Pediatric Pulmonary Vascular Disease or Adult Pulmonary Vascular Disease

Registry-based estimation of cardiac event-free survival in congenital heart disease complicated by pulmonary hypertension: A nationwide registry study from Japan

Taku Ishii, Tatsuhiko Anzai, Keiko Uchida, Susumu Hosokawa, Naofumi F. Sumitomo, Hidekazu Ishida, Keiichi Hirono, Jun Muneuchi, Ayako Chida-Nagai, Ryo Inuzuka, Hirofumi Sawada, Sayo Suzuki, Jun Maeda, Hisaaki Aoki, Lisheng Lin, Takashi Murakami, Yusuke Nakano, Tatsuya Onishi, Takuya Wakamiya, Kei Inai, Shinichi Takatsuki, Atsushi Yao, Shigetoyo Kogaki, Hiroyuki Fukushima, Yuichi Tamura, Kunihiko Takahashi, Hiroyuki Yamagishi, […]

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Surgical repair of extremely late presentation of supracardiac total anomalous pulmonary vein connection: a case series

Dicky Fakhri, Salomo Purba, Indriwanto Sakdijan, Ardiansyah, Aditya Agam NugrahaNational Cardiovascular Center Harapan Kita.Indonesia Journal of Cardiothoracic SurgeryJ Cardiothorac Surg 2026; DOI: 10.1186/s13019-026-04046-4 AbstractBackground: A late-presenting total anomalous pulmonary venous connection is extremely rare, and surgical repair remains a significant challenge.Cases presentation: We present two cases of surgical repair for late-presenting supracardiac total anomalous pulmonary vein connection: a

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Evolving Concepts in Pulmonary Hypertension: Implementation challenges of the current guidelines and proceedings in the US

Sandeep Sahay, Rodolfo A. Estrada, Megan Griffiths, Naomi Habib, Sandhya Murthy, Steven D. Nathan, Rachel T. Sullivan, James R. Klinger, Raymond BenzaHouston Methodist Hospital. UT Health San Antonio. Children’s Medical Center Dallas and University of Texas Southwestern. Norton Thoracic Institute. Montefiore-Einstein Heart Center. Inova Fairfax Hospital. Monroe Carell Jr. Children’s Hospital and Vanderbilt University. Rhode

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The relationship between pulmonary hypertension and graft vascular resistance and rejection in liver transplant patients

Burak Yagdiran, Batuhan Kirisci, Nedim Cekmen, Ahmed Uslu, Mehmet HaberalBaskent University Medical Center. Turkey BioMedical Central Pulmonary MedicineBMC Pulm Med 2026; DOI: 10.1186/s12890-026-04351-7 AbstractPurpose: Pulmonary hypertension (PH) is associated with systemic hemodynamic changes that may influence graft perfusion following liver transplantation (LT). In this study, we aimed to evaluate whether pre-transplant PH risk, as estimated by transthoracic

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Variation in SNX29 and Acute Vasodilator Response in Pulmonary Arterial Hypertension

Jason H. Karnes, Changlei Bao, Shuxin Liang, Timothy Thayer, John Zagorski, Samisubbu R. Naidu, James D. West, Rae-Hwi Schwantes-An, Ehsan Khajouei, Kasturi Banerjee, Hemant K. Tiwari, Juvie Farol, Kiana L. Martinez, Dingyuan Liu, Yao Ning, Yanan Sun, Yangfan Jia, Jian Wang, Amit Arora, Ken Batai, Stephen J. Halliday, Katie Lutz, Anna Walsworth, Andrea L. Frump,

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Sickle cell disease-associated pulmonary hypertension: an integrated framework linking pathologies, mechanisms, and clinical phenotypes

Florence Vallelian, Dominik J. Schaer, Benoit Lechartier, Paul W. Buehler, David C. IrwinUniversity of Zurich. Lausanne University Hospital and University of Lausanne. University of Maryland. Anschutz Medical Campus School of Medicine and University of Colorado. Switzerland and United States eBioMedicineeBioMedicine 2026; DOI: 10.1016/j.ebiom.2026.106288 AbstractSickle cell disease-associated pulmonary hypertension (SCD-PH) affects approximately 10% of adults with SCD

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Advances in the pathogenesis and clinical management of pulmonary hypertension

Yi Yan, Zhuoyuan Xu, Yanghanyue Zhou, Xike Wang, Hao ZhangShanghai Children’s Medical Center, National Children’s Medical Center and Shanghai Jiao Tong University School of Medicine. Guizhou Branch of Shanghai Children’s Medical Center and Guizhou Provincial People’s Hospital.China Medical ReviewMed Rev 2026; 6: 120-141DOI: 10.1515/mr-2026-0002 AbstractPulmonary hypertension (PH) is a severe cardiopulmonary disorder characterized by pulmonary vascular

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Pathogenesis, Evaluation, and Management of Pulmonary Vein Stenosis: JACC Review Topic of the Week

Trevor Simard, Dhruv Sarma, William R. Miranda, Charles Jain, Jason H. Anderson, Jeremy D. Collins, Abdallah El Sabbagh, Aravdeep Jhand, Tobias Peikert, Guy S. Reeder, Thomas M. Munger, Douglas L. Packer, David R. HolmesMayo Clinic.United States Journal of the American College of CardiologyJ Am Coll Cardiol 2023; 81: 2361-2373DOI: 10.1016/j.jacc.2023.04.016 AbstractPulmonary vein stenosis (PVS) can arise

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Clinical Presentations, Comorbidities, and Diagnostic Approaches in Sinus Venosus Atrial Septal Defect: A Literature Review

Dima Bsat, Dalia Safi, Jad Abdul Khalek, Issam El Rassi, Mariam ArabiAmerican University of Beirut Medical Center. Al Jalila Children’s Hospital.Lebanon and United Arab Emirates Cardiology in ReviewCardiol Rev 2026; DOI: 10.1097/CRD.0000000000001284 AbstractSinus venosus atrial septal defect is a rare congenital heart defect that is frequently associated with partial anomalous pulmonary venous return (PAPVR). This defect

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The Right Ventricle, the Forgotten Chamber or Not

Ranjini Srinivasan, Alessandro Castiglione, Michael Antonchak, Ellen OstenfeldWeill Cornell School of Medicine. Lund University and Skåne University Hospital. New York University Grossman School of Medicine.United States and Sweden Magnetic Resonance Imaging Clinics of North AmericaMagn Reson Imaging Clin N Am 2026; 34: 217-230DOI: 10.1016/j.mric.2026.01.011 AbstractRight ventricular (RV) enlargement or dysfunction evaluation is the cornerstone for diagnosis, prognostications, and treatment planning in a variety

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