Diagnostic Testing for Pulmonary Vascular Disease. Invasive Testing

Impact of pulmonary artery capacitance index on early outcomes following paediatric heart transplantation

Angela M. Monafo, William A. Harris, Carolyn L. Taylor, Minoo N. Kavarana, Jason R. Buckley, Andrew J. Savage, Anthony M. Hlavacek, VarshaM. Bandisode, John F. Rhodes, John M. Costello, Shahryar M. ChowdhuryMedical University of South Carolina.  Medical University of South Carolina Shawn Jenkins Children’s Hospital.United States Cardiology in the YoungCardiol Young 2025; DOI: 10.1017/S1047951125100747 AbstractBackground: Pulmonary artery […]

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Echo-Derived Right Ventricular Strain Identifies Pulmonary Hypertension in Pediatric Ventricular Assist Device Patients

Ryan S. Bishop, Tam T. Doan, Claudia Lara, Lindsay F. Eilers, Hari P. Tunuguntla, Joseph A. Spinner, Ricardo H. Pignatelli, Anitha Parthiban, James C. WilkinsonTexas Children’s Hospital and Baylor College of Medicine.United States American Society for Artificial Internal OrgansASAIO 2025; DOI: 10.1097/MAT.0000000000002489 AbstractIdentifying pulmonary hypertension in pediatric patients with continuous-flow ventricular assist device (cf-VAD) remains challenging,

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Echocardiographic Prediction of Hemodynamics During Acute Vasoreactivity Testing in Pediatric Pulmonary Arterial Hypertension

Charles T. Simpkin, Benjamin S. Frank, Yuanqing Liu, Zhaozing Pan, D. Dunbar Ivy, Dale A. BurkettChildren’s Hospital Colorado and University of Colorado-Anschutz Medical Campus.United States EchocardiographyEchocardiography 2025; DOI: 10.1111/echo.70232 AbstractPurpose: In pediatric pulmonary arterial hypertension (PAH), echocardiography is frequently used to assess response to acute vasodilator therapy. We sought to evaluate whether echocardiography is sensitive enough to

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The Impact of Cardiac Output Methods on the Classification of Pulmonary Hypertension

Léon Genecand, Gaëtan Simian, Mona Lichtblau, Jean‐Marc Fellrath, Julian Klug, Hugues Turbé, Christian Lovis, Stéphane Noble, Julie Wacker, Julian Müller, Roberto Desponds, Maurice Beghetti, Benoit Lechartier, David Montani, Olivier Sitbon, Silvia Ulrich, Frédéric LadorGeneva University Hospitals and University of Geneva. University Hospital of Zurich and University of Zurich. Hopital Pourtales, Reseau Hospitalier Neuchâtelois. Lausanne University

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Predicting pulmonary hemodynamics in pediatric pulmonary arterial hypertension using cardiac magnetic resonance imaging and machine learning: an exploratory pilot study

Hung Chu, Rosaria J. Ferreira, Chantal Lokhorst, Johannes M. Douwes, Meindina G. Haarman, Tineke P. Willems, Rolf M.F. Berger, Mark-Jan PloegstraBeatrix Children’s Hospital, University Medical Center Groningen and University of Groningen. Frisius Medical Center Leeuwarden.Netherlands International Journal of Cardiovascular ImagingInt J Cardiovasc Imaging 2025; DOI: 10.1007/s10554-025-03434-6 AbstractPurpose: Pulmonary arterial hypertension (PAH) significantly affects the pulmonary vasculature, requiring

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Programmatic Approach to Outpatient Cardiac Catheterization in Children With Stable Pulmonary Arterial Hypertension

Gregory T. Adamson, Minnie N. Dasgupta, Zachary Kleiman, Lynn F. Peng, Michelle Ogawa, Vidhya Balasubramanian, Chandra Ramamoorthy, Jeffrey A. FeinsteinStanford University School of Medicine. United States Pulmonary CirculationPulm Circ 2025; 15: DOI: 10.1002/pul2.70105 AbstractWhen performing cardiac catheterization in pediatric outpatients with pulmonary arterial hypertension (PH), our approach is to allow spontaneous ventilation, minimize procedural length, and

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Reduced pulmonary arterial compliance predicts poor short-term outcome in children with pulmonary arterial hypertension independent of pulmonary vascular resistance

Eva Gouwy, Mark-Jan Ploegstra, Meindina G. Haarman, Marcus T. R. Roofthooft, Rolf M. F. Berger, Johannes M. DouwesBeatrix Children’s Hospital, University Medical Center Groningen and University of Groningen.Netherlands Frontiers in Cardiovascular MedicineFront Cardiovasc Med 2025; 12: DOI: 10.3389/fcvm.2025.1526435 AbstractBackground and study aim: Pulmonary arterial hypertension (PAH) is a progressive pulmonary vascular disease with pulmonary vascular remodelling leading

Reduced pulmonary arterial compliance predicts poor short-term outcome in children with pulmonary arterial hypertension independent of pulmonary vascular resistance Read More »

Dysregulated Tricarboxylic Acid Cycle Metabolism Is Associated With Right Ventricular Maladaptation in Pulmonary Vascular Disease

Darin T. Rosen, Todd M. Kolb, Stephen C. Mathai, Karthik Suresh, Rachel Damico, Steven Hsu, Ryan J. Tedford, Anna R. Hemnes, Jane A. Leopold, Evelyn M. Horn, Erika S. Berman‐Rosenzweig, Franz Rischard, Robert P. Frantz, Serpil C. Erzurum, Gerald J. Beck, Nicholas S. Hill, John Barnard, Samar Farha, Gabriele Grunig, Christine Jellis, Deborah H. Kwon, Reena Mehra, Margaret M. Park, W. H. Wilson Tang, Paul M. Hassoun, Catherine E. Simpson, the PVDOMICS Study GroupJohns Hopkins University. University of Miami, Medical University of South Carolina. Vanderbilt University. Brigham and Women’s Hospital. Cornell University Medical Center. Westchester Medical Center and New

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Efficacy of bubble contrast echocardiography in detecting pulmonary arteriovenous fistulas in children with univentricular heart after total cavopulmonary connection

Dai Asada, Yuma Morishita, Yoko Kawai, Yo Kajiyama, Kazuyuki IkedaKyoto Prefectural University of Medicine.Japan Cardiology in the YoungCardiol Young 2020; 30: 227-230DOI: 10.1017/S104795111900324X AbstractBackground: Development of pulmonary arteriovenous fistulas in patients with cavopulmonary anastomosis may result in a significant morbidity. Although the use of bubble contrast echocardiography with selective injection into both the branch pulmonary arteries in

Efficacy of bubble contrast echocardiography in detecting pulmonary arteriovenous fistulas in children with univentricular heart after total cavopulmonary connection Read More »

Use of a ductal occluder device as a test and then permanent closure of a large ductus arteriosus with increased pulmonary vascular resistance: a case report

Nelly Fabiani, Alexandra Heath-Freudenthal, Inge Von Alvensleben, Gabriel Echazú, Franz Freudenthal, Abraham RothmanCentro Médico Quirúrgico Boliviano Belga. University of Nevada Las Vegas and Children’s Heart Center. Bolivia and United States Cardiology in the YoungCardiol Young 2025; DOI: 10.1017/S1047951125001726 AbstractA 3-year-old girl with a large ductus arteriosus had increased pulmonary vascular resistance at cardiac catheterisation. Test occlusion

Use of a ductal occluder device as a test and then permanent closure of a large ductus arteriosus with increased pulmonary vascular resistance: a case report Read More »

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