Class 3. Pulmonary Hypertension Associated with Lung Hypoplasia

Pulmonary vasculature development in congenital diaphragmatic hernia: a novel automated quantitative imaging analysis

Emrah Aydin, Furkan Durmus, Nilhan Torlak, Marc Oria, Nilgün Güler Bayazit, Esin Öztürk Isik, Birol Aslanyürek, Jose L. PeiroCincinnati Children’s Hospital Medical Center and University of Cincinnati College of Medicine. Boğaziçi University. Yildiz Technical University.United States and Turkey Pediatric Surgery InternationalPediatr Surg Int 2024; 40:DOI: 10.1007/s00383-024-05643-x AbstractPurpose: Impaired fetal lung vasculature determines the degree of pulmonary hypertension […]

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Risk Factors for Preoperative Pneumothorax in Neonates With Isolated Left-Sided Congenital Diaphragmatic Hernia: An International Cohort Study

Kazunori Masahata, Kouji Nagata, Keita Terui, Takuya Kondo, Ashley H. Ebanks, Matthew T. Hartling, Terry L. Buchmiller, Yasunori Sato, Hiroomi Okuyama, Noriaki Usui, Congenital Diaphragmatic Hernia Study GroupOsaka University Graduate School of Medicine. Kyushu University. Chiba University. McGovern Medical School at the University of Texas Health Science Center and Children’s Memorial Hermann Hospital. Keio University.

Risk Factors for Preoperative Pneumothorax in Neonates With Isolated Left-Sided Congenital Diaphragmatic Hernia: An International Cohort Study Read More »

Increased Elastase and Matrix Metalloproteinase Levels in the Pulmonary Arteries of Infants With Congenital Diaphragmatic Hernia

Jui-Hsia Hung, Stéphanie Langlois, Meagen Weibe, Benjamin Wild, Jessica Barré-Dunn, Kyle N. CowanUniversity of Ottawa and Children’s Hospital of Eastern Ontario. Canada Journal of Pediatric SurgeryJ Pediatr Surg 2024;DOI: 10.1016/j.jpedsurg.2024.01.028 AbstractBackground: Pulmonary vascular disease (PVD) complicated with pulmonary hypertension (PH) is a leading cause of mortality in congenital diaphragmatic hernia (CDH). Unfortunately, CDH patients are often resistant

Increased Elastase and Matrix Metalloproteinase Levels in the Pulmonary Arteries of Infants With Congenital Diaphragmatic Hernia Read More »

Intra-Amniotic Sildenafil and Rosiglitazone Late in Gestation Ameliorate the Pulmonary Hypertension Phenotype in Congenital Diaphragmatic Hernia

Shino Yoshida, Olivia Eichelberger, Michael Ulis, Alexander M. Kreger, George K. Gittes, Joseph T. ChurchUniversity of Pittsburgh School of Medicine and UPMC Children’s Hospital of Pittsburgh. University of Michigan Medical School.United States Pediatric SurgeryPediatr Surg 2024;DOI: 10.1016/j.jpedsurg.2024.01.010 AbstractBackground: Pulmonary hypertension remains difficult to manage in congenital diaphragmatic hernia (CDH). Prenatal therapy may ameliorate postnatal pulmonary hypertension. We

Intra-Amniotic Sildenafil and Rosiglitazone Late in Gestation Ameliorate the Pulmonary Hypertension Phenotype in Congenital Diaphragmatic Hernia Read More »

Congenital Diaphragmatic Hernia: Pulmonary Hypertension and Pulmonary Vascular Disease

Shiran S. Moore, Roberta L. Keller, Gabriel AltitDana Dwek Children’s Hospital and Tel Aviv Sourasky Medical Center. UCSF Benioff Children’s Hospital and University of California San Francisco. McGill University Health Centre and Montreal Children’s Hospital.Israel, United States and Canada Clinics in PerinatologyClin Perinatol 2024; 51: 151-170DOI: 10.1016/j.clp.2023.10.001 AbstractThis review provides a comprehensive summary of the current

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Survival of Infants With Severe Congenital Kidney Disease After ECMO and Kidney Support Therapy

Kara Short, Martha McBride, ScottAnderson, Rachel Miller, Daryl Ingram, Carl Coghill, Brian Sims, David AskenaziChildren’s of Alabama and University of Alabama at Birmingham.United States PediatricsPediatrics 2024; DOI: 10.1542/peds.2023-062717 AbstractCongenital kidney failure not only affects the homeostatic functions of the kidney, but also affects neonatal respiratory integrity. Until recently, extracorporeal membrane oxygenation (ECMO) support was not used

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Rescuing lung development through embryonic inhibition of histone acetylation

Giangela Stokes, Zhuowei Li, Nicole Talaba, William Genthe, Maria B. Brix, Betty Pham, Mark D. Weihold, Gracia Sandok, Rebecca Hernan, Julia Wynn, Haiyang Tang, Diana M. Tabima, Allison Rodgers, Timothy A. Hacker, Naomi C. Chesler, Pan Zhang, Rabi Murad, Jason X.-J. Yuan, Yufeng Shen, Wendy K. Chung, David J. McCulleyUniversity of California, San Diego. University

Rescuing lung development through embryonic inhibition of histone acetylation Read More »

Fetal MRI-Based Mediastinal Shift Angle (MSA) and Percentage Area of Left Ventricle (pALV) as Prognostic Parameters for Congenital Diaphragmatic Hernia

Greta Thater, Lara Angermann, Silviu-Viorel Virlan, Christel Weiss, Neysan Rafat, Michael Boettcher, Julia Elrod, Tom Bayer, Oliver Nowak, Stefan O. Schönberg, Meike WeisUniversity Medical Center Mannheim. Hospital Stuttgart. Germany Journal of Clinical MedicineJ Clin Med 2024; 13:DOI: 10.3390/jcm13010268 AbstractObjective: Fetal magnetic resonance imaging (MRI) is broadly used as a method for assessing prognosis in congenital diaphragmatic hernia

Fetal MRI-Based Mediastinal Shift Angle (MSA) and Percentage Area of Left Ventricle (pALV) as Prognostic Parameters for Congenital Diaphragmatic Hernia Read More »

Predischarge death or lung transplantation in tracheostomy and ventilator dependent grade 3 bronchopulmonary dysplasia

Roy Maynard, Madeline Armstrong, Katrin O’Grady, Brooke Moore, Stephen Kurachek, George B. Mallory, William WheelerChildren’s Minnesota. Pediatric Home Service. Johns Hopkins University. Texas Children’s Hospital and Baylor College of Medicine. United States Pediatric PulmonologyPediatr Pulmonol 2024;DOI: 10.1002/ppul.26837 AbstractBackground: Premature infants surviving beyond a postmenstrual age (PMA) of 36 weeks with severe or grade 3 bronchopulmonary dysplasia (sBPD)

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LRP4 site-specific variants in the third β-propeller domain causes congenital myasthenic syndrome type 17

Tariq Al Jabry, Nadia Al-Hashmi, Basem Abdelhadi, Almundher Al-MaawaliSultan Qaboos University Hospital. Royal Hospital.Oman European Journal of Medical GeneticsEir J Med Genet 2023;DOI: 10.1016/j.ejmg.2023.104903 AbstractLRP4 is expressed in many organs. It mediates SOST-dependent inhibition of bone formation and acts as an inhibitor of WNT signaling. It is also a postsynaptic end plate cell surface receptor at

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