Pediatric Pulmonary Vascular Disease or Adult Pulmonary Vascular Disease

Pulmonary Hypertension and Lung Transplantation

Sophie Kruszona, Khalil Aburahma, Nunzio Davide de Manna, Dmitry Bobylev, Arjang Ruhparwar, Christian Kuehn, Jawad Salman, Fabio IusHannover Medical School.Germany Zentralblatt für ChirurgieZentralbl Chir 2025; DOI: 10.1055/a-2590-2620 AbstractPulmonary artery hypertension (PAH), a subtype of pulmonary hypertension, is a rare end-stage lung disease. Bilateral lung and combined heart and lung transplantation have long been considered as a gold standard therapy for PAH. This manuscript […]

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ThoroughFare atrial pressure controller device to create a controlled interatrial right-to-left shunt in advanced pulmonary arterial hypertension – A pilot study

Bojja Venkata Satya Roopesh, Girija Haritha, S. V. Kishore, Muthukumaran Chinnasamy Sivaprakasam, Shreesha Maiya, Saileela Rajan, Pramod Sagar, Kothandam SivakumarMadras Medical Mission. Apollo Children’s Hospital. Narayana Health. MIOT HospitalIndia Annals of Pediatric CardiologyAnn Pediatr Cardiol 2024; 17: 408-414DOI: 10.4103/apc.apc_209_24 AbstractBackground: Atrial flow regulators are used in patients with pulmonary arterial hypertension (PAH) who present with syncope or

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Role of phosphodiesterase-3 inhibitor in cardiorespiratory fitness and functional class of patients with pulmonary hypertension: A randomized, double-blind, placebo-controlled trial

Sefri N. Sofia, Udin Bahrudin, Ilham Uddin, Muhammad A. Sobirin, Erna Setiawati, Galuh Hardaningsih, Kevin C. Tjandra, Edward K. S. LimijadiUniversitas Diponegoro. Dr. Kariadi Hospital. Indonesia Narra JNarra J 2025; 5: DOI: 10.52225/narra.v5i1.1301 AbstractMany patients with acyanotic shunt congenital heart disease (CHD) are diagnosed only in adulthood, by which time pulmonary hypertension (PH) has developed, impairing

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Is Pulmonary Embolism a Chronic Disease?

Gerard Gurumurthy, Lianna Reynolds, Kirsten de Wit, Lara N. Roberts, Jecko ThachilUniversity of Manchester. Royal Manchester Children’s Hospital. Queen’s University. McMaster University. King’s College Hospital NHS. United Kingdom and Canada Clinical Medicine JournalClin Med 2025;DOI: 10.1016/j.clinme.2025.100325 AbstractPulmonary embolism (PE) is often regarded as an acute disorder, yet emerging evidence underscores its chronic trajectory. Many survivors endure

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The clinical and genetic features of hereditary haemorrhagic telangiectasia (HHT) in central South Africa-three novel pathogenic variants

Tendaishe T. Mutize, Riaz Y. Seedat, Johannes K. Ploos van Amstel, Johannes J. Mager, Stephen C. Brown, Fekade Gebremariam, Marius J. CoetzeeUniversity of the Free State nd Universitas Academic Hospital. Utrecht University. Shelly Beach Hospital. National Health Laboratory Service.South Africa and Netherlands Molecular Biology ReportsMol Biol Rep 2020; 47: 9967-9972DOI: 10.1007/s11033-020-05985-4 AbstractHereditary haemorrhagic telangiectasia (HHT) is

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Pulmonary arteriole narrowing in end-stage cystic fibrosis lungs occurs with and without small airway disease

Astrid Vermaut, Gitte Aerts, Lynn Willems, Vincent Geudens, Charlotte Hooft, Pieterjan Kerckhof, Lise Vanvuchelen, Marta Zapata-Ortega, Hanne Beeckmans, Xin Jin, Yousry Mohamady, Jan Van Slambrouck, Lucia Aversa, Janne Verhaegen, Emanuela E. Cortesi, Charlotte De Fays, Birgit Weynand,Dirk E. Van Raemdonck, Laurens J. Ceulemans, Wim A. Wuyts, Marianne Carlon, Robin Vos, Natalie Lorent, Ghislaine Gayan-Ramirez, Laurent

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Pulmonary Complications in Patients With Fontan Circulation: JACC Review Topic of the Week

Ali Abdulkarim, Shawn Shaji, Mahmud Elfituri, Megan Gunsaulus, Muhammad A. Zafar, Ali N. Zaidi, Robert H. Pass, Brian Feingold, Geoffrey Kurland, Jacqueline Kreutzer, Rod Ghassemzadeh, Bryan Goldstein, Shawn West, Tarek AlsaiedIcahn School of Medicine at Mount Sinai. University of Pittsburgh Medical Center, Children’s Hospital of Pittsburgh and University of Pittsburgh School of Medicine. University of

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Pulmonary vein stenosis: future optimism

Patcharapong Suntharos, Marin Satawiriya, Lourdes R. PrietoCleveland Clinic Children’s Hospital. Ramathibodi Hospital, Mahidol University. Nicklaus Children’s Hospital.United States and Thailand Current Opinion in CardiologyCurr Opin Cardiol 2025; DOI: 10.1097/HCO.0000000000001217 AbstractPurpose of review: Pulmonary vein stenosis (PVS) is a rare disease with high morbidity and mortality. Prevention of restenosis remains challenging. This review will highlight recent advances in

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The Challenge in Burden of Pulmonary Arterial Hypertension: A Perspective From the Global Burden of Disease Study

Yicheng Yang, Zhiwei Zeng, Qiaoxi Yang, Huan Wang, Hanwen Zhang, Wenjie Yan, Peizhi Wang, Chuangshi Wang, Zhanhao Su, Pugazhenthan Thangaraju, Sher Zaman Safi, Beilan Yang, Yaoyao Wang, Jingjing Zhou, Zhiyong Zou, Yuan Huang, Songren Shu, Changming XiongFuwai Hospital, National Center for Cardiovascular Diseases, Chinese Academy of Medical Sciences and Peking Union Medical College. Anzhen Hospital

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GATA2 Deficiency With Early-Onset and Progressive Interstitial Lung Disease

Yuriko Sugiura, Takahiro Ando, Hirokazu Urushiyama, Akihisa Mitani, Goh Tanaka, Kenichi Kashimada, Tomohiro Morio, Hidenori KageUniversity of Tokyo. Institute of Science Tokyo.Japan Respirology Case ReportsRespirol Case Rep 2025; 13: DOI: 10.1002/rcr2.70165 AbstractGATA2 deficiency is a rare disease caused by germline heterozygous variants. This mutation is known to cause a decrease in haematopoietic stem cells and a

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