Heart Dysfunction Associated with Pulmonary Vascular Disease

Current State of RV Multimodality Imaging in Pediatric Pulmonary Hypertension: Current Evidence, Knowledge Gaps, and Future Research Directions

Kimberley G. Miles, Dan M. Dorobantu, Johannes Menno Douwes, Benjamin S. Frank, Pei-Ni Jone, Vivek Muthurangu, D. Dunbar Ivy, Hythem Nawaytou, Mark K. FriedbergCincinnati Children’s Hospital and University of Cincinnati College of Medicine. Bristol Royal Hospital for Children and Heart Institute. Beatrix Children’s Hospital, University Medical Center Groningen and University of Groningen. University of Colorado Denver Anschutz […]

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Right ventricular adaptation in congenital heart disease: Does the type of right ventricular overload matter?

Renee S. Joosen, Gregor J. Krings, Heleen B. van der Zwaan, Nefise Karaman, Marco Guglielmo, Lucas R. Celant, Marco J. W. G€otte, Michael G. Dickinson, Michiel Voskuil, Marielle C. van de Veerdonk, Johannes M. P. J. BreurUniversity Medical Center Utrecht. Amsterdam University Medical Center and University of Amsterdam. Netherlands Journal of Thoracic and Cardiovascular Surgery

Right ventricular adaptation in congenital heart disease: Does the type of right ventricular overload matter? Read More »

AI learning for pediatric right ventricular assessment: development and validation across multiple centers

Charitha Reddy, Yi Yan, Min Qiu, Yi Tang, Bo Jin, Zhi Han, Yuhang Li, Sihan Zhou, Qiming Tang, Huan Xiao, Shu Yang, Qigui Wen, Lan-Ping Wu, Li-Jun Fu, Ze-Yu Jing, Yi-Jia Yang, Yu-Qi Zhang, Naoto Ozawa, Takumi Ichikawa, Ellen Ling, Ronald J. Wong, Nima Aghaeepour, Brice Gaudilliere, Martin S. Angst, Karl G. Sylvester, Harvey J.

AI learning for pediatric right ventricular assessment: development and validation across multiple centers Read More »

Paediatric pulmonary arterial hypertension following congenital heart defect repair: Enhanced risk stratification and outcomes in a national cohort

Andrew Constantine, Konstantinos Dimopoulos, Robin Condliffe, Paul Clift, Katrijn Jansen, S. John Wort, Grace Chaplin, Kaushiga Krishnathasan, Rami Dhillon, Joydeep Mookerjee, W. Brodie Knight, Caroline B. Jones, Maria N. Velasco Forte, Dirk Wilson, Helen Michael, Alberto Mendoza Soto, Carlos Labrandero, Alejandro Rodríguez Ogando, Antonio Moreno Galdó, Inmaculada Guillén Rodríguez, Lina M. Caicedo Cuenca, Francesca Perin,

Paediatric pulmonary arterial hypertension following congenital heart defect repair: Enhanced risk stratification and outcomes in a national cohort Read More »

Use of SGLT2 (Sodium-Glucose Cotransporter 2) Inhibitors in Pulmonary Hypertension

Benoit Aguado, Grégoire Ruffenach, Thomas Lacoste-Palasset, Agnes Görlach, Marianne Riou, Mathieu Gourmelon, Fabrice Bauer, Marc Humbert, Valerie Schini-Kerth, Jean-Luc Vachiéry, David Montani, Fabrice AntignyUniversité Paris-Saclay and French National Institute for Health and Medical Research. Hôpital Bicêtre and Hôpital Marie Lannelongue. Technical University Munich and German Centre for Cardiovascular Research. Nouvel Hôpital Civil and University Hospital

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Inactivation of AXL in Cardiac Fibroblasts Alleviates Right Ventricular Remodeling in Pulmonary Hypertension

Li-Wei Wu, Min Chen, Chen-Yu Jiang, Dai-Ji Jiang, Xu Zhang, Xiao-He Xu, Yi-Wei Liu, Bei Feng, Lin-Cai Ye, Yang-Yang He, Xu Huang, Yi-Chi Zhang, Xing-Liang Zhou, Yi Shen, Tian-Yu Liu, Li-Jun Fu, Yi Yan, Hao ZhangShanghai Children’s Medical Center, National Children’s Medical Center and Shanghai Jiao Tong University School of Medicine. Second Affiliated Hospital and

Inactivation of AXL in Cardiac Fibroblasts Alleviates Right Ventricular Remodeling in Pulmonary Hypertension Read More »

Volume Loading May Compromise Left Ventricular Filling in Patients with a Borderline Hypoplastic Left Ventricle

Machi Yamashita, Hirofumi Saiki, Kanchi Saito, Akira Sato, Seiko Kuwata, Satoshi Nakano, Hideaki Senzaki, Junichi KoizumiIwate Medical University. Nihon Institute of Medical Science.Japan International Heart JournalInt Heart J 2025; 66: 1019-1024DOI: 10.1536/ihj.25-216 AbstractGiven the high prevalence of end-organ damage in the long term after the Fontan procedure, patients presenting with borderline hypoplastic left ventricle (LV) are

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Longitudinal changes of left ventricular hypoplasia and ventricular disproportion in congenital diaphragmatic hernia neonates

Flaminia Pugnaloni, Bartolomeo Bo, Judith Leyens, Irma Capolupo, Andrea Dotta, Pietro Bagolan, Andreas Mueller, Neil Patel, Florian KipfmuellerChildren’s Hospital, University Hospital Bonn and University of Bonn. Bambino Gesù Children’s Hospital-Research Institute, IRCCS. University Medical Center, Mannheim and Heidelberg University. University of Rome “Tor Vergata”. Royal Hospital for Children. Germany, Italy and United Kingdom Journal of

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Can N-terminal pro-brain natriuretic peptide accurately diagnose chronic pulmonary hypertension among extremely low gestational age neonates: A Retrospective Cohort Study

Macarena Garcia Gozalo, Amish Jain, Dany E. Weisz, Bonny JasaniLa Paz University Hospital.  Mount Sinai Hospital. University of Toronto. Sunnybrook Health Sciences Centre. Hospital for Sick Children.Spain and Canada Journal of PerinatologyJ Perinatol 2025; DOI: 10.1038/s41372-025-02462-3 AbstractObjective: To evaluate the utility of N-terminal pro-brain natriuretic peptide (NT pro-BNP) for screening and diagnosis of chronic pulmonary hypertension (cPH)

Can N-terminal pro-brain natriuretic peptide accurately diagnose chronic pulmonary hypertension among extremely low gestational age neonates: A Retrospective Cohort Study Read More »

Early left ventricular diastolic function and disease severity in congenital diaphragmatic herni

Giulia Vanina Cantone, Abhijit Bhattacharya, David Healy, Dana Levinkopf, Anna Claudia Massolo, Flaminia Pugnaloni, Giovanni Vento, Anne Marie Heuchan, Florian Kipfmueller, Neil PatelFondazione Policlinico Universitario “A. Gemelli” IRCCS and Università Cattolica del Sacro Cuore. Royal Hospital for Children. “Bambino Gesù” Children Hospital – IRCCS.  University Medical Center Mannheim and University Heidelberg.Italy, United Kingdom and Germany

Early left ventricular diastolic function and disease severity in congenital diaphragmatic herni Read More »

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