Pediatric Pulmonary Vascular Disease

Mechanism and Treatment of Right Ventricular Failure Due to Pulmonary Hypertension in Children

Bibhuti B. DasUniversity of Mississippi Medical Center.United States ChildrenChildren 2025; 12: DOI: 10.3390/children12040476 AbstractPulmonary hypertension (PH) is a progressive disorder characterized by obstructive changes in the pulmonary vasculature, leading to increased pulmonary vascular resistance (PVR), right ventricular (RV) strain, and eventual RV failure (RVF). Despite advancements in medical therapy, PH remains associated with significant morbidity and […]

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Real-Time Assessment of Pulmonary Blood Flow in Pulmonary Vein Stenosis Using the Fluoroscopic Flow Calculator

Yuval Barak-Corren, Mudit Gupta, Yoav Dori, Jessica Tang, Christopher L. Smith, Jonathan J. Rome, Matthew J. Gillespie, Matthew A. Jolley, Michael L. O’Byrne, Ryan CallahanChildren’s Hospital of Philadelphia and Perelman School of Medicine at the University of Pennsylvania.United States Journal of the Society for Cardiovascular Angiography and InterventionsJ Soc Cardiovasc Angiogr Interv 2025; 4:DOI: 10.1016/j.jscai.2025.102639 AbstractBackground: Restenosis

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Bronchopulmonary Dysplasia-Associated Pulmonary Hypertension: Screening and Management

Samuel F. Schaeffer, Bwaar Omer, Akshaya Vachhaarajani, Chaitanya PanchangamUniversity of Missouri.United States NeoreviewsNeoreviews 2025; 26: e316-e327DOI: 10.1542/neo.26-5-013 AbstractScreening for pulmonary hypertension (PH) in infants with bronchopulmonary dysplasia (BPD) was recommended by the American Thoracic Society in 2015. However, the definition of BPD has since changed. This review summarizes the current definition of BPD, the recommendations and

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Case Report: Congenital hepatic hemangioma with arteriovenous fistula: 2-year multidisciplinary management and outcomes

Renping Mao, Weiwei Ruan, Jianming Zhu, Li Li, Haiyan Jiang, Yanhong LiAffiliated Women and Children’s Hospital of Ningbo University.China Frontiers in PediatricsFront Pediatr 2025; 13: DOI: 10.3389/fped.2025.1511892 AbstractBackground: Congenital hepatic hemangioma with arteriovenous fistula (HHAVF) is a rare condition in newborns that may manifest as respiratory distress, pulmonary hypertension, and heart failure shortly after birth. This report

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Retinal detachment in a neonate with congenital chylothorax and purpura fulminans associated with the PAK2 genetic variant: A case report

Arijit Lodha, Majeeda Kamaluddeen, Stephanie Dotchin, Julie Lauzon, Patrick MitchellUniversity of Alberta. Cumming School of Medicine, University of Calgary. Canada International Journal of Surgery Case ReportsInt J Surg Case Rep 2025; 130: DOI: 10.1016/j.ijscr.2025.111341 AbstractIntroduction and importance: A potential relationship between bilateral retinal detachment, chylothorax, and purpura fulminans in a female neonate with a PAK2 gene variant

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Lymphaticovenous and Lymph Node-to-Vein Anastomosis to Improve Milroy Disease-Related Chylothorax and Lymphedema

Feres Alshomer, Jeongmok Cho, Hyungjoo Noh, Changsik John Pak, Hyunsuk Peter Suh, Joon Pio HongUniversity of Ulsan College of Medicine and Seoul Asan Medical Center.Republic of Korea Plastic and Reconstructive SurgeryPlast Reconstr Surg 2025; 155: 610e-617eDOI: 10.1097/PRS.0000000000011635 AbstractBackground: Primary lymphedema is characterized by lymphatic dysplasia in which one variant is Milroy disease. The association with congenital chylothorax

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Successful Treatment of Congenital Chylothorax by Early Use of Prednisolone: A Case Report

Kyoka Hirano , Koji Nakae , Manaka Matsunaga , Kentaro Ueno , Yasuhiro OkamotoKagoshima University Hospital.Japan CureusCureus 2024; 16:DOI: 10.7759/cureus.60628 AbstractCongenital chylothorax is the most common form of pleural effusion during the neonatal period; however, no treatment strategy exists. The pathogenesis and etiology of this disease are not fully understood; hence, several cases are difficult to

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Congenital lymphatic dysplasia and severe bone disease in a term neonate with a novel homozygous PIEZO1 variant

Elizabeth H. Ketchum, Charles L. Groomes, Alexis N. Ghersi, Brian B. Graziose, Sharen C. Wilson, Sidney E. Zven, Rebecca L. Hicks, William A. Langley, Michael A. Reott Jr,. John P. Schacht, Elizabeth V. Schulz, Jerri CurtisUniformed Services University. Walter Reed National Military Medical Center. MNG Laboratories.United States Clinical Case ReportsClin Case Rep 2024; 12: DOI: 10.1002/ccr3.9082

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Factors Associated with Early-Childhood Ipsilateral Perfusion Abnormalities among Patients with Congenital Diaphragmatic Hernia

Akila B. Ramaraj, Hannah V. Breitschopf, Kylie I. Holden, Vikas S. Gupta, Carrie L. Foster, Ashley H. Ebanks, Chase M. Miller, Terry L. Buchmiller, Matthew T. Harting, Rebecca A. Stark, CDH Study GroupSeattle Children’s Hospital and UConn Health. McGovern Medical School at the University of Texas Health Science Center and Children’s Memorial Hermann Hospital. Boston

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Ductus Arteriosus Patency for the Hemodynamic Management of Newborns With Pulmonary Hypertension on Veno-Venous Extracorporeal Membrane Oxygenation

Andrea Moscatelli, Isabella Buffoni, Maria E. Derchi, Francesca Bagnasco, Francesca Febbo, Elisabetta Lampugnani, Stefano Pezzato, Stefania Bianzina, Camilla Micalizzi, Lara Petrucci, Silvia Buratti, Ravi R. ThiagarajanIRCCS Istituto Giannina Gaslini. Boston Children’s Hospital.Italy and United States American Society for Artificial Internal Organs JournalASAIO J 2025;DOI: 10.1097/MAT.0000000000002437 AbstractIn neonates with pulmonary hypertension (PH) supported on veno-venous extracorporeal membrane

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