Pediatric Pulmonary Vascular Disease or Adult Pulmonary Vascular Disease

Multimodality assessment of right ventricular-pulmonary arterial coupling and pulmonary artery compliance in youth with pulmonary arterial hypertension: A pilot study

Shashi Raj, Basha Khan, Vimal Raj, Vamsidhar Reddy Pulagam, Bibhuti B. DasNarayana Institute of Cardiac Sciences. Methodist Children’s Hospital. India and United States Journal of Heart and Lung Transplantation OpenJHLT Open 2026; 14: DOI: 10.1016/j.jhlto.2026.100664 AbstractBackground: Cardiac magnetic resonance (CMR) enables comprehensive assessment of right ventricular (RV) function and ventricular-vascular interaction in pulmonary arterial hypertension (PAH). This

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Post-Tuberculosis Lung Disease: Clinical Spectrum, Management Principles, and Lifelong Consequences

Brian W. Allwood, Alistair Broadhurst, Muhammad Saadiq Moolla, Anthony Carrozzi, Marieke M. van der Zalm, Anthony ByrneStellenbosch University. St Vincent’s Hospital and University of New South Wales clinical School. Socios En Salud Sucursal.South Africa, Australia and Peru Cold Spring Harbor Perspectives in MedicineCold Spring Harb Perspect MedDOI: 10.1101/cshperspect.a041887 AbstractPost-tuberculosis lung disease (PTLD) is an increasingly recognized

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An analysis of imaging modalities to assess the right and left heart in pulmonary hypertension with left-to-right shunts

Musawenkosi M. F. Henema, Stephen C. Brown, Francis E. Smit, Lezelle BotesDr. George Mukhari Academic Hospital and Central University of Technology. University of the Free State. South Africa Cardiovascular Journal of AfricaCardiovasc J Afr 2026; 37: 345-353DOI: 10.5830/CVJA-2026-033 AbstractBackground: Pulmonary hypertension (PH) secondary to congenital left-to-right shunts leads to serious consequences in sub-Saharan Africa. This study used

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The Epidemiology of Pulmonary Hypertension in Sub-Saharan Africa-A Systematic Report

Katarina Zeder, Lanjing Wang, Veranyuy Ngah, Armella Santi, Eric W. Robbins, Ana O. Mocumbi, Judith Namuyonga, Peter Nyasulu, Gabor Kovacs, Marc Humbert, Geoff Strange, Simon Stewart, Guoqing Diao, Bradley A. MaronUniversity of Maryland. Medical University of Graz. George Washington University. Stellenbosch University. University Eduardo Mondlane. Uganda Heart Institute and Makerere University College of Health Sciences.

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Isolated Left Ventricular Apical Hypoplasia, from Transient Neonatal Dysfunction to Maternal Hemodynamic Stress: A Comprehensive Review with Illustrative Cases

Mattia Pasquinucci, Martina Avesani, Anna La Rosa, Maria Elena Derchi, Davide Meneghesso, Davide Buffi, Federico Prefumo, Laura Tralli, Michela Marchesini, Anna Nocerino, Alessandra Grison, Claudia Santagati, Giulia Bordin, Gabriele De Tonetti, Elena Sofia Milandri, Giovanni Di Salvo, Gianluca TrocchioIRCCS Istituto Giannina Gaslini. AULSS 7 Pedemontana-San Bassiano Hospital. Padua University Hospital. AULSS 8 Berica-San Bortolo Hospital.

