Diagnostic Testing for Pulmonary Vascular Disease. Invasive Testing

Pulmonary Artery Pulsatility Index: A Novel Marker for Risk Assessment and Prognosis in Pediatric Idiopathic Pulmonary Arterial Hypertension

Emine Gülsah Torun, Nevin Özdemiroglu, Denizhan Bagrul, Ibrahim EceTurkish Ministry of Health, Ankara Bilkent City Hospital and Gaziantep City Hospital.Turkey Pediatric CardiologyPediatr Cardiol 2025; DOI: 10.1007/s00246-025-03970-x AbstractThe pulmonary artery pulsatility index (PAPi), calculated as (systolic pulmonary artery pressure – diastolic pulmonary artery pressure)/mean right atrial pressure). This study aimed to assess the clinical utility of PAPi […]

Pulmonary Artery Pulsatility Index: A Novel Marker for Risk Assessment and Prognosis in Pediatric Idiopathic Pulmonary Arterial Hypertension Read More »

Distinctive hemodynamic phenotype in Fontan-type circulation patients with distal esophageal varices

Luis Téllez, Luis, María Toledano, María Álvarez, Elvira Garrido-Lestache, Elena Garrido, Antonio Guerrero, Jesús Donate, Lorenzo Canova, María Torres, Cristian Perna, María Jesús del Cerro, Agustín AlbillosHospital Universitario Ramón y Cajal, IRYCIS, CIBERehd, Universidad de Alcalá. Spain HepatologyHepatology 2025;  DOI: 10.1097/HEP.0000000000001472 AbstractBackground aims: Esophageal varices (EV) are common in adults with Fontan-type circulation and may arise via

Distinctive hemodynamic phenotype in Fontan-type circulation patients with distal esophageal varices Read More »

Congenital unilateral pulmonary venous atresia with pulmonary veno-occlusive disease in contralateral lung: an unusual association

Savitri Shrivastava, James H . Moller, Jesse E . EdwardsUniversity of Minnesota.United States Pediatric CardiologyPediatr Cardiol 1986; 7: 213-219DOI: 10.1007/BF02093183 AbstractA patient presenting with the rare association of congenital unilateral pulmonary venous atresia in one lung and pulmonary veno-occlusive disease in the other is described. The patient first presented at the age of 3 1/2 years

Congenital unilateral pulmonary venous atresia with pulmonary veno-occlusive disease in contralateral lung: an unusual association Read More »

Predicting Outcomes in Pediatric Intraluminal Pulmonary Vein Stenosis Using a Comprehensive Standardized Catheterization Assessment: A Prospective Study

Ryan Callahan, Kimberlee Gauvreau, Mirjam Keochakian, Jesse J. Esch, Diego Porras, Lisa Bergersen, Rebecca Beroukhim, Michael Farias, David M. Harrild, Christina M. Ireland, Neha Kwatra, Kathy J. JenkinsChildren’s Hospital of Philadelphia and University of Pennsylvania Perelman School of Medicine. Boston Children’s Hospital and Harvard Medical School. United States Circulation Cardiovascular InterventionsCirc Cardiovasc Interv 2025; DOI: 10.1161/CIRCINTERVENTIONS.124.015002

Predicting Outcomes in Pediatric Intraluminal Pulmonary Vein Stenosis Using a Comprehensive Standardized Catheterization Assessment: A Prospective Study Read More »

Computed Tomography Angiography in Pediatric Pulmonary Hypertension: Evaluating MPA-to-Aortic Ratios as Diagnostic Markers

Ali Nazım Güzelbag, Serap Ba, Demet Kangel, Muhammet Hamza Halil Toprak, Ahmet Saki Oguz, Selin Saglam, Ibrahim Cansaran Tanıdır, Erkut ÖzturkSaglik Bilimleri University and Basaksehir Cam and Sakura City Hospital. Turkey DiagnosticsDiagnostics 2025; 15: DOI: 10.3390/diagnostics15131614 AbstractBackground: Pulmonary hypertension (PHT) is a rare but serious condition in children, requiring early diagnosis to prevent right ventricular failure. Non-invasive

