A. Chartan, Ryan D. Coleman, Natalie Villafranco, Fadel E. Ruiz, Raysa Morales-Demori, Elise Whalen, Erin Ely, Rozmeen Fombin, Nidhy P. VargheseTexas Children’s Hospital and Baylor College of Medicine.United States Frontiers in PediatricsFront Pediatr 2023; 11: DOI: 10.3389/fped.2023.1050508 AbstractSelexipag, a selective prostacyclin receptor agonist, is approved for treating pulmonary arterial […]

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Novel use of a Synovis™ coupler device for a surgical lymphovenous anastomosis for the treatment of refractory chylothorax in a patient with central lymphatic flow disorder

Joshua Rezkalla, Majid Husain, Ginger Slack, Sanjay SinhaMayo Clinic. David Geffen School of Medicine at UCLA. University of California Irvine-Children’s Hospital of Orange County.United States Clinical Case ReportsClin Case Rep 2022; 10: DOI: 10.1002/ccr3.5636 AbstractRefractory post-operative chylothorax in congenital heart disease is difficult to treat. We present a case of intractable neonatal chylothorax after cardiac surgery due to central lymphatic

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Thoracoscopic removal of a displaced thoracoamniotic shunt in a newborn with antenatal pleural effusion-a case report

Goby T. W. Sham, Patrick H. Y. Chung, Iris M. C. Chan, W. C. Leung, Kenneth K. Y. WongThe University of Hong Kong. Kwong Wah Hospital.Hong Kong Translational PediatricsTransl Pediatr 2020; 9: 702-706DOI: 10.21037/tp-20-74 AbstractThoracoamniotic shunt has been considered as a treatment for antenatal pleural effusion and complication is rare. In majority of cases, the shunt

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Paediatric acute respiratory distress syndrome: consider the role of lymphatics

Mimi Lu, Elena Cavazzoni, Hiran Selvadurai, Juerg Martin BurrenChildren’s Hospital at Westmead. University of Sydney Discipline of Child and Adolescent Health. Australia British Medical Journal Case ReportsBMJ Case Rep 2022; 15: DOI: 10.1136/bcr-2021-245543 AbstractWe present a case of a 7-day-old male infant with severe respiratory disease requiring venoarterial extracorporeal membrane oxygenation therapy with evidence of lymphangiectasia

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Lymphangiography as a Treatment for Refractory Congenital Chylothorax Due to RASopathies: A Report of Two Cases

Naoya Kinota, Hiroshi Kodama, Taiki Moriyama, Junichi Taniguchi, Mitsunari Maruyama, Atsushi Ogasawara, Yasukazu Kako, Kaoru Kobayashi, Haruyuki Takaki, Akio Shibata, Kyoko Minagawa, Yasuhiro Takeshima, Koichiro YamakadoHyogo College of Medicine. Ashiya Municipal Hospital. Shimane University.Japan Interventional RadiologyInterv Radiol 2022; 7: 17-20DOI: 10.22575/interventionalradiology.2021-0014 AbstractIn this study, we report two cases in which intranodal lymphangiography helped improve congenital chylothorax

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Etilefrine infusion for idiopathic chyle leakage in a critically ill child

Saki Kinoshita, Kazuhiro Shoya, Akihiro Shimotakahara, Hiroshi Hataya, Osamu SaitoTokyo Metropolitan Children’s Medical Center.Japan Pediatrics InternationalPediatr Int 2022; 64: DOI: 10.1111/ped.14850 AbstractAbstract Not Available CategoryPrimary Pulmonary Lymphatic DiseaseSurgical and Catheter-mediated Interventions for Pulmonary Vascular Disease Age Focus: Pediatric Pulmonary Vascular Disease Fresh or Filed Publication: Filed (PHiled). Greater than 1-2 years since publication Article AccessFree PDF

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Sirolimus efficacy in the treatment of critically ill infants with congenital primary chylous effusions

Shreva Agarwal, Berkley Kingman Anderson, Priya Mahajan, Caraciolo J. Fernandes, Judith F. Margolin, Ionela IacobasTexas Children’s Hospital and Baylor College of Medicine.United States Pediatric Blood and CancerPediatr Blood Cancer 2022; 69: DOI: 10.1002/pbc.29510 AbstractBackground: Chylothorax can be a presenting symptom of complex lymphatic anomaly in children and is associated with significant respiratory morbidity. Historically, the traditional pharmacological

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Intranodal lipiodol injection for the treatment of chyle leak in children – a preliminary experience

Amit Gupta, Priyanka Naranje, Zainab Vora, Raju Sharma, Manisha Jana, Ashu Seith Bhalla, Pallavi Sinha, Rohan Malik, Prabudh Goel, Anjan Dhua, Devasenathipathy KandasamyAll India Institute of Medical SciencesIndia British Journal of RadiologyBr J Radiol 2022; 95: DOI: 10.1259/bjr.20211270 AbstractObjective: To assess the effectiveness of intranodal lymphangiography using ethiodised oil (Lipiodol; Guerbet Japan, Tokyo, Japan) for the treatment

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Management of refractory chylothorax in the neonatal intensive care unit: A 22-year experience

Yoshiaki Takahashi, Yoshiaki Kinoshita, Takashi Kobayashi, Yuhki Arai, Toshiyuki Ohyama, Naoki Yokota, Koichi Saito, Yu Sugai, Shoichi TakanoNiigata University Graduate School of Medical and Dental SciencesJapan Pediatric InternationalPediatr Int 2022; 64: DOI: 10.1111/ped.15043 AbstractBackground: The aim was to assess the therapeutic strategy of patients with chylothorax in a neonatal intensive care unit.Methods: Twenty-eight infants with chylothorax were included

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Pathogenic variants in MDFIC cause recessive central conducting lymphatic anomaly with lymphedema

Alicia B. Byrne, Pascal Brouillard, Drew L. Sutton, Jan Kazenwadel, Saba Montazaribarforoushi, Genevieve A. Secker, Anna Oszmiana, Milena Babic, Kelly L. Betterman, Peter J. Brautigan, Melissa White, Sandra G. Piltz, Paul Q. Thomas, Christopher N. Hahn, Matthias Rath, Ute Felbor, G. Christoph Korenke, Christopher L. Smith, Kathleen H. Wood, Sarah E. Sheppard, Denise M. Adams,

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