Isolated Left Ventricular Apical Hypoplasia, from Transient Neonatal Dysfunction to Maternal Hemodynamic Stress: A Comprehensive Review with Illustrative Cases Read More »

A Study on the Clinical Phenotypes and Genetic Analysis of ENG Variants in Four Hereditary Hemorrhagic Telangiectasia Type 1 Families

Yujing Gong, Tingmin Zhou, Xinru Fu, Yiyi Jiang, Danping Wang, Chuangjie Gu, Ruiting Wu, Dan Wang, Chang YuAffiliated Women and Children’s Hospital of Jiaxing University. First Affiliated Hospital of Wenzhou Medical University. Taizhou Hospital of Zhejiang Province Affiliated to Wenzhou Medical University. China Human MutationHum Mutat 2026; DOI: 10.1155/humu/8307860 AbstractBackground: Hereditary hemorrhagic telangiectasia (HHT) is an autosomal

A Study on the Clinical Phenotypes and Genetic Analysis of ENG Variants in Four Hereditary Hemorrhagic Telangiectasia Type 1 Families Read More »

Clinically significant posture-related oxygen saturation variability in Fontan circulation: Prevalence and determinants

Hiroki Uchiyama, Aya Miyazaki, Takamichi Ishikawa, Nao Inoue, Daisuke Masui, Mikihiro Shimizu, Yasumi NakashimaSeirei Hamamatsu General Hospital. Hamamatsu University School of Medicine and Hamamatsu University Hospital.Japan Journal of CardiologyJ Cardiol 2026; DOI: 10.1016/j.jjcc.2026.08.002 AbstractBackground: Patients with Fontan circulation often have low baseline oxygen saturation (SpO₂), and posture-related SpO₂ variability is sometimes observed in clinical practice. However, the

Clinically significant posture-related oxygen saturation variability in Fontan circulation: Prevalence and determinants Read More »

Early Detection and Therapy of Asymptomatic Group 1 Pulmonary Hypertension Following Genetic Testing: A Case Involving Familial KCNK3 Variants

Julia Rodighiero, Joshua Durbin, Lauren Badalato, Stephen L. ArcherQueen’s University. Canada Canadian Journal of Cardiology OpenCJC Open 2026; DOI: 10.1016/j.cjco.2026.04.013 AbstractAbstract Not Available CategoryClass I. Heritable Pulmonary HypertensionGenetic Factors Associated with Pulmonary Vascular Disease Age Focus: Pediatric Pulmonary Vascular Disease or Adult Pulmonary Vascular Disease Fresh or Filed Publication: Fresh (PHresh). Less than 1-2 years since

Early Detection and Therapy of Asymptomatic Group 1 Pulmonary Hypertension Following Genetic Testing: A Case Involving Familial KCNK3 Variants Read More »

Surviving Males With PORCN Variants: Expanding the Clinical, Molecular, and Mechanistic Spectrum

Lucía Miranda-Alcaraz, Simone Carbonera, Mónica Mora-Gómez, Natalia Gallego-Zazo, Inmaculada Guillén, Elena Padilla, Gaia Visani, Alessia Asaro, Valeria Vásquez-Amell, Mario Cazalla, Manuel Rodríguez-Canó, Cristina Silván, Pedro Arias, Juan Andrés Jiménez-Estrada, Tomás Valle, Alejandro Cruz-Utrilla, Pilar Escribano-Subías, Nuria Ochoa Parra, María Jesús del Cerro Marín, Julián Nevado, Spanish PAH Consortium, Pablo Lapunzina, Fabio Sirchia, Jair Tenorio-CastanoHospital Universitario

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The Heterogeneity of Long-Term Cardiopulmonary Outcomes in Children Born Preterm May Benefit from Pulmonary Hypertension-Specialty Outpatient Follow-Up

Meaghan C. Rousset, Rachel T. Sullivan, Anna M. Brown, Samantha R. Eagle, Eric D. AustinVanderbilt University Medical Center. United States Pulmonary CirculationPulm Circ 2026; 16: DOI: 10.1002/pul2.70380 AbstractPreterm birth survivors reaching adulthood are a growing population, with bronchopulmonary dysplasia (BPD), the chronic lung disease of prematurity, common among this cohort. Infants with BPD are at increased

The Heterogeneity of Long-Term Cardiopulmonary Outcomes in Children Born Preterm May Benefit from Pulmonary Hypertension-Specialty Outpatient Follow-Up Read More »

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