Diagnostic Testing for Pulmonary Vascular Disease. Invasive Testing

Mid-term prognosis and risk stratification in patients with post-operative pulmonary hypertension: Insights from the Japanese Association of Congenital Heart Disease Registry (JACPHR)

Naofumi F. Sumitomo, Taku Ishii, Keiko Uchida, Susumu Hosokawa, Reina Ishizaki, Yoshiyuki Furutani, Hidekazu Ishida, Shinichi Takatsuki, Kei Inai, Shigetoyo Kogaki, Hiroyuki Fukushima, Yuichi Tamura, Hiroyuki Yamagishi, Shozaburo Doi, on behalf of The Japanese Association of Congenital Heart Disease Registry (JACPHR) membersKeio University School of Medicine. Institute of Science Tokyo. Tokyo Medical University. Japanese Red […]

Mid-term prognosis and risk stratification in patients with post-operative pulmonary hypertension: Insights from the Japanese Association of Congenital Heart Disease Registry (JACPHR) Read More »

Finding a Path to the Heart: Right Heart Catheterization in Patients with Right Congenital Diaphragmatic Hernia and Anomalous Venous Anatomy

Teresa A. Evans, Roberta L. Keller, Anita J. Moon-Grady, David Teitel, Elena K. AminUniversity of California San Francisco and UCSF Benioff Children’s Hospital. Valley Children’s Healthcare.United States Pediatric CardiologyPediatr Cardiol 2026; DOI: 10.1007/s00246-026-04229-9 AbstractChildren with congenital diaphragmatic hernia (CDH) may require cardiac catheterization for evaluation of pulmonary hypertension. The extent of abnormal systemic venous return complicating

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Adams-Oliver syndrome with widespread CMTC and fatal pulmonary vascular disease

Ophelia Entsir Dadzie, Lidia Tyszczuk, Susan E. Holder, Fernanda Teixeira, Aikaterina Charakida, Julia Scarisbrick, Anthony ChuHammersmith Hospital.United Kingdom Pediatric DermatologyPediatr Dermatol 2007; 24: 651-653DOI: 10.1111/j.1525-1470.2007.00556.x AbstractWe report a neonate with cutis marmorata telangiectatica congenita and clinical features of Adams-Oliver syndrome in association with severe pulmonary vascular disease. We provide an overview of cutis marmorata telangiectatica congenita,

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Clinical Utility of Stroke Volume Index in Children with Idiopathic and Heritable Pulmonary Arterial Hypertension

Shinichi Takatsuki, Kinjal Parikh, Mio Sato, Yuta Kawamura, Yurika Shimizu, Reiko Kawai, Dunbar IvyToho University Omori Medical Center. Inova Children’s Hospital. University of Colorado School of Medicine.Japan and United States Pediatric CardiologyPediatr Cardiol 2026; DOI: 10.1007/s00246-026-04241-z AbstractTo determine the prognostic value of stroke volume index (SVi) in children with idiopathic and heritable pulmonary arterial hypertension (PAH).

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Pulmonary Hypertension in Pediatric Patients with Noonan Syndrome Undergoing Cardiac Catheterization

Shane L. Collins, Paul J. Critser, Kimberlee Gauvreau, Diego Porras, Amy E. Roberts, Mary P. MullenBoston Children’s Hospital and Harvard Medical School. Cincinnati Children’s Hospital and University of Cincinnati College of Medicine. United States Pediatric CardiologyPediatr Cardiol 2026; DOI: 10.1007/s00246-026-04235-x AbstractNoonan syndrome (NS) is an autosomal dominant genetic disorder associated with a high incidence of cardiovascular

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Reversing the irreversible? A case of successful surgical repair in a late-presenting aortopulmonary window with severe pulmonary hypertension

Rido Mulawarman, Ericko Ongko Joyo, Muhamad Adrin Aefiansyah Putra, Aditya Agita Sembiring, Sisca Natalia Siagian, Oktavia LilyasarUniversitas Indonesia. Indonesia Egyptian Heart JournalEgypt Heart J 2026; 78: DOI: 10.1186/s43044-026-00726-7 AbstractBackground: Aortopulmonary window (APW) is a rare congenital heart defect, accounting for only 0.2-0.6% of all congenital cardiac anomalies, and is usually identified and surgically corrected within the first

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A Large Animal Model of Heritable Pulmonary Arterial Hypertension Using Gene-edited BMPR2 Sheep

Sanjeev A. Datar, Nicholas Werry, Austin R. Brown, Devon S. Fitzpatrick, Oluwafemi Falade, Josephine F. Trott, Rachel Hutchings, Elena K. Amin, Jessica M. Morgan, Hythem Nawaytou, Gail H. Deutsch, Eric G. Johnson, Omar A. Gonzales Viera, Thomas F. Bishop, Tara Urbano, Bret R. McNabb, Eric D. Austin, Jeffery R. Fineman, and Alison L. Van EenennaamUniversity

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Beyond the Echocardiogram: Cardiac Catheterization in Infants With Bronchopulmonary Dysplasia Associated Pulmonary Hypertension

Samuel J. Gentle, Audrey HebertYale School of Medicine. Centre Hospitalier Universitaire de Quebec.United States and Canada Journal of PediatricsJ Pediatr 2026; DOI: 10.1016/j.jpeds.2026.115026 AbstractAbstract Not Available CategoryClass III. Pulmonary Hypertension Associated with Lung DiseaseDiagnostic Testing for Pulmonary Vascular Disease. Non-invasive TestingDiagnostic Testing for Pulmonary Vascular Disease. Invasive Testing Age Focus: Pediatric Pulmonary Vascular Disease Fresh or

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Increased lung vasoreactivity in children from Leadville, Colorado, after recovery from high-altitude pulmonary edema

James W. Fasules, James W. Wiggins, Robert R. WolfeUniversity of Colorado School of Medicine.United States CirculationCirculation 1985; 72: 957-962DOI: 10.1161/01.cir.72.5.957 AbstractCardiac catheterization was performed on seven children after recovery from high-altitude pulmonary edema. All were life-long residents at elevations above 10,000 feet. Three of the seven had developed pulmonary edema without antecedent travel to low altitude

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Right ventricular adaptation in congenital heart disease: Does the type of right ventricular overload matter?

Renee S. Joosen, Gregor J. Krings, Heleen B. van der Zwaan, Nefise Karaman, Marco Guglielmo, Lucas R. Celant, Marco J. W. G€otte, Michael G. Dickinson, Michiel Voskuil, Marielle C. van de Veerdonk, Johannes M. P. J. BreurUniversity Medical Center Utrecht. Amsterdam University Medical Center and University of Amsterdam. Netherlands Journal of Thoracic and Cardiovascular Surgery

Right ventricular adaptation in congenital heart disease: Does the type of right ventricular overload matter? Read More »

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