Pediatric Pulmonary Vascular Disease

Reintervention Is Associated With Improved Survival in Pediatric Patients With Pulmonary Vein Stenosis

Melinda J. Cory, Yinn K. Ooi, Michael S. Kelleman, Robert N. Vincent, Dennis W. Kim, Christopher J. PetitChildren’s Healthcare of Atlanta and Emory University School of Medicine. United States Journal of the American College of Cardiology Cardiovascular InterventionsJACC Cardiovasc Interv 2017; 10: 1788-1798DOI: 10.1016/j.jcin.2017.05.052 AbstractObjectives: The aim of this study was to evaluate survival following catheter intervention […]

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Paucicellular Fibrointimal Proliferation Characterizes Pediatric Pulmonary Vein Stenosis: Clinicopathologic Analysis of 213 Samples From 97 Patients

Alexandra E. Kovach, Philip M. Magcalas, Christina Ireland, Kerry McEnany, Andre M. Oliveira, Mark W. Kieran, Christopher W. Baird, Kathy Jenkins, MD, Sara O. VargasBoston Children’s Hospital. Dana Farber Cancer Institute. Mayo Clinic.United States American Journal of Surgical PathologyAm J Surg Pathol 2017; 41: 1198-1204DOI: 10.1097/PAS.0000000000000892 AbstractPulmonary vein stenosis (PVS) is a luminal narrowing of extrapulmonary

Paucicellular Fibrointimal Proliferation Characterizes Pediatric Pulmonary Vein Stenosis: Clinicopathologic Analysis of 213 Samples From 97 Patients Read More »

Primary Pulmonary Vein Stenosis: Outcomes, Risk Factors, and Severity Score in a Multicentric Study

David Kalfa, Emre Belli, Emile Bacha, Duccio di Carlo, Martin Kostolny, Jukka Salminen, Matej Nosal, Alain Poncelet, Jurgen Horer, Hakan Berggren, Illya Yemets, Mark Hazekamp, Bohdan Maruszewski, George Sarris, Marco Pozzi, Tjark Ebels, Francois Lacour-Gayet for the European Congenital Heart Surgeons AssociationMorgan Stanley Children’s Hospital of New York-Presbyterian and Columbia University Medical Center. Marie Lannelongue

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Unilateral congenital pulmonary lymphangiectasis presenting with pneumothorax and an NRAS variant

Majid Al Teneiji, Marie-Anne Brundler, Mary Noseworthy, Kyle C. KurekAlberta Children’s Hospital and University of Calgary. Canada Pediatric PulmonologyPediatr Pulmonol 2021; 56: 2374-2376DOI: 10.1002/ppul.25401 AbstractNo Abstract Available CategoryPrimary Pulmonary Lymphatic DiseaseGenetic Factors Associated with Pulmonary Vascular DiseasePulmonary Vascular Pathology Age Focus: Pediatric Pulmonary Vascular Disease Fresh or Filed Publication: Filed (PHiled). Greater than 1-2 years since

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A rare case of pulmonary lymphangiectasia associated with CHD

Claudio Henriques, Ana Lai, Helena Andrade, Raquel Pina, Antonio Marinho-da-Silva, Antonio PiresPaediatric Hospital and University Hospital.Portugal Cardiology in the YoungCardiol Young 2022; 32: 132-134DOI: 10.1017/S1047951121002328 AbstractCHD may, at times, occur in the framework of other rare pathologies. These, having similar clinical manifestations, present a diagnostic dilemma for the clinician.The authors present the case of an infant

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[Diffuse pulmonary lymphangiomatosis with pleural and pericardial involvement. Pediatric case report]

Rodolfo P. Moreno, Yanina Hernández, Patricia Garrido, Bethy Camargo Vargas, Alberto Hernández, Javier Faín, Cecilia Seligra, Patricia Topp, Alberto Maffey, Gustavo CardigniSanatorio de la Trinidad Palermo. Argintina Archives of Argentina PediatricsArch Argent Pediatr 2021; 119: e264-e268DOI: 10.5546/aap.2021.e264 AbstractDiffuse pulmonary lymphangiomatosis is a rare disease characterized by marked proliferation and dilation of lymphatic vessels in the lungs,

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Midodrine, an Oral Alpha-1 Adrenoreceptor Agonist, Successfully Treated Refractory Congenital Chylous Pleural Effusion and Ascites in a Neonate

Satoshi Tamaoka, Asami Osada, Takane Kin, Takeshi Arimitsu, Mariko HidaKeio University School of Medicine.Japan ChestChest 2021; 159: e189-e191DOI: 10.1016/j.chest.2020.10.071 AbstractA trisomy 21 neonate presented with congenital chylous pleural effusion and ascites that was refractory to conventional pharmacotherapy. Midodrine, an oral alpha-1-adrenoreceptor agonist, achieved remission of chylous effusion without any adverse effects. To the best of our

Midodrine, an Oral Alpha-1 Adrenoreceptor Agonist, Successfully Treated Refractory Congenital Chylous Pleural Effusion and Ascites in a Neonate Read More »

Non-immune hydrops fetalis secondary to congenital chylothorax with diffuse interstitial lung disease: a diagnostic conundrum

Alvin Jia Hao Ngeow, Mei Yoke Chan, Oon Hoe Teoh, Sarat Kumar Sanamandra, Daisy Kwai Lin ChanSingapore General Hospital. KK Women’s and Children’s Hospital. Singapore British Medical Journals Case ReportsBMJ Case Rep 2021; 14: DOI: 10.1136/bcr-2020-240688 AbstractA Chinese male infant was born at 35 weeks weighing 2935 g to a mother with polyhydramnios and prenatal hydrops

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Recurrent prenatal PIEZO1-related lymphatic dysplasia: Expanding molecular and ultrasound findings

Gioia Mastromoro, Daniele Guadagnolo, Antonella Giancotti, Maria Grazia Di Gregorio, Enrica Marchionni, Flaminia Vena, Francesca Romana Lepri, Lavinia Bargiacchi, Flavia Ventriglia, Cira Di Gioia, Antonio Novelli, Antonio PizzutiSapienza University of Rome. Ospedale San Pietro Fatebenefratelli. Bambino Gesù Children’s Hospital. University of Rome.Italy European Journal of Medical Genetics Eur J Med Genet 2021; 64: DOI: 10.1016/j.ejmg.2020.104106 AbstractGeneralized

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Thoracic Empyema Secondary to Congenital Chylothorax in a 14-Month-Old Boy with Noonan Syndrome

Takeru Oikawa, Chiharu Ota, Shinya Iwasawa, Takehiko Onoki, Hideyuki Ikeda, Takushi HanitaTohoku University Hospital.Japan Case Reports in PediatricsCase Rep Pediatr 2021; DOI: 10.1155/2021/6620353 AbstractThoracic empyema usually occurs as a complication of bacterial pneumonia, but in rare cases, it is caused by hematogenous dissemination secondary to nonpulmonary diseases. Congenital chylothorax or chylothorax in children is associated with

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