Pediatric Pulmonary Vascular Disease or Adult Pulmonary Vascular Disease

Bullous Lung Disease in Turner Syndrome: An Underrecognized Comorbidity?

Stevin Lu, Lois J. Starr, Rachel A. Taylor, Anji T. YetmanCreighton Medical School. University of Nebraska Medical Center.United States American Journal of Medical Genetics Part AAm J Med Genet A 2024; DOI: 10.1002/ajmg.a.63908 AbstractCongenital pulmonary anomalies in Turner syndrome (TS) are rarely reported. Herein, we describe a female with TS who presented with emphysema in infancy […]

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Late-Onset Noninfectious Pulmonary Complications after Hematopoietic Stem Cell Transplantation

AndrewC. Harris, Kimia Ganjaei, Camila Vilela, Alexander GeyerMemorial Sloan Kettering Cancer Center. Lenox Hill Hospital and Northwell Health. United States Transplantation and Cellular TherapyTransplant Cell Ther 2024; 30: DOI: 10.1016/j.jtct.2024.05.022 AbstractAbstract Not Available CategoryClass V. Pulmonary Hypertension Associated with Hematological, Systemic, Metabolic and Other DisordersReview Articles Concerning Pulmonary Vascular Disease Age Focus: Pediatric Pulmonary Vascular Disease

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Whole-exome sequencing reveals the genetic causes and modifiers of moyamoya syndrome

Akikazu Nakamura, Shunsuke Nomura, Shoko Hara, Thiparpa Thamamongood, Taketoshi Maehara, Tadashi Nariai, Shasha Khairullah, Kay Sin Tan, Kenko Azuma, Ayako Chida‐Nagai, Yoshiyuki Furutani, Takahiro Hori, Koji Yamaguchi, Takakazu Kawamata, Constantin Roder, Hiroyuki AkagawaTokyo Women’s Medical University and Adachi Medical Center. University of Toronto. Tokyo Medical and Dental University. University of Malaya. Hokkaido University Hospital. Eberhard

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The role of immune cells in the pathogenesis of connective tissue diseases-associated pulmonary arterial hypertension

Zhe Li, Juan Ma, Xuejing Wang, Liquan Zhu, Yu Gan, Baoquan DaiWeifang Maternal and Child Health Hospital. Shandong Second Medical University.China Frontiers in ImmunologyFront Immunol 2024; 15: DOI: 10.3389/fimmu.2024.1464762 AbstractConnective tissue diseases-related pulmonary arterial hypertension (CTD-PAH) is a disease characterized by an elevated pulmonary artery pressure that arises as a complication of connective tissue diseases. The

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Utility of factor D and other alternative complement factors as biomarkers in systemic sclerosis-associated pulmonary arterial hypertension (SSc-PAH)

Eva Petrow, Changyong Feng, Ashley Frazer-Abel, Roberta Goncalves Marangoni, Katie Lutz, William C. Nichols, V. Michael Holers, Christopher Ritchlin, R. James White III, Benjamin D. KormanUniversity of Rochester Medical Center. University of Colorado School of Medicine. Cincinnati Children’s Medical Center and University of Cincinnati College of Medicine. United States Seminars in Arthritis and RheumatismSemin Arthritis

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A survey of cystic fibrosis physicians’ views on lung transplant referral in the era of elexacaftor/tezacaftor/ivacaftor

Nora Burdis, Tijana Milinic, Lauren E. Bartlett, Louisa Goss, Erin Tallarico, Abigail Boyle, Abigail Thaxton, Grant A. Turner, Luke J. Benvenuto, Albert Faro, Christopher H. Goss, Siddhartha G. Kapnadak, Kathleen J. RamosUniversity of Washington and Seattle Children’s Research Institute. Cystic Fibrosis Foundation. University of California at Los Angeles. Columbia University. United States Pediatric PulmonologyPediatr Pulmonol

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Inhibition of DLL4/Notch Signaling Pathway Promotes M2 Polarization and Cell Proliferation in Pulmonary Arterial Hypertension

Guangxing Tan, Chenxia Juan, Yan Mao, Gang Xue, Zhuyuan FangJiangsu Province Hospital of Chinese Medicine, Wuxi Hospital of Traditional Chinese Medicine and Affiliated Hospital of Nanjing University of Chinese Medicine. Yangzhou Hospital of Traditional Chinese Medicine. China American Chemical Society OmegaACS Omega 2024; 9: 37923-37933DOI: 10.1021/acsomega.4c04307 AbstractIn this study, we conducted a comprehensive analysis to identify

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Long-term outcomes of transcatheter atrial septal defect closure: a single-center retrospective study

Lalita Honghiranrueng, Supaporn Roymanee, Kanjarut Wongwaitaweewong, Jirayut Jarutach, Rujira BuntharikpornpunQueen Sirikit National Institute of Child Health. Prince of Songkla University.Thailand Frontiers in Cardiovascular MedicineFront Cardiovasc Med 2024; 11: DOI: 10.3389/fcvm.2024.1448967 AbstractBackground: Transcatheter atrial septal defect (ASD) closure is the primary approach for treating ASD secundum; however, data on long-term outcomes remain limited. This study aimed to elucidate

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Circulating Endothelin 1 but Not Transforming Growth Factor-β Levels Are Reduced after Pulmonary Endarterectomy in Subjects Affected by Chronic Thromboembolic Pulmonary Hypertension: A Prospective Cohort Study

Pasquale Totaro, Claudio Tirelli, Lucia Sacchi, Annalisa De Silvestri, Mara DeAmici, Fabrizio Grosjean, Giorgia Testa, Alessia Alloni, Eraldo Kushta, Riccardo Albertini, Teresa Rampino, Andrea Maria D’ArminiFoundation I.R.C.C.S. Policlinico San Matteo. University of Milan. University of Pavia. Italy Journal of Clinical MedicineJ Clin Med 2024; DOI: 10.3390/jcm13174977 AbstractBackground and objectives: Endothelin-1 (ET-1) and transforming growth factor-β (TGF-β) play

Circulating Endothelin 1 but Not Transforming Growth Factor-β Levels Are Reduced after Pulmonary Endarterectomy in Subjects Affected by Chronic Thromboembolic Pulmonary Hypertension: A Prospective Cohort Study Read More »

Effect of fasudil on clinical outcomes of pulmonary hypertension: a systematic review and meta-analysis

Wanying Bao, Mengxin Cheng, Xiaoye Chen, Tao Wang, Dan Xu, Hualin Liao, Lei Chen, Fuqiang Wen, Junyun He, Jun ChenWest China Hospital, West China School of Medicine and Sichuan University. West China Second University Hospital. Union Hospital, Tongji Medical College and Huazhong University of Science and Technology. Hospital of Chengdu.China Expert Review of Clinical PharmacologyExp

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