Pediatric Pulmonary Vascular Disease

Pediatric Lung Transplantation in Israel: 29 Cases from a Single Center’s Experience

Eyal Jacobi, Moshe Heching, Osnat Shtraichman, Dror Rosengarten, Barak Pertzov, Ophir Bar-On, Hagit Levine, Ofer Schiller, Yury Peysakhovich, Dario Prais, Yaron Barac, Mordechai Reuven KramerSchneider Children’s Medical Center, Rabin Medical Center, Gray Faculty of Medical and Health Sciences and Tel Aviv University. Israel Israel Medical Association JournalIsrael Med Assoc J 2025; 27: 778-782DOI: Not Available

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Reversible Pulmonary Hypertension in CblC Deficiency (MMACHC c.80 A>G): long-term outcomes of metabolic and PH-targeted therapy

Ruxuan He, Jinrong Liu, Xiaolei Tang, Hui Liu, Yuelin Shen, Xioayan Zhang, Huimin Li, Shunying Zhao, Haiming YangBeijing Children’s Hospital and Capital Medical University. Children’s Hospital of Xinjiang Uygur Autonomous Region, Xinjiang Hospital of Beijing Children’s Hospital and Seventh People’s Hospital of Xinjiang Uygur Autonomous Region.China Pediatric ResearchPediatr Res 2025; DOI: 10.1038/s41390-025-04720-8 AbstractBackground: Cobalamin C (cblC) deficiency,

Reversible Pulmonary Hypertension in CblC Deficiency (MMACHC c.80 A>G): long-term outcomes of metabolic and PH-targeted therapy Read More »

Six cases of ENPP1 pathogenic variants causing autosomal recessive hypophosphatemic rickets type 2 and generalized arterial calcification of infancy

Lucy Collins, Jessica Sandy, Stephanie Ly, Kate E. Lomax, Sarah Black, Fiona McKenzie, Eadaoin Hayes, Cathryn Poulton, Craig Jefferies, Wendy Hunter, Peter Simm, Christine Rodda, Andrew Biggin, Craig Munns, Aris SiafarikasRoyal Children’s Hospital. Monash University. Children’s Hospital at Westmead. University of Sydney. Perth Children’s Hospital. University of Western Australia. King Edward Memorial Hospital. Starship Children’s

Six cases of ENPP1 pathogenic variants causing autosomal recessive hypophosphatemic rickets type 2 and generalized arterial calcification of infancy Read More »

An Approach to Children with Pulmonary Edema at High Altitude

Deborah R. Liptzin, Steven H. Abman, Ann Giesenhagen, D. Dunbar IvyUniversity of Colorado School of Medicine and Children’s Hospital ColoradoUnited States High Altitude Medicine and BiologyHigh Altit Med Biol 2018;DOI: 10.1089/ham.2017.0096 AbstractIntroduction: Diagnosis of high-altitude illness can be more challenging in children, especially those who are preverbal. Families often travel to high elevations for family vacations, either

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A prospective, multicenter, open-label, single-arm Phase 2 study to investigate the pharmacokinetics, safety, tolerability, and exploratory efficacy of selexipag in children with pulmonary arterial hypertension

Maurice Beghetti, Lene Nygaard Axelsen, Julian I. Borissoff, Mahdi Farhan, Simon Grill, Sining Leng, Alberto Russu, Catherine Lesage, Tatiana Remeňová, Shu-Fang Hsu Schmitz, Shahin MoledinaUniversity Hospitals of Geneva. Johnson & Johnson. Great Ormond Street Hospital. Switzerland and United Kingdom ChestChest 2025; DOI: 10.1016/j.chest.2025.12.013 AbstractBackground: Selexipag is an oral selective prostacyclin receptor agonist approved for treating pulmonary arterial

A prospective, multicenter, open-label, single-arm Phase 2 study to investigate the pharmacokinetics, safety, tolerability, and exploratory efficacy of selexipag in children with pulmonary arterial hypertension Read More »

