Pediatric Pulmonary Vascular Disease

Hypertrophic Cardiomyopathy as a Key Feature of MRAS-Related Noonan Syndrome: New Case and Comprehensive Literature Review

Romain Martineau, Constance Wells, Florent Fuchs, Sophie Collardeau‐Frachon, Valentin Ruault, Sophie Colomb, Jean‐Michel Faure, Caroline Bartholmot, Marie Vincenti, Benjamin Ganne, Marjolaine WillemsUniversity Hospital of Montpellier and Montpellier University. CESP Center for Research in Epidemiology and Population Health. Hospices Civils de Lyon & Université Claude Bernard. France Prenatal DiagnosisPrenat Diagn 2026; DOI: 10.1002/pd.70134 AbstractNoonan syndrome (NS) is […]

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Case Report: Diffuse pulmonary lymphangiomatosis in a child

Ya-nan Zhang, Zhen Yuan, Jin-chen Du, Bin Liu, Fu Li, Shou-Cai Hu, Qing-Xin Li940th Hospital of Joint Logistics Support Force of Chinese People’s Liberation Army. Gansu University of Traditional Chinese Medicine.China Frontiers in PediatricsFront Pediatr 2026; 13: DOI: 10.3389/fped.2025.1591611 AbstractWe report a rare case of generalized lymphatic anomaly (GLA) in a 12-year-old male, presenting with intermittent

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Common pulmonary vein atresia: a case report and treatment experience sharing of a newborn diagnosed with common pulmonary vein atresia after two operations

Kun Zhang, Shuguang Tao, Wei Gao, Jiangrong Gu, Linlin Wen, Yun FanHebei Children’s Hospital.China Frontiers in PediatricsFront Pediatr 2025; 13:DOI: 10.3389/fped.2025.1590620 AbstractCommon pulmonary vein atresia (CPVA) is a rare congenital heart disease characterized by the absence of functional connectivity between the pulmonary vein and any other heart cavity or systemic venous structure. A 13-h-old newborn (G3P3)

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Outcomes and Patency Following Surgical Repair of Previously Stented Pulmonary Veins in Pediatric Patients

Allison Beckham Davila, Mariana Chavez, Kimberlee Gauvreau, Christina Ireland, Kathy J. Jenkins, Michael Farias, Eric N. Feins, Christopher W. BairdBoston Children’s Hospital and Harvard Medical School. Lurie Children’s Hospital of Chicago and Feinberg School of Medicine.United States Annals of Thoracic SurgeryAnn Thorac Surg 2026; DOI: 10.1016/j.athoracsur.2026.03.056 AbstractBackground: The study objective was to evaluate surgical outcomes of patients

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Does inhaled nitric oxide treatment of pulmonary hypertension in extremely premature infants improve patient outcomes?

Tyler L. King, Patrick J. McNamara, Adrianne R. BischoffUniversity of Iowa.United States Journal of PerinatologyJ Perinatol 2026; DOI: 10.1038/s41372-026-02666-1 AbstractAbstract Not Available CategoryClass III. Pulmonary Hypertension Associated with Lung DiseaseMedical Therapy. Efficacy or Lack of Efficacy Age Focus: Pediatric Pulmonary Vascular Disease Fresh or Filed Publication: Fresh (PHresh). Less than 1-2 years since publication Article Access

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Melatonin effects on the left ventricular function in neonates with persistent pulmonary hypertension

Sarah M. Nofal, Abdel‑Rahman M. El‑Mashad, Asmaa M. Elmesiry, Amany M. Abouelenain, Mostafa M. AwnyTanta University.Egypt European Journal of PediatricsEur J Pediatr 2026; 185: DOI: 10.1007/s00431-026-06864-z AbstractThe aim of this study is to investigate the effects of melatonin on the left ventricular (LV) function in persistent pulmonary hypertension of the newborn (PPHN) and to assess its

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Eccentricity Index Is Associated With Pulmonary Arterial Hypertension in Children After Repair of Complete Atrioventricular Septal Defects

Charles T. Simpkin, Marissa DeLima, Morgan MacBeth, Dale A. Burkett, D. Dunbar Ivy, Benjamin S. FrankUniversity of Colorado Medical Campus and Children’s Hospital Colorado.United States Echocardiography Echocardiography 2026; DOI: 10.1111/echo.70451 AbstractIntroduction: Eccentricity Index is an echocardiographic predictor of disease severity in children with pulmonary arterial hypertension (PAH). Its utility after atrioventricular septal defect (AVSD) repair remains unclear

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Lifesaving Compassionate-Use of Sotatercept in a 12-Year-old With Idiopathic Pulmonary Arterial Hypertension

Weronika Pelczar‐Płachta, Rafał Surmacz, Waldemar BobkowskiPoznan University of Medical Sciences.Poland Pulmonary CirculationPulm Circ 2026; 16DOI: 10.1002/pul2.70293 AbstractPediatric idiopathic pulmonary arterial hypertension (IPAH) refractory to maximal medical therapy is associated with high morbidity and mortality, and therapeutic options remain limited. We describe a 12-year-old girl with end-stage IPAH who developed acute decompensated right heart failure despite triple

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Persistent pulmonary hypertension, neonatal stroke, coagulopathy and multi-organ failure due to severe enterovirus sepsis: two case reports

Arangan Kirubakaran, Kirsty Gray, Thomas Slater, Zoe Cass-Tansey, Amna Alvi, Sundar, Sathiyamurthy, Ujwal Kariholumperial College Healthcare NHS Trust. Hillingdon Hospitals NHS Foundation Trust.United Kingdom BioMedical Central PediatricsBMC Pediatr 2026; DOI: 10.1186/s12887-026-06812-8 AbstractBackground: Disseminated neonatal enteroviral infection is a rare and life-threatening condition with significant multi-organ involvement. It often presents with nonspecific symptoms that may be mistakenly

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Sildenafil for bronchopulmonary dysplasia-associated pulmonary hypertension: A systematic search and narrative synthesis

Yoshinori Katayama, Katsuya Hirata, Yutaka Nishimura, Atsuko, Nakahari, Mami Takeoka, Masahiko Watanabe, Tetsuya Isayama, Japan Evidence Based NeonatologyTakatsuki General Hospital. Osaka Women’s and Children’s Hospital. Hiroshima City Hiroshima Citizens Hospital. Jichi Medical University Saitama Medical Center. Mie University Graduate School of Medicine. National Center for Child Health and Development.Japan Pediatrics InternationalPediatr Int 2026; 68: DOI: 10.1111/ped.70385

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