Pediatric Pulmonary Vascular Disease or Adult Pulmonary Vascular Disease

A systematic review of clinical study evidence for pulmonary vasodilator therapy following surgery with cardiopulmonary bypass in children with CHD

Henry P. Foote, Christoph P. Hornik, Kevin D. Hill, Alexandre T. Rotta, Karan R. Kumar, Elizabeth J. ThompsonDuke University School of MedicineUnited States Cardiology in the YoungCardiol Young 2022; 20: DOI: 10.1017/S1047951122002293 AbstractObjectives: Complications from pulmonary hypertension are one of the leading contributors to morbidity and mortality post-cardiopulmonary bypass surgery in children with CHD. Pulmonary vasodilator therapies […]

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Single-stage arterial switch operation conversion with dextro-transposition of the great arteries and pulmonary arterial hypertension due to baffle leak after a Senning procedure

Sorachi Shimada, Tomomi Uyeda, Yoshichika Maeda, Takumi Kobayashi, Kanako Kishiki, Yuji Hamamichi, Satoshi Yazaki, Naoki Wada, Yukihiro Takahashi, In-Sam Park, Tadahiro YoshikawaSakakibara Heart Institute. Asahikawa Medical University. Nishiogi Kimura Clinic.Japan Journal of Cardiology CasesJ Cardiol Cases 2022; 26: 345-347DOI: 10.1016/j.jccase.2022.07.008 AbstractPatients who have undergone an atrial switch operation for dextro-transposition of the great arteries (dTGA) sometimes

Single-stage arterial switch operation conversion with dextro-transposition of the great arteries and pulmonary arterial hypertension due to baffle leak after a Senning procedure Read More »

Congenital portosystemic shunt with multiple splenic artery aneurysms: Reversing pulmonary hypertension and preventing aneurysm rupture

Anand P. Subramanian, Adaligere Paraswanath Bharath, Ashita Barthur, Mahimarangaiah JayranganathSri Jayadeva Institute of Cardiovascular Sciences and ResearchIndia Annals of Pediatric CardiologyAnn Pediatr Cardiol 2022; 15: 300-303DOI: 10.4103/apc.apc_142_21 AbstractWe report an unusual occurrence of multiple splenic artery aneurysms and splenomegaly in a young woman with severe pulmonary hypertension, secondary to a congenital portosystemic shunt (CPS). The splenic

Congenital portosystemic shunt with multiple splenic artery aneurysms: Reversing pulmonary hypertension and preventing aneurysm rupture Read More »

Misclassification of Pulmonary Hypertension in Partial Anomalous Pulmonary Venous Return

Clifford W. Chin, David P. BichellVanderbilt University and Monroe Carell Junior Children’s HospitalUnited States Annals of Thoracic SurgeryAnn Thorac Surg 2022; 114: e447-e449DOI: 10.1016/j.athoracsur.2022.02.021 AbstractPartial anomalous pulmonary venous return is a rare congenital heart defect that can escape detection until adulthood and can be misdiagnosed as pulmonary hypertension and managed with vasodilators before the anomaly is

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Proteomics discovery of pulmonary hypertension biomarkers: Insulin-like growth factor binding proteins are associated with disease severity

Melanie K. Nies, Jun Yang, Megan Griffiths, Rachel Damico, Jie Zhu, Dhananjay Vaydia, Zongming Fu, Stephanie Brandal, Eric D. Austin, Dunbar D. Ivy, Paul M. Hassoun, Jennifer E. Van Eyk, Allen D. EverettJohns Hopkins University. Columbia University New York. Vanderbilt University. Children’s Hospital Colorado. Cedars-Sinai Medical Center.United States Pulmonary CirculationPulm Circ 2022; 12:DOI: 10.1002/pul2.12039 AbstractPulmonary arterial

Proteomics discovery of pulmonary hypertension biomarkers: Insulin-like growth factor binding proteins are associated with disease severity Read More »

High haemoglobin levels at the time of occlusion predict worse outcome for patients with patent ductus arteriosus and pulmonary hypertension

Kanta Kishi, Jirayut Jarutach, Yinn Khurn Wong, Marhisham Che Mood, Geetha Kandhavello, Mazeni Alwi, Ming Chern Leong Osaka Medical and Pharmaceutical University. Prince of Songkla University. Serdang Hospital. Sarawak General Hospital. Institut Jantung Negara.Japan, Thailand and Malaysia Cardiology in the YoungCardiol Young 2022; DOI: 10.1017/S104795112200244X AbstractIntroduction: Current guidelines discourage shunt closure in patients with pulmonary vascular resistance

High haemoglobin levels at the time of occlusion predict worse outcome for patients with patent ductus arteriosus and pulmonary hypertension Read More »

Channelopathy Genes in Pulmonary Arterial Hypertension

Carrie L. Welch, Wendy K. ChungColumbia University Irving Medical Center.United States BiomoleculesBiomolecules 2022; 12: DOI: 10.3390/biom12020265 AbstractPulmonary arterial hypertension (PAH) is a rare, progressive vasculopathy with significant cardiopulmonary morbidity and mortality. The underlying pathogenetic mechanisms are heterogeneous and current therapies aim to decrease pulmonary vascular resistance but no curative treatments are available. Causal genetic variants can

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Correlation Between Right Ventricular Echocardiography Measurements and Functional Capacity in Patients With Pulmonary Arterial Hypertension

Joyce L. Woo, Michael P. DiLorenzo, Eliana Rosenzweig, Nikhil Pasumarti, Gerson Valencia Villeda, Erika Berman-Rosenzweig, Usha KrishnanAnn and Robert H. Lurie Children’s Hospital of Chicago and Northwestern University Feinberg School of Medicine. Columbia University Medical Center. Arnold Palmer Hospital for Children.United States Texas Heart Institute JournalTex Heart Inst J 2022; 49: DOI: 10.14503/THIJ-21-7719 AbstractBackground: Accelerometry is an

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ISHLT consensus statement: Perioperative management of patients with pulmonary hypertension and right heart failure undergoing surgery

Dana P. McGlothlin, John Granton, Walter Klepetko, Maurice Beghetti, Erika B. Rosenzweig, Paul A. Corris, Evelyn Horn, Manreet K. Kanwar, Karen McRae, Antonio Roman, Ryan Tedford, Roberto Badagliacca, Sonja Bartolome, Raymond Benza, Marco Caccamo, Rebecca Cogswell, Celine Dewachter, Laura Donahoe, Elie Fadel, Harrison W. Farber, Jeffrey Feinstein, Veronica Franco, Robert Frantz, Michael Gatzoulis, Choon Hwa

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Clinical differences between children and adults with idiopathic and heritable pulmonary arterial hypertension

Shinichi Takatsuki, Hiroto Shimokawahara, Yukira Shimizu, Reiko Kawai, Hiroyuki Matsuura, Hiromi MatsubaraToho University Omori Medical Center. National Hospital Organization Okayama Medical Center.Japan Cardiology in the YoungCardiol Young 2022; DOI: 10.1017/S1047951122003432 AbstractBackground: Although previous studies have demonstrated that paediatric pulmonary arterial hypertension remains distinct from that in adults, there are limited studies evaluating a direct comparison between children

Clinical differences between children and adults with idiopathic and heritable pulmonary arterial hypertension Read More »

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