Pediatric Pulmonary Vascular Disease or Adult Pulmonary Vascular Disease

A new variant of Abernethy malformation treated by transhepatic interventional closure: a case report

Ludger Sieverding, Michael Hofbeck, Jörg Michel, Andreas Hornung, Christian Scheckenbach, Gerd Grözinger, Ekkehard Sturm, Steven W. Warmann, Anja HanserUniversity Children’s Hospital, University Hospital of Tübingen and University of Tübingen. Germany BioMed Central GastroenterologyBMC Gastroenterol 2022; 22: DOI: 10.1186/s12876-022-02123-1 AbstractBackground: Congenital portosystemic shunts (CPSS) are rare vascular malformations and can be classified into extrahepatic and intrahepatic shunts. Extrahepatic […]

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Heterogenous Disease Course and Long-Term Outcome of Children’s Interstitial Lung Disease Related to Filamin A Gene Variants

Julia Carlens, K. Taneille Johnson, Andrew Bush, Diane Renz, Ute Hehr, Florian Laenger, Claire Hogg, Martin Wetzke, Nicolaus Schwerk, Jonathan H. RaymentImperial College London and Royal Brompton Hospital. University of Regensburg. Hannover Medical School. University of British Columbia and British Columbia Children’s Hospital Research Institute.United Kingdom, Germany and Canada Annals of the American Thoracic SocietyAnn

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Neonatal intermittent hypoxia persistently impairs lung vascular development and induces long-term lung mitochondrial DNA damage

Andreas Damianos, Shathiyah Kulandavela, Pingping Chen, Patrick Nwajei, Sunil Batlahally, Mayank Sharma, Silvia Alvarez-Cubela, Juan Dominguez-Bendala, Ronald Zambrano, Jian Huang, Joshua M. Hare, Augusto Schmidt, Merline Benny, Nelson Claure, Karen YoungUniversity of Miami Miller School of Medicine.United States Journal of Applied PhysiologyJ Appl Physiol 2022; 133: 1031-1041DOI: 10.1152/japplphysiol.00708.2021 AbstractAdults born preterm have an increased risk of

Neonatal intermittent hypoxia persistently impairs lung vascular development and induces long-term lung mitochondrial DNA damage Read More »

Long-term results of the Warden procedure for right partial anomalous pulmonary venous connection

Clément Dubost, Carine Pavy, Pierre Maminirina, Nadir Benbrik, Olivier BaronHospital for Children and Adolescents.France Cardiology in the YoungCardiol Young 2023; 33: 457-462DOI: 10.1017/S1047951122001184 AbstractIntroduction: Surgery is considered as the first-line therapeutic strategy of partial anomalous pulmonary venous connection. The Warden technique has very good short-term results. The aim of this study is to evaluate the stability of

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Acute vasodilator testing: An opportunity to advance the precision care of pulmonary hypertension

Meghan M. Cirulis, Lynda O. Jorgensen, Ronald W. DayUniversity of Utah and Primary Children’s Hospital.United States Respiratory Medicine Case ReportsRespir Med Case Rep 2019; 28: DOI: 10.1016/j.rmcr.2019.100911 AbstractThe pulmonary arterial pressure of a child with severe pulmonary arterial hypertension immediately normalized while breathing nitric oxide during heart catheterization at 8 years of age. Her acute pulmonary

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A systematic review of clinical study evidence for pulmonary vasodilator therapy following surgery with cardiopulmonary bypass in children with CHD

Henry P. Foote, Christoph P. Hornik, Kevin D. Hill, Alexandre T. Rotta, Karan R. Kumar, Elizabeth J. ThompsonDuke University School of MedicineUnited States Cardiology in the YoungCardiol Young 2022; 20: DOI: 10.1017/S1047951122002293 AbstractObjectives: Complications from pulmonary hypertension are one of the leading contributors to morbidity and mortality post-cardiopulmonary bypass surgery in children with CHD. Pulmonary vasodilator therapies

A systematic review of clinical study evidence for pulmonary vasodilator therapy following surgery with cardiopulmonary bypass in children with CHD Read More »

Single-stage arterial switch operation conversion with dextro-transposition of the great arteries and pulmonary arterial hypertension due to baffle leak after a Senning procedure

Sorachi Shimada, Tomomi Uyeda, Yoshichika Maeda, Takumi Kobayashi, Kanako Kishiki, Yuji Hamamichi, Satoshi Yazaki, Naoki Wada, Yukihiro Takahashi, In-Sam Park, Tadahiro YoshikawaSakakibara Heart Institute. Asahikawa Medical University. Nishiogi Kimura Clinic.Japan Journal of Cardiology CasesJ Cardiol Cases 2022; 26: 345-347DOI: 10.1016/j.jccase.2022.07.008 AbstractPatients who have undergone an atrial switch operation for dextro-transposition of the great arteries (dTGA) sometimes

Single-stage arterial switch operation conversion with dextro-transposition of the great arteries and pulmonary arterial hypertension due to baffle leak after a Senning procedure Read More »

Congenital portosystemic shunt with multiple splenic artery aneurysms: Reversing pulmonary hypertension and preventing aneurysm rupture

Anand P. Subramanian, Adaligere Paraswanath Bharath, Ashita Barthur, Mahimarangaiah JayranganathSri Jayadeva Institute of Cardiovascular Sciences and ResearchIndia Annals of Pediatric CardiologyAnn Pediatr Cardiol 2022; 15: 300-303DOI: 10.4103/apc.apc_142_21 AbstractWe report an unusual occurrence of multiple splenic artery aneurysms and splenomegaly in a young woman with severe pulmonary hypertension, secondary to a congenital portosystemic shunt (CPS). The splenic

Congenital portosystemic shunt with multiple splenic artery aneurysms: Reversing pulmonary hypertension and preventing aneurysm rupture Read More »

Misclassification of Pulmonary Hypertension in Partial Anomalous Pulmonary Venous Return

Clifford W. Chin, David P. BichellVanderbilt University and Monroe Carell Junior Children’s HospitalUnited States Annals of Thoracic SurgeryAnn Thorac Surg 2022; 114: e447-e449DOI: 10.1016/j.athoracsur.2022.02.021 AbstractPartial anomalous pulmonary venous return is a rare congenital heart defect that can escape detection until adulthood and can be misdiagnosed as pulmonary hypertension and managed with vasodilators before the anomaly is

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Proteomics discovery of pulmonary hypertension biomarkers: Insulin-like growth factor binding proteins are associated with disease severity

Melanie K. Nies, Jun Yang, Megan Griffiths, Rachel Damico, Jie Zhu, Dhananjay Vaydia, Zongming Fu, Stephanie Brandal, Eric D. Austin, Dunbar D. Ivy, Paul M. Hassoun, Jennifer E. Van Eyk, Allen D. EverettJohns Hopkins University. Columbia University New York. Vanderbilt University. Children’s Hospital Colorado. Cedars-Sinai Medical Center.United States Pulmonary CirculationPulm Circ 2022; 12:DOI: 10.1002/pul2.12039 AbstractPulmonary arterial

Proteomics discovery of pulmonary hypertension biomarkers: Insulin-like growth factor binding proteins are associated with disease severity Read More »

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