Pediatric Pulmonary Vascular Disease

Congenital Chylothorax and Hydrops Fetalis: A Novel Neonatal Presentation of RASA1 Mutation

Alessia Gallipoli, Gillian MacLean, Jagdeep S. Walia, Anupam SehgalQueen’s University.Canada PediatricsPediatrics 2021; 147: DOI: 10.1542/peds.2020-011601 AbstractMutations in the RASA1 gene are known to cause arteriovenous malformations (AVMs), with evidence of associated lymphatic malformations. We report for the first time, to the best of our knowledge, an infant with RASA1 mutation presenting with hydrops fetalis and chylothorax, but without an associated […]

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Chylothorax in the neonate-A stepwise approach algorithm

Gustavo Rocha, Vanessa Arnet, Paulo Soares, Ana Cristina Gomes, Sandra Costa, Paula Guerra, Jorge Casanova, Ines AzevedoCentro Hospitalar Universitário de São João. Universidade do Porto. Portugal Pediatric PulmonologyPediatr Pulmonol 2021; 56: 3093-310DOI: 10.1002/ppul.25601 AbstractBackground: Chylothorax in neonates results from leakage of lymph from thoracic lymphatic ducts and is mainly congenital or posttraumatic. The clinical course of the

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Pulmonary vasodilators can lead to various complications in pulmonary “arterial” hypertension associated with congenital heart disease

Ayako Chida‑Nagai, Koichi Sagawa, Takao Tsujioka, Takanori Fujimoto, Kota Taniguchi, Osamu Sasaki, Gaku Izumi, Hirokuni Yamazawa, Naoki Masaki, Atsushi Manabe, Atsuhito TakedaHokkaido University. Fukuoka Children’s Hospital. Tohoku University Graduate School of Medicine.Japan Heart and VesselsHeart Vessels 2020; 35: 1307-1315DOI: 10.1007/s00380-020-01604-1 AbstractCongenital heart disease-associated pulmonary arterial hypertension (CHD-PAH) is one of the major complications in patients with CHD. A timely closure of the left-to-right shunt will generally result

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A Case of Pulmonary Veno-occlusive Disease Following Hepatic Veno-occlusive Disease After Autologous Hematopoietic Stem Cell Transplantation for Neuroblastoma

Kyohei Isshiki, Karuko Shima, Fumito Yamazaki, Toshiki Takenouchi, Hiroyuki ShimadaKeio University School of MedicineJapan Journal od Pediatric Hematology OncologyJ Pediatr Hematol Oncol 2020; 42(7):e677-e679DOI: 10.1097/MPH.0000000000001566 AbstractPulmonary veno-occlusive disease (PVOD) is an uncommon form of pulmonary hypertension that is usually difficult to diagnose and is refractory to conservative treatment. PVOD can occur in connection with high-dose chemotherapy

A Case of Pulmonary Veno-occlusive Disease Following Hepatic Veno-occlusive Disease After Autologous Hematopoietic Stem Cell Transplantation for Neuroblastoma Read More »

Pulmonary hypertension secondary to pulmonary veno occlusive disease: Catastrophe in the catheterization laboratory

Anuj Sharma, Prashant Raviprakash Bobhate, Tanuja Karande, Ravindra Pawar, Snehal KulkarniKokilaben Dhirubhai Ambani Hospital.India Annals of Pediatric CardiologyAnn Pediatr Cardiol 2020; 13: 377-379DOI: 10.4103/apc.APC_142_20 AbstractNo Abstract Available CategoryClass I. Pulmonary Veno-occlusive Disease and Pulmonary Capillary HemangiomatosisDiagnostic Testing for Pulmonary Vascular Disease. Invasive TestingMedical Therapy. Adverse Effects or Lack of Adverse Effects Age Focus: Pediatric Pulmonary Vascular

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Valved reverse Potts shunt in a case of pulmonary hypertension due to pulmonary veno-occlusive disease

Swati Garekar, Talha Meeran, Shyam Dhake, Dhananjay MalankarFortis Hospital. India Indian Journal of Thoracic and Cardiovascular SurgeryInd J Thorac Cardiovasc Surg 2021; 37: 89-92DOI: 10.1007/s12055-020-00993-2 AbstractIdiopathic pulmonary hypertension has a predictably morbid natural history with an absence of a uniformly successful treatment strategy. We describe our palliative surgical strategy in a symptomatic teenager. A 16-year-old girl,

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Clinical Implications of the Genetic Background in Pediatric Pulmonary Arterial Hypertension: Data from the Spanish REHIPED Registry

Alejandro Cruz-Utrilla1, Natalia Gallego-Zazo, Jair Antonio Tenorio-Castaño, Inmaculada Guillén, Alba Torrent-Vernetta, Amparo Moya-Bonora, Carlos Labrandero, María Elvira Garrido-Lestache Rodríguez-Monte, Alejandro Rodríguez-Ogando, María del Mar Rodríguez Vázquez Del Rey, Juana Espín, Beatriz Plata-Izquierdo, María Álvarez-Fuente, Antonio Moreno-Galdó, Pilar Escribano-Subias, María Jesús Del Cerro MarínHospital Universitario 12 de Octubre. Hospital Universitario La Paz. Instituto de Salud Carlos

Clinical Implications of the Genetic Background in Pediatric Pulmonary Arterial Hypertension: Data from the Spanish REHIPED Registry Read More »

Genetic cause of pulmonary veno-occlusive disease

Kaustubh Mohite, Anil Kumar SapareNarayana Health City.India Lung IndiaLung India 2022; 39: 191-194DOI: 10.4103/lungindia.lungindia_252_21 AbstractPulmonary veno-occlusive disease (PVOD) is an important cause of pulmonary arterial hypertension (PAH) and is classified under idiopathic cause of PAH. Over a period of time, PVOD has been studied in detail in the western countries and various diagnostic criteria are formulated.

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Pediatric pulmonary veno-occlusive disease associated with a novel BMPR2 variant

Wataru Takemori, Kenichiro Yamamura, Yoshitaka Tomita, Naoki Egami, Hazumu Nagata, Hiromitsu Shirouzu, Yuichi Ishikawa, Daisuke Nakajima, Akihiko Yoshizawa, Hiroshi Date, Shouichi OhgaKyushu University. Fukuoka Children’s Hospital. Kyoto University Graduate School of Medicine, Kyoto and Kyoto University Hospital.Japan Pediatric PulmonologyPediatr Pulmonol 2022; 57: 1366-1369DOI: 10.1002/ppul.25877 AbstractPulmonary veno-occlusive disease (PVOD) and idiopathic/heritable pulmonary arterial hypertension (I/HPAH) cause progressive

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Pulmonary veno-occlusive disease after respiratory syncytial virus infection in a post hematopoietic stem cell transplantation patient

Tatsuo Watanabe, Kazutoshi Komori, Shoji Saito, Eriko Uchida1,Takashi Kurata, Masatomo Kitamura, Hikoro Matsui, Kohta Takei, Yoshifumi Ogiso, Keiko Ohta-Ogo, Yozo Nakazawa, Kazuo SakashitaNagano Children’s Hospital. Shinshu University School of Medicine. The University of Tokyo. National Cerebral and Cardiovascular Center.Japan Blood Cell TherapyBlood Cell Ther 2023; DOI: 10.31547/bct-2022-005 AbstractBackground: Pulmonary veno-occlusive disease (PVOD) is a rare but fatal

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