Interorgan Communication-Pulmonary Vein Stenosis in Children-A Review of Epidemiology, Pathophysiology, and Current Management Principles

Usha S. Krishnan, Mary P. MullenVagelos College of Physicians and Surgeons of Columbia University Irving Medical Center and Morgan Stanley Children’s Hospital of New York Presbyterian. Boston Children’s Hospital and Harvard Medical School. United States Comprehensive Physiology Interorgan Communication in Health and DiseaseCompre Physiol 2025; DOI: 10.1002/cph4.70085 AbstractUnderstanding communication between various organ systems is vital to

Interorgan Communication-Pulmonary Vein Stenosis in Children-A Review of Epidemiology, Pathophysiology, and Current Management Principles Read More »

Development and validation of a pre-trained language model for neonatal morbidities: a retrospective, multicentre, prognostic study

Feng Xie, Philip Chung, Jonathan D. Reiss, Erico Tjoa, Davide De Francesco, Thanaphong Phongpreecha, William Haberkorn, Dipro Chakraborty, Alan Lee Chang, Tomin James, Yeasul Kim, Samson Mataraso, Camilo Espinosa, Liu Yang, Chi-Hung Shu, Lei Xue, Eloïse Berson, Neshat Mohammadi, Sayane Shome, S Momsen Reincke, Marc Ghanem, Ivana Maric, Brice Gaudilliere, Martin S Angst, Karl Sylvester,

Development and validation of a pre-trained language model for neonatal morbidities: a retrospective, multicentre, prognostic study Read More »

Reduction in Prostacyclin Infusion Errors Following a Comprehensive Multidisciplinary Process Transformation for Hospitalized Pediatric Patients with Pulmonary Hypertension: A Quality Improvement Project

Christa Kirk, Anne Davis, Delphine YungDuquesne University School of Pharmacy. Seattle Children’s Hospital. University of Washington School of Medicine.United States Journal of Pediatric Pharmacology and TherapeuticsJ Pediatr Pharmacol Ther 2025; 30: 800-806DOI: 10.5863/JPPT-25-00033 AbstractObjective: Owing to a rise in potentially serious errors with parenteral prostacyclin infusions associated with using an unfamiliar MedFusion 3500 syringe pump (MedFusion), we

Reduction in Prostacyclin Infusion Errors Following a Comprehensive Multidisciplinary Process Transformation for Hospitalized Pediatric Patients with Pulmonary Hypertension: A Quality Improvement Project Read More »

Noncirrhotic Portopulmonary Hypertension Due to Hepatoportal Sclerosis in Adams-Oliver Syndrome

Jennifer Merk, Delphine Yung, Jason N. Wright, Raj P. KapurUniversity of Washington and Seattle Children’s Hospital.United States PediatricsPediatrics 2025;DOI: 10.1542/peds.2025-073243 AbstractA 13-year-old girl presented for evaluation of pulmonary hypertension after symptoms of dyspnea and exercise intolerance. Full evaluation was negative except for abdominal ultrasonography with splenomegaly and esophageal varices suggestive of portal hypertension. Cardiac and hepatic

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Generation of 5 hiPSC lines from pediatric patients with Heritable pulmonary arterial hypertension (HPAH) caused by heterozygous mutations in the TBX4 gene

Valeria Fernandez Vallone, Kristin Fischer, Judit Küchler, Franziska Diekmann, Georg Hansmann, Harald StachelscheidBerlin Institute of Health at Charité – Universitätsmedizin Berlin. Hannover Medical School. Children’s Hospital, General Hospital Vienna, Medical University of Vienna. European Pediatric Pulmonary Vascular Disease Network.Germany and Austria Stem Cell ResearchStem Cell Res 2025; DOI: 10.1016/j.scr.2025.103886 AbstractHeritable pulmonary arterial hypertension (HPAH) and underlying

Generation of 5 hiPSC lines from pediatric patients with Heritable pulmonary arterial hypertension (HPAH) caused by heterozygous mutations in the TBX4 gene Read More »

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