Pediatric Pulmonary Vascular Disease

Congenital Diaphragmatic Hernia – Is there a sex specific severity phenotype?

Angeo Zarfati, Luca Pio, Arimatias Raitio, Ahmed Abu-Zaid, Khadidja Khadir, Alexandra Benachi, Paul D. LostyUniversité Paris-Saclay, Assistance Publique – Hôpitaux de Paris (AP-HP), Bicêtre Hospital. University of Rome Tor Vergata. Centre de Référence Maladie Rare. University of Turku and Turku University Hospital. Alfaisal University. Antoine Béclère Hospital. University of Liverpool. Ramathibodi Hospital, Mahidol, Mahidol University.France, […]

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Isolated absence of the right pulmonary artery in a neonate: a rare but critical incidental diagnosis

Srashti Kulshrestha, Pratibha RaiManipal Hospital. Banaras Hindu University.India Cardiology in the YoungCardiol Young 2025; DOI: 10.1017/S1047951125110184 AbstractThis case underscores an uncommon presentation of pulmonary artery hypertension which, to our knowledge, has limited neonatal data. Its atypical course reveals diagnostic pitfalls that, if unrecognized, may delay effective therapy. This report highlights options for early recognition and management. It serves

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Marked improvement in severe pulmonary arterial hypertension following airway infection in a patient with a heterozygous BMP9 nonsense mutation: a case report

Makito Sakurai, Yohei Yamaguchi, Kei Takasawa, Susumu Hosokawa, Taku IshiiInstitute of Science Tokyo. Japanese Red Cross Musashino Hospital.Japan European Heart Journal Case ReportsEur Heart J Case Rep 2025; 9: DOI: 10.1093/ehjcr/ytaf386 AbstractBackground: Pulmonary arterial hypertension (PAH) is a severe and life-threatening disease. Genetic factors, inflammation and immune system play important roles in their pathogenesis. However, their precise

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Pectus excavatum repair during lung transplantation in a 5-year-old: A case report

Marisa E. Schwab, Elisabeth Martin, Xin Si, Stephanie D. ChaoLucile Packard Children’s Hospital, Stanford University School of Medicine.United States Interdisciplinary Cardiovascular and Thoracic SurgeryInterdiscip Cardiovasc Thorac Surg 2025; DOI: 10.1093/icvts/ivaf263 AbstractChest wall deformities are considered a risk factor for lung transplantation. A 5-year-old girl with protein surfactant C deficiency, interstitial lung disease, pulmonary hypertension, pectus excavatum

Pectus excavatum repair during lung transplantation in a 5-year-old: A case report Read More »

Early Echocardiographic Indicators of Pulmonary Vascular Disease in Preterm Infants at Risk for Bronchopulmonary Dysplasia

Valentina Gava Chakr, Rita C. Silveira, Livia da Rosa Pauletto, Stelamaris Luchese, Patricia Martins Moura Barrios, Vanessa Bustamente Estrada, Carolina Real Cappallaro, Maria Eduarda de Freitas Horn, Renato S. ProcianoyUniversidade Federal do Rio Grande do Sul and Hospital de Clínicas de Porto Alegre. Brazil Pediatric CardiologyPediatr Cardiol 2025; DOI: 10.1007/s00246-025-04079-x AbstractPremature infants, particularly those with bronchopulmonary

Early Echocardiographic Indicators of Pulmonary Vascular Disease in Preterm Infants at Risk for Bronchopulmonary Dysplasia Read More »

Phenoxybenzamine: Old Wine in a Bright New Bottle-Taming the wild side of Phenoxybenzamine

R. Benedict Raj, Srinath Reddy Narahari, Vasudev Vemala, Jyotiprakash ReddyAster Ramesh Hospitals.India Journal of Pharmacy and BioAllied SciencesJ Pharm Bioall Sci 2025; 17 (Suppl 3): S2135-S2137DOI: 10.4103/jpbs.jpbs_868_25 AbstractBackground: Phenoxybenzamine (PBZ), a long-acting α-blocker, was once widely used in pediatric cardiac surgeries but fell out of favor due to concerns about systemic hypotension. In the context of developing

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Treatment options for children with pulmonary arterial hypertension associated with congenital heart disease

Julie Wacker, Raphael Joye, Maurice BeghettiGeneva University Hospitals.Switzerland Expert Review of Respiratory MedicineExpert Rev Respir Med 2025; DOI: 10.1080/17476348.2025.2581340 AbstractIntroduction: Pulmonary hypertension associated with congenital heart disease (PAH-CHD) represents one of the leading causes of pediatric pulmonary hypertension. Within this entity, patients can be classified into distinct subgroups, each characterized by specific clinical features, pathophysiological mechanisms, and

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Persistent Pulmonary Hypertension of the Newborn: A Pragmatic Review of Pathophysiology, Diagnosis, and Advances in Management

Karolina Chojnacka, Yogen Singh, Sheen Gahlaut, Witold Blaz, Agata Jerzak, Tomasz SzczapaPoznan University of Medical Sciences. University of California and UC Davis Children’s Hospital. Oxford University. Saint Jadwiga the Queen Clinical Provincial Hospital and University of Rzeszow.Poland, United States and United Kingdom BiomedicinesBiomedicines 2025; 13: DOI: 10.3390/biomedicines13102332 AbstractPersistent pulmonary hypertension of the newborn (PPHN) results from

Persistent Pulmonary Hypertension of the Newborn: A Pragmatic Review of Pathophysiology, Diagnosis, and Advances in Management Read More »

Abnormal Fetal/Neonatal Lung Development Manifested as Some Functional Heart Abnormalities During the Third Trimester of Fetal Life

Julia Murlewska, Oskar Sylwestrzak, Maciej Słodki, Iwona Strzelecka, Łukasz Sokołowski, Monika Wójtowicz-Marzec, Iwona Maroszynska, Ewa Cichos, Hanna Romanowicz, Anita J. Moon-Grady, Maria Respondek-LiberskaPolish Mother’s Memorial Hospital Research Institute. Mazovian Academy in Plock. Medical University of Lodz. Medical University of Lublin. Benioff Children’s Hospital and University of California, San Francisco.Poland and United States BiomedicinesBiomedicines 2025; 13:

Abnormal Fetal/Neonatal Lung Development Manifested as Some Functional Heart Abnormalities During the Third Trimester of Fetal Life Read More »

Novel Pulmonary Manifestations in Pediatric Late-Onset Congenital Central Hypoventilation Syndrome: A Case Series of PHOX2B-Associated Pulmonary Hypertension and Pulmonary Alveolar Hemorrhage

Yuhong Guan, Xiaohui Wen, Xiaoyan Zhang, zhifei Xu, Shunying Zhao, Haiming YangBeijing Children’s Hospital, Capital Medical University and National Center for Children’s Health.China Pediatric PulmonologyPediatr Pulmonol 2025; 60: DOI: 10.1002/ppul.71347 AbstractAnstract Not Available CategoryClass III. Pulmonary Hypertension Associated with Airway Disease, Apnea or HypoventilationSymptoms and Findings Associated with Pulmonary Vascular Disease Age Focus: Pediatric Pulmonary Vascular

Novel Pulmonary Manifestations in Pediatric Late-Onset Congenital Central Hypoventilation Syndrome: A Case Series of PHOX2B-Associated Pulmonary Hypertension and Pulmonary Alveolar Hemorrhage Read More »

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