Heart Dysfunction Associated with Pulmonary Vascular Disease

Inactivation of AXL in Cardiac Fibroblasts Alleviates Right Ventricular Remodeling in Pulmonary Hypertension

Li-Wei Wu, Min Chen, Chen-Yu Jiang, Dai-Ji Jiang, Xu Zhang, Xiao-He Xu, Yi-Wei Liu, Bei Feng, Lin-Cai Ye, Yang-Yang He, Xu Huang, Yi-Chi Zhang, Xing-Liang Zhou, Yi Shen, Tian-Yu Liu, Li-Jun Fu, Yi Yan, Hao ZhangShanghai Children’s Medical Center, National Children’s Medical Center and Shanghai Jiao Tong University School of Medicine. Second Affiliated Hospital and […]

Inactivation of AXL in Cardiac Fibroblasts Alleviates Right Ventricular Remodeling in Pulmonary Hypertension Read More »

Volume Loading May Compromise Left Ventricular Filling in Patients with a Borderline Hypoplastic Left Ventricle

Machi Yamashita, Hirofumi Saiki, Kanchi Saito, Akira Sato, Seiko Kuwata, Satoshi Nakano, Hideaki Senzaki, Junichi KoizumiIwate Medical University. Nihon Institute of Medical Science.Japan International Heart JournalInt Heart J 2025; 66: 1019-1024DOI: 10.1536/ihj.25-216 AbstractGiven the high prevalence of end-organ damage in the long term after the Fontan procedure, patients presenting with borderline hypoplastic left ventricle (LV) are

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Longitudinal changes of left ventricular hypoplasia and ventricular disproportion in congenital diaphragmatic hernia neonates

Flaminia Pugnaloni, Bartolomeo Bo, Judith Leyens, Irma Capolupo, Andrea Dotta, Pietro Bagolan, Andreas Mueller, Neil Patel, Florian KipfmuellerChildren’s Hospital, University Hospital Bonn and University of Bonn. Bambino Gesù Children’s Hospital-Research Institute, IRCCS. University Medical Center, Mannheim and Heidelberg University. University of Rome “Tor Vergata”. Royal Hospital for Children. Germany, Italy and United Kingdom Journal of

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Can N-terminal pro-brain natriuretic peptide accurately diagnose chronic pulmonary hypertension among extremely low gestational age neonates: A Retrospective Cohort Study

Macarena Garcia Gozalo, Amish Jain, Dany E. Weisz, Bonny JasaniLa Paz University Hospital.  Mount Sinai Hospital. University of Toronto. Sunnybrook Health Sciences Centre. Hospital for Sick Children.Spain and Canada Journal of PerinatologyJ Perinatol 2025; DOI: 10.1038/s41372-025-02462-3 AbstractObjective: To evaluate the utility of N-terminal pro-brain natriuretic peptide (NT pro-BNP) for screening and diagnosis of chronic pulmonary hypertension (cPH)

Can N-terminal pro-brain natriuretic peptide accurately diagnose chronic pulmonary hypertension among extremely low gestational age neonates: A Retrospective Cohort Study Read More »

Early left ventricular diastolic function and disease severity in congenital diaphragmatic herni

Giulia Vanina Cantone, Abhijit Bhattacharya, David Healy, Dana Levinkopf, Anna Claudia Massolo, Flaminia Pugnaloni, Giovanni Vento, Anne Marie Heuchan, Florian Kipfmueller, Neil PatelFondazione Policlinico Universitario “A. Gemelli” IRCCS and Università Cattolica del Sacro Cuore. Royal Hospital for Children. “Bambino Gesù” Children Hospital – IRCCS.  University Medical Center Mannheim and University Heidelberg.Italy, United Kingdom and Germany

Early left ventricular diastolic function and disease severity in congenital diaphragmatic herni Read More »

Right ventricular dysfunctions in type 1 diabetic mice: A longitudinal study

Jian-Jian Yu, Jian-Ge Han, Yi Tan, Jian-Xiang Xu, Amanda LeBlanc, Bradley B. Keller, Jiapeng Huang, Lu CaiUniversity of Louisville School of Medicine. Tianjin University Chest Hospital. Cincinnati Children’s Heart Institute and University of Cincinnati. United States and China World Journal of DiabetesWorld J Diabetes 2025; 13: DOI: 10.4239/wjd.v16.i10.109526 AbstractBackground: Diabetes has become a widespread metabolic disease affecting

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“Gentle” cardio-respiratory management in congenital diaphragmatic hernia: Time for a precision-medicine approach?

Anna Foth, David Tingay, Florian KipfmuellerUniversity Medical Center Mannheim and Heidelberg University. Murdoch Children’s Research Institute and University of Melbourne. Germany and Australia Seminars in Fetal and Neonatal MedicineSemin Fetal Neonatal Med 2025; DOI: 10.1016/j.siny.2025.101660 AbstractCongenital diaphragmatic hernia (CDH) remains one of the most challenging conditions to manage in neonatal intensive care, with outcomes determined by

“Gentle” cardio-respiratory management in congenital diaphragmatic hernia: Time for a precision-medicine approach? Read More »

Risk Factors for low Cardiac Output Syndrome in Children less than 6 years old Undergoing Ventricular Septal Defect Closure: a Retrospective Cohort Study

Takumi Yamaguchi, Yumi Tomonari, Shiori Utsunomiya, Nakako Fujioka, Takahiro AsanoJapan Community Health Care Organization Chukyo Hospital. Japan Pediatric CardiologyPediatr Cardiol 2025; DOI: 10.1007/s00246-025-04041-x AbstractLow cardiac output syndrome (LCOS) is a critical complication following ventricular septal defect (VSD) closure in children. Despite its clinical importance, the risk factors specific to LCOS in VSD cases are underexplored. This

Risk Factors for low Cardiac Output Syndrome in Children less than 6 years old Undergoing Ventricular Septal Defect Closure: a Retrospective Cohort Study Read More »

Right atrial function is impaired in pediatric pulmonary arterial hypertension: a multi-center cardiac MRI study

Kimberley G. Miles, Hieu T. Ta, Kurt R. Bjorkman, Zhiqian Gao, Nicholas J. Ollberding, Russel Hirsch, D. Dunbar Ivy, Sean M. Lang, Michelle Cash, Melissa Magness, Meredith O’Neil, Kimberly Luebbe, Benjamin S. Frank, Paul J. CritserCincinnati Children’s Hospital Medical Center and University of Cincinnati College of Medicine. Helen DeVos Children’s Hospital. University of Colorado School

Right atrial function is impaired in pediatric pulmonary arterial hypertension: a multi-center cardiac MRI study Read More »

The Effect of Microvascular Remodeling on Fluid Dynamics in the Pressure Overloaded Right Ventricle

Ilham Essafri, Kenzo Ichimura, Dunbar Ivy, Kurt R. Stenmark, Helena A. Turton, Laura L. Pyle, Edda Spiekerkoetter, Vitaly O. KheyfetsUniversity of Colorado Anschutz Medical Campus and Children’s Hospital Colorado. Stanford University, Stanford. United States American Journal of Physiology Heart and Circulatory PhysiologyAm J Physiol Heart Circ Physiol 2025; DOI: 10.1152/ajpheart.00147.2025 AbstractRight ventricular (RV) failure, a major

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