Class 2. Pulmonary Hypertension Associated with Pulmonary Vein Stenosis

Death or resolution: the “natural history” of pulmonary hypertension in bronchopulmonary dysplasia

Gabriel Altit, Shazia Bhombal, Rachel K. Hopper, Theresa A. Tacy, Jeffrey FeinsteinMcGill University and Montreal Children’s Hospital – McGill University Health Centre. Stanford University School of Medicine and Lucile Packard Children’s Hospital. Canada and United States Journal of PerinatologyJ Perinatol 2019; 39: 415-425DOI: 10.1038/s41372-018-0303-8 AbstractObjectives: The primary objective was to describe the early “natural history” of pulmonary […]

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Mortality in infants with bronchopulmonary dysplasia: Data from cardiac catheterization

Martina A. Steurer, Hythem Nawaytou, Elyssa Guslits, Elizabeth Colglazier, David Teitel, Jeffrey R. Fineman, Roberta L. KellerUniversity of California, San Francisco.United States Pediatric PulmonologyPediatr Pulmonol 2019; 54: 804-813DOI: 10.1002/ppul.24297 AbstractRationale: Pulmonary hypertension (PH) is relatively common in infants with severe bronchopulmonary dysplasia (BPD), however, hemodynamic data and factors associated with mortality in this patient group are sparsely

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Intervening with the Nitric Oxide Pathway to Alleviate Pulmonary Hypertension in Pulmonary Vein Stenosis

Richard W. B. van Duin, Kelly Stam, André Uitterdijk, Beatrijs Bartelds, A. H. Jan Danser, Irwin K. M. Reiss, Dirk J. Duncker, Daphne MerkusErasmus MC Rotterdam. Sophia Children’s Hospital. University Hospital, LMU Munich.Netherlands and Germany Journal of Clinical MedicineJ Clin Med 2019; 8: DOI: 10.3390/jcm8081204 AbstractPulmonary hypertension (PH) as a result of pulmonary vein stenosis (PVS)

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Is This My Home? A Palliative Care Journey Through Life and Death in the NICU: A Case Report

Aurora Walters, Jordan GrosseChildren’s Hospital ColoradoUnited States Advances in Neonatal CareAdv Neonatal Care 2020; 20: 127-135DOI: 10.1097/ANC.0000000000000697 AbstractBackground: With advancements in neonatology, patients in the neonatal intensive care unit (NICU) are living in the hospital with complex life-limiting illnesses until their first birthday or beyond. As palliative care (PC) becomes a standard of care in neonatology, a

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Infantile Scimitar Syndrome With Contralateral Pulmonary Vein Stenosis and Refractory Pulmonary Hypertension

Janelle Buysse, Ramya Deepthi Billa, Daniel McLennan, Ravi Ashwath, Aditya Badheka, Madhuradhar ChegondiUniversity of Iowa Stead Family Children’s Hospital.United States CureusCureus 2021; 13: DOI: 10.7759/cureus.17203 AbstractInfantile scimitar syndrome is associated with pulmonary hypertension which can be difficult to manage. We present a three-month-old infant with scimitar syndrome, who eventually developed refractory pulmonary hypertension, posing a significant

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Primary pulmonary vein stenosis among premature infants with single-vessel disease

Eli Zettler, Brian K. Rivera, Corey Stiver, Brian Boe, Clifford Cua, Molly K. Ball, Charles V. Smith, Jonathan L. Slaughter, Bernadette Chen, Ryan Callahan, Carl H. BackesNationwide Children’s Hospital and Ohio State University. University of Washington School of Medicine. Boston Children’s Hospital and Harvard Medical School. United States Journal of PerinatologyJ Perinatol 2021; 41: 1621-1626DOI: 10.1038/s41372-020-00830-9

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Clinical Syndromic Phenotypes and the Potential Role of Genetics in Pulmonary Vein Stenosis

Abbas H. Zaidi, Jessica M. Yamada, David T. Miller, Kerry McEnaney, Christina Ireland, Amy E. Roberts, Kimberlee Gauvreau, Kathy J. Jenkins, Ming Hui ChenBoston Children’s Hospital and Harvard Medical School.United States ChildrenChildren 2021; 8: DOI: 10.3390/children8020128 AbstractPulmonary vein stenosis (PVS) is a rare, frequently lethal disease with heterogeneous phenotypes and an unclear etiology. Limited studies have

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Pulmonary vein stenosis

Chen-Chih J. Sun, Thomas Doyle, Richard E. RingelUniversity of Maryland.United States Human PathologyHum Pathol 1995; 26: 880-886DOI: 10.1016/0046-8177(95)90011-x AbstractPulmonary vein stenosis (PVS) is a rare disorder. Accurate diagnosis often requires anatomical examination. We report four children with pulmonary vein stenosis. Autopsy showed bilateral lesions in two patients who were thought clinically to have unilateral disease. A diagnosis of PVS was made

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Predictive Factors for Postoperative Intensive Care Unit Admission and Mechanical Ventilation After Cardiac Catheterization for Pediatric Pulmonary Vein Stenosis

Wiriya Maisat, Koichi YukiBoston Children’s Hospital and Harvard Medical School.United States Journal of Cardiothoracic and Vascular AnesthesiaJ Cardiothorac Vasc Anesth 2022; 36: 2500-2508DOI: 10.1053/j.jvca.2022.02.024 AbstractObjective: To investigate the predictive factors for postoperative intensive care unit (ICU) admission and mechanical ventilation (MV) after cardiac catheterization for pediatric pulmonary vein stenosis (PVS).Design: A retrospective observational study.Setting: At a single tertiary academic

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The many faces and outcomes of pulmonary vein stenosis in early childhood

Tilman Humpl, Jeffrey Fineman, Athar M. QureshiUniversity Children’s Hospital Berne. University of California, San Francisco. Texas Children’s Hospital and Baylor College of Medicine.Switzerland and United States Pediatric PulmonologyPediatr Pulmonol 2021; 56: 649-655DOI: 10.1002/ppul.24848 AbstractPulmonary vein stenosis is a rare and poorly understood condition causing obstruction of the large pulmonary veins and of blood flow from the

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