Pediatric Pulmonary Vascular Disease

Impact of Hernia Sac in Congenital Diaphragmatic Hernia: Associations with Morbidity and Mortality

Krysta M Sutyak 1, Kylie I Holden 2, Charles Green 3, Matthew T Harting 2, KuoJen Tsao 4, Kouji Nagata 5, Richard Keijzer 6, Marietta Jank 6, Tim Jancelewicz 7, Joseph T Church 8, Pamela A Lally 2, Kevin P Lally 4; For, The Congenital Diaphragmatic Hernia Study Group McGovern Medical School and University of Texas Health Science Center at Houston and Children’s Memorial Hermann Hospital. Kyushu University. University of Manitoba. University of Tennessee Health Science Center. University of […]

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Endomyocardial calcification with pulmonary and systemic hypertension in a term neonate with multisystem inflammatory syndrome of newborn (MIS-N)

Swasthi Kabi Satpathy. Choudri Muzafar Paswal, Neeraj Gupta, Jai Prakash Soni, Sushil Kumar ChoudharyAll India Institute of Medical Sciences Jodhpur. Dr Sampurnanand Medical College.India British Medical Journal Case ReportsBMJ Case Rep 2026; 19:DOI: 10.1136/bcr-2025-270053 AbstractMultisystem inflammatory syndrome in neonates (MIS-N) is a rare condition linked to perinatal exposure to SARS-CoV-2. We report a case of a

Endomyocardial calcification with pulmonary and systemic hypertension in a term neonate with multisystem inflammatory syndrome of newborn (MIS-N) Read More »

Liver herniation in congenital diaphragmatic hernia is associated with delayed resolution of pulmonary hypertension

Uthaya Kumaran Kanagaraj, Mimi T.Y. Kuan, Michael Castaldo, Erik Skarsgard, Joseph Y. TingUniversity of British Columbia. University of Alberta.Canada Pediatrics and NeonatologyPediatr Neonatol 2026; DOI: 10.1016/j.pedneo.2025.11.011 AbstractBackground: Severe and persistent pulmonary hypertension (PH) predicts mortality and short-term pulmonary morbidity in infants with congenital diaphragmatic hernia (CDH). Intrathoracic liver herniation (liver-up) is a predictor of survival and increased

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Scimitar syndrome presenting in infancy

Charles B. Huddleston, Vernat Exil, Charles E. Canter, Eric N. MendeloffWashington University School of Medicine and St. Louis Children’s Hospital.United States Annals of Thoracic SurgeryAnn Thorac Surg 1999; 67: 154-159DOI: 10.1016/s0003-4975(98)01227-2 AbstractBackground: Scimitar syndrome has a variable presentation based on the age at which the diagnosis is made. In general, infants presenting in heart failure have a

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A Novel Rat Model for Group 2 Pulmonary Hypertension by Total Pulmonary Vein Banding: Multi-Omics Insights into Pathophysiological Mechanisms

Jin Shentu, Wenxuan Dai, Chang Chen, Jiawei Huang, Lijun Chen, Yi Yan, Han Zhang, Zhongqun Zhu, Guocheng Shi, Huiwen ChenShanghai Children’s Medical Center and Shanghai Jiao Tong University School of Medicine. China Journal of Thoracic and Cardiovascular SurgeryJ Thorac Cardiovasc Surg 2026; DOI: 10.1016/j.jtcvs.2026.01.017 AbstractObjectives: Group 2 pulmonary hypertension (PH) remains a highly morbid disease, yet no

A Novel Rat Model for Group 2 Pulmonary Hypertension by Total Pulmonary Vein Banding: Multi-Omics Insights into Pathophysiological Mechanisms Read More »

Expanding the phenotypic spectrum of MECOM-associated syndrome: rare variants are associated with syndromic pulmonary arterial hypertension

Carrie L. Welch , Meriel McEntagart, Shahin Moledina, Cara Morgan, Emilia Swietlik, Chao Hou, Lu Qiao, Emily Callejo, Savanna Craib, Damian Smedley, Emilia K. Bijlsma, Patrice Bouvagnet, Nahir Cortes-­Santiago, Tamir Dagan, Jacqueline Eason, Frances Flinter, Aakash Joshi, Jeremie Mortreux, Fadel E. Ruiz, Deborah Shears, Celia Azevedo Soares, Nidhy P. Varghese, Wendy K ChungBoston Children’s Hospital,

Expanding the phenotypic spectrum of MECOM-associated syndrome: rare variants are associated with syndromic pulmonary arterial hypertension Read More »

Successful bridge to diagnosis: Extracorporeal life support in generalized arterial calcification of infancy

Sarah D. King, Spencer Wilhelm, Ruth Lewit, Erin E. Perrone, Arul ThirumoorthiUniversity of Michigan,.United States PerfusionPerfusion 2026; DOI: 10.1177/02676591261420652 AbstractIntroduction: Generalized arterial calcification of infancy (GACI) is a rare, difficult to recognize, autosomal recessive disorder with high neonatal mortality due to vascular calcification and cardiopulmonary collapse.Case Report: We report a term female presenting with persistent pulmonary

Successful bridge to diagnosis: Extracorporeal life support in generalized arterial calcification of infancy Read More »

Prevalence and severity of persistent pulmonary hypertension of the newborns among asphyxiated neonates admitted in Enugu State University Teaching Hospital

Ani Okechukwu, Odutola Odetunde, Ekwochi Uchenna, Josephat M ChinawaEnugu State University College of Medicine. University of Nigeria Teaching Hospital Ituku/Ozalla and University of Nigeria ItukuNigeria British Medical Journal Paediatrics OpenBMJ Paediatr Open 2026; 10: DOI: 10.1136/bmjpo-2025-004351 AbstractBackground: Persistent pulmonary hypertension of newborns (PPHN) is an acute neonatal disorder with a high mortality rate despite several advances in

Prevalence and severity of persistent pulmonary hypertension of the newborns among asphyxiated neonates admitted in Enugu State University Teaching Hospital Read More »

Microbiome-Metabolome Axis in BALF Reveals Novel Diagnostic Biomarkers for Congenital Heart Disease-Associated Pulmonary Arterial Hypertension

Xiaoyu Zhang, Liming Cheng, Yuan Zhou, Jiahui Xie, Wenting Gui, Jiaxiang Chen, Zidan Zhang, Kai Liu, Runwei MaFuwai Yunnan Hospital, Chinese Academy of Medical Sciences, Affiliated Cardiovascular Hospital of Kunming Medical University. Kunming Children’s Hospital.China Journal of Cardiovascular Development and DiseaseJ Cardiovasc Dev Dis 2026; 13: DOI: 10.3390/jcdd13010032 AbstractBackground: Early identification of irreversible pulmonary vascular remodeling in

Microbiome-Metabolome Axis in BALF Reveals Novel Diagnostic Biomarkers for Congenital Heart Disease-Associated Pulmonary Arterial Hypertension Read More »

Infant with Complex Congenital Cardiac Anomalies: A Case Report and Review of Literature

Aliasgar Taha, Abdullah Ahmed Tariq, Yusur Abbas Mahmood, Leah Leslie Dias, Rahul Binu, Subhranshu Sekhar Kar, Alaa Mohamad HussainRas Al Khaimah Medical and Health Sciences University.United Arab Emirits Annals of African MedicineAnn Afr Med 2026; DOI: 10.4103/aam.aam_631_25 AbstractThe coexistence of multiple complex congenital cardiac anomalies in a single infant – particularly unbalanced Atrioventricular Septal Defect; Double

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