Review Articles Concerning Pulmonary Vascular Disease

Advances in the pathogenesis and clinical management of pulmonary hypertension

Yi Yan, Zhuoyuan Xu, Yanghanyue Zhou, Xike Wang, Hao ZhangShanghai Children’s Medical Center, National Children’s Medical Center and Shanghai Jiao Tong University School of Medicine. Guizhou Branch of Shanghai Children’s Medical Center and Guizhou Provincial People’s Hospital.China Medical ReviewMed Rev 2026; 6: 120-141DOI: 10.1515/mr-2026-0002 AbstractPulmonary hypertension (PH) is a severe cardiopulmonary disorder characterized by pulmonary vascular […]

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Sotatercept in Children with Pulmonary Hypertension-A Narrative Review

Johanna Schulz, Veronika C. Stark, Lars Harbaum, Rainer Kozlik-Feldmann, Thomas S. Mir, Fridrike Stute, Jakob OlfeUniversity Heart & Vascular Center Hamburg. University Medical Centre Hamburg-Eppendorf Hamburg.Germany ChildrenChildren 2026; 13: DOI: 10.3390/children13040465 AbstractBackground/objectives: Pulmonary arterial hypertension (PAH) is a rare but life-threatening disease that presents particular therapeutic challenges in children. It is characterized by pulmonary vasoconstriction and vascular

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The Importance of Sex as a Biological Variable in Pulmonary Vascular Research

Mikala Mueller, Sue Gu, Krithika Lingappan, R. Blair Dodson, Chelsea M. MaginUniversity of Colorado. Children’s Hospital of Philadelphia and University of Pennsylvania. Research Triangle Institute International.United States American Journal of Physiology Lung Cellular and Molecular PhysiologyAm J Physiol Lung Cell Mol Physiol 2026; DOI: 10.1152/ajplung.00036.2026 AbstractSex differences shape disease susceptibility, progression, and therapeutic response across human

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Bronchopulmonary Dysplasia: A Contemporary Review for Pediatric Practice

Marie Berg, Silvia Maria del Rocio Delgado-Villalta, Catalina BazacliuUniversity of Florida College of Medicine. United States Pediatrics in ReviewPediatr in Rev 2026; DOI: 10.1542/pir.2024-006701 AbstractBronchopulmonary dysplasia (BPD) remains a significant source of morbidity and mortality among preterm infants, especially those born before 28 weeks gestation. Although the survival of preterm infants has improved, the incidence of

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Pathogenesis, Evaluation, and Management of Pulmonary Vein Stenosis: JACC Review Topic of the Week

Trevor Simard, Dhruv Sarma, William R. Miranda, Charles Jain, Jason H. Anderson, Jeremy D. Collins, Abdallah El Sabbagh, Aravdeep Jhand, Tobias Peikert, Guy S. Reeder, Thomas M. Munger, Douglas L. Packer, David R. HolmesMayo Clinic.United States Journal of the American College of CardiologyJ Am Coll Cardiol 2023; 81: 2361-2373DOI: 10.1016/j.jacc.2023.04.016 AbstractPulmonary vein stenosis (PVS) can arise

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Clinical Presentations, Comorbidities, and Diagnostic Approaches in Sinus Venosus Atrial Septal Defect: A Literature Review

Dima Bsat, Dalia Safi, Jad Abdul Khalek, Issam El Rassi, Mariam ArabiAmerican University of Beirut Medical Center. Al Jalila Children’s Hospital.Lebanon and United Arab Emirates Cardiology in ReviewCardiol Rev 2026; DOI: 10.1097/CRD.0000000000001284 AbstractSinus venosus atrial septal defect is a rare congenital heart defect that is frequently associated with partial anomalous pulmonary venous return (PAPVR). This defect

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The Right Ventricle, the Forgotten Chamber or Not

Ranjini Srinivasan, Alessandro Castiglione, Michael Antonchak, Ellen OstenfeldWeill Cornell School of Medicine. Lund University and Skåne University Hospital. New York University Grossman School of Medicine.United States and Sweden Magnetic Resonance Imaging Clinics of North AmericaMagn Reson Imaging Clin N Am 2026; 34: 217-230DOI: 10.1016/j.mric.2026.01.011 AbstractRight ventricular (RV) enlargement or dysfunction evaluation is the cornerstone for diagnosis, prognostications, and treatment planning in a variety

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Pediatric Pulmonary Vein Stenosis and Treatment

Joice Prodigios, Stephanie El Omeiri, Marcus Meneses, Bethelhem Belachew, Hansel J. Otero, David M. Biko, Jordan B. RappChildren’s Hospital of Philadelphia and Perelman School of Medicine at The University of Pennsylvania.United States Seminars in RoentenologySemin Roentenol 2025;DOI: 10.1053/j.ro.2025.09.006 AbstractPulmonary vein stenosis (PVS) is an uncommon but often progressive condition in children, associated with high morbidity and

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From standard to individualized diazoxide therapy in congenital hyperinsulinism: a narrative review

Teresa Wong, Daniel Chan, Cherie Chua, Wenqi Cher, Selina Lim, Suresh Chandran, Fabian YapKK Women’s and Children’s Hospital. Duke NUS Medical School. Singapore Frontiers in PharmacologyFront Pharmacol 2026; 17:DOI: 10.3389/fphar.2026.1781424 AbstractPurpose: Congenital hyperinsulinism (CHI) is the commonest cause of persistent hypoglycaemia in neonates and infants (blood glucose <3.0 mmol/L in first 2-3 days of life; <3.5 mmol/L

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Hypertrophic Cardiomyopathy as a Key Feature of MRAS-Related Noonan Syndrome: New Case and Comprehensive Literature Review

Romain Martineau, Constance Wells, Florent Fuchs, Sophie Collardeau‐Frachon, Valentin Ruault, Sophie Colomb, Jean‐Michel Faure, Caroline Bartholmot, Marie Vincenti, Benjamin Ganne, Marjolaine WillemsUniversity Hospital of Montpellier and Montpellier University. CESP Center for Research in Epidemiology and Population Health. Hospices Civils de Lyon & Université Claude Bernard. France Prenatal DiagnosisPrenat Diagn 2026; DOI: 10.1002/pd.70134 AbstractNoonan syndrome (NS) is

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