Pediatric Pulmonary Vascular Disease or Adult Pulmonary Vascular Disease

A very rare cause of pre-capillary pulmonary hypertension: The PAMI syndrome

Manuela Iseppi, Giulio Savonitto, Alberto Tommasini, Alessia Pin, Gianfranco Sinagra, Davide Stolfozienda Sanitaria Universitaria Giuliano-Isontina (ASUGI) and University of Trieste. University of Verona. Karolinska Institutet.Italy and Sweden Pulmonary CirculationPulm Circ 2023; 13: DOI: 10.1002/pul2.12300 AbstractWe report the first known case of PAMI syndrome associated with pulmonary arterial hypertension (PAH) with a positive response to cyclophosphamide and […]

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Efficacy of a Commercial Physical Activity Monitor in Longitudinal Tracking of Patients With Pulmonary Hypertension: A Pilot Study

Eliana Rosenzweig, Gerson Antonio Valencia Villeda, Sarah Crook, Fatima Koli, Erika B. Rosenzweig, Usha S. KrishnanColumbia University Irving Medical Center and New York Presbyterian Hospital. Orlando Health Arnold Palmer Hospital for Children.United States Texas Heart Institue JournalTex Heart Inst J 2023; 50DOI: 10.14503/THIJ-22-7866 AbstractBackground: Patients with pulmonary arterial hypertension have quality-of-life limitations, decreased exercise capacity, and poor

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Fenestration: Integrating Wings Into the Atrial Septal Occluder for Navigating a Challenging Terrain

Anil K. Singhi, Soumya K. Mohapatra, Dilip Kumar, Arindam Pande, Ashesh Halder, Somnath Dey, Anish Nath, Arnab DeMedica Superspecialty Hospital. India CureusCureus 2023; 15DOI: 10.7759/cureus.45260 AbstractBackground: Atrial septal defect (ASD) closure with significant left-to-right shunt and concurrent comorbidities poses challenges for intervention. A fenestrated atrial septal defect (FASD) device is a viable option for patients who

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Exercise-Induced Electrocardiography Changes in Pulmonary Arterial Hypertension

Maya Kailas, Aimee M. Layton, Meredith Pesce, Leonardo Liberman, Thomas J. Starc, Michael A. Fremed, Robert Garafano, Erika B. Rosenzweig, Usha S. KrishnanMount Sinai Kravis Children’s Hospital. Columbia University Irving Medical Center. Yale New Haven Hospital.United States American Journal of CardiologyAm J Cardiol 2023; 208: 60-64DOI: 10.1016/j.amjcard.2023.09.014 AbstractCardiopulmonary exercise testing (CPET) is an important tool in

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Pediatric lung transplantation. Indications, techniques, and early results

Thomas L. Spray, George B. Mallory, Charles B. Canter, Charles B. HuddlestonWashington University School of Medicine.United States Journal of Thoracic and Cardiovascular SurgeryJ Thorac Cardiovasc Surg 1994; 107: 990-999DOI: Not Available AbstractFrom July 1990 to April 1993, 36 lung transplantations in 33 patients were performed in our pediatric transplant program (0.25 to 23 years, mean

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BMPR2 variant may be related to pulmonary hypertension after lung irradiation

Masako Harada, Ai Yamada, Shun Nagasawa, Naoto Yamashita, Mariko Kinoshita, Koh-Ichiro Yoshiura, Hiroshi MoritakeUniversity of Miyazaki. Nagasaki University. Japan Pediatrics InternationalPediatr Int 2023; 65DOI: 10.1111/ped.15652 AbstractNo Abstract Available CategoryGenetic Factors Associated with Pulmonary Vascular DiseaseEnvironmental Factors Associated with Pulmonary Vascular Disease Age Focus: Pediatric Pulmonary Vascular Disease or Adult Pulmonary Vascular Disease Fresh or Filed Publication:

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Long-Term Effect of TBX4 Germline Mutation on Pulmonary Clinico-Histopathologic Phenotype

Elizabeth S. Doughty, Christian Norvik, Alice Levin, Jenna Bodmer, Karin Tran-Lundmark, Steven H. Abman, Csaba GalambosThe University of Colorado and Children’s Hospital Colorado. Lund University and Wallenberg Center for Molecular Medicine.United States and Sweden Pediatric and Developmental PathologyPediatr and Dev Pathol 2023; DOI: 10.1177/10935266231199933 AbstractTbx4 protein, expressed in mesenchyme of the developing lung, contributes to airway

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Early Outcomes for In Situ Pericardial Roll Repair for Distant Anomalous Pulmonary Venous Return

Hani K. Najm, Munir Ahmad, Yezan Salam, Jared Klein, Saad M. Hasan, David Majdalany, Robert D. Stewart, Gosta Pettersson, Tara KaramlouCleveland Clinic Children’s Hospital and Cleveland Clinic. Alfaisal University.United States and Saudi Arabia Annals of Thoracic SurgeryAnn Thorac Surg 2021; 111: 169-175DOI: 10.1016/j.athoracsur.2020.03.063 AbstractBackground: Repair of anomalous pulmonary venous return (APVR) when veins are remote from the

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Right partial anomalous pulmonary venous connection to the superior vena cava following the Warden procedure

Carine Pavy, Nathaly Gavira, Pierre Maminirina, Olivier BaronUniversity Hospital Nantes.France Journal of Cardiac SurgeryJ Card Surg 2018; 33: 565-569DOI: 10.1111/jocs.13782 AbstractBackground and aims: Surgical repair of right partial pulmonary anomalous connection to the superior vena cava (SVC) with the Warden procedure can be complicated by SVC obstruction, pulmonary veins obstruction, and sinus node dysfunction. We review our

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Eisenmenger Syndrome: A Revisit of a Hidden but Catastrophic Disease

J. M. Chinawa, I. Arodiwe, J. T. Onyia, A. T. ChinawaUniversity of Nigeria/University of Nigeria Teaching Hospital. Enugu State University College of Medicine. Nigeria West African Journal of MedicineWest Afr J Med 2023; 40: 973-981DOI Not Available AbstractBackground: Eisenmenger syndrome (ES) is a rare condition seen in children with congenital heart disease (CHD). It is characterized

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