Computed Tomography Angiography in Pediatric Pulmonary Hypertension: Evaluating MPA-to-Aortic Ratios as Diagnostic Markers Read More »

Impact of pulmonary artery capacitance index on early outcomes following paediatric heart transplantation

Angela M. Monafo, William A. Harris, Carolyn L. Taylor, Minoo N. Kavarana, Jason R. Buckley, Andrew J. Savage, Anthony M. Hlavacek, VarshaM. Bandisode, John F. Rhodes, John M. Costello, Shahryar M. ChowdhuryMedical University of South Carolina.  Medical University of South Carolina Shawn Jenkins Children’s Hospital.United States Cardiology in the YoungCardiol Young 2025; DOI: 10.1017/S1047951125100747 AbstractBackground: Pulmonary artery

Impact of pulmonary artery capacitance index on early outcomes following paediatric heart transplantation Read More »

Echo-Derived Right Ventricular Strain Identifies Pulmonary Hypertension in Pediatric Ventricular Assist Device Patients

Ryan S. Bishop, Tam T. Doan, Claudia Lara, Lindsay F. Eilers, Hari P. Tunuguntla, Joseph A. Spinner, Ricardo H. Pignatelli, Anitha Parthiban, James C. WilkinsonTexas Children’s Hospital and Baylor College of Medicine.United States American Society for Artificial Internal OrgansASAIO 2025; DOI: 10.1097/MAT.0000000000002489 AbstractIdentifying pulmonary hypertension in pediatric patients with continuous-flow ventricular assist device (cf-VAD) remains challenging,

Echo-Derived Right Ventricular Strain Identifies Pulmonary Hypertension in Pediatric Ventricular Assist Device Patients Read More »

Echocardiographic Prediction of Hemodynamics During Acute Vasoreactivity Testing in Pediatric Pulmonary Arterial Hypertension

Charles T. Simpkin, Benjamin S. Frank, Yuanqing Liu, Zhaozing Pan, D. Dunbar Ivy, Dale A. BurkettChildren’s Hospital Colorado and University of Colorado-Anschutz Medical Campus.United States EchocardiographyEchocardiography 2025; DOI: 10.1111/echo.70232 AbstractPurpose: In pediatric pulmonary arterial hypertension (PAH), echocardiography is frequently used to assess response to acute vasodilator therapy. We sought to evaluate whether echocardiography is sensitive enough to

Echocardiographic Prediction of Hemodynamics During Acute Vasoreactivity Testing in Pediatric Pulmonary Arterial Hypertension Read More »

The Impact of Cardiac Output Methods on the Classification of Pulmonary Hypertension

Léon Genecand, Gaëtan Simian, Mona Lichtblau, Jean‐Marc Fellrath, Julian Klug, Hugues Turbé, Christian Lovis, Stéphane Noble, Julie Wacker, Julian Müller, Roberto Desponds, Maurice Beghetti, Benoit Lechartier, David Montani, Olivier Sitbon, Silvia Ulrich, Frédéric LadorGeneva University Hospitals and University of Geneva. University Hospital of Zurich and University of Zurich. Hopital Pourtales, Reseau Hospitalier Neuchâtelois. Lausanne University

The Impact of Cardiac Output Methods on the Classification of Pulmonary Hypertension Read More »

Predicting pulmonary hemodynamics in pediatric pulmonary arterial hypertension using cardiac magnetic resonance imaging and machine learning: an exploratory pilot study

Hung Chu, Rosaria J. Ferreira, Chantal Lokhorst, Johannes M. Douwes, Meindina G. Haarman, Tineke P. Willems, Rolf M.F. Berger, Mark-Jan PloegstraBeatrix Children’s Hospital, University Medical Center Groningen and University of Groningen. Frisius Medical Center Leeuwarden.Netherlands International Journal of Cardiovascular ImagingInt J Cardiovasc Imaging 2025; DOI: 10.1007/s10554-025-03434-6 AbstractPurpose: Pulmonary arterial hypertension (PAH) significantly affects the pulmonary vasculature, requiring

Predicting pulmonary hemodynamics in pediatric pulmonary arterial hypertension using cardiac magnetic resonance imaging and machine learning: an exploratory pilot study Read More »

Scroll to Top