Class 2. Pulmonary Hypertension Associated with Pulmonary Vein Stenosis

Primary pulmonary vein stenosis among premature infants with single-vessel disease

Eli Zettler, Brian K. Rivera, Corey Stiver, Brian Boe, Clifford Cua, Molly K. Ball, Charles V. Smith, Jonathan L. Slaughter, Bernadette Chen, Ryan Callahan, Carl H. BackesNationwide Children’s Hospital and Ohio State University. University of Washington School of Medicine. Boston Children’s Hospital and Harvard Medical School. United States Journal of PerinatologyJ Perinatol 2021; 41: 1621-1626DOI: 10.1038/s41372-020-00830-9 […]

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Clinical Syndromic Phenotypes and the Potential Role of Genetics in Pulmonary Vein Stenosis

Abbas H. Zaidi, Jessica M. Yamada, David T. Miller, Kerry McEnaney, Christina Ireland, Amy E. Roberts, Kimberlee Gauvreau, Kathy J. Jenkins, Ming Hui ChenBoston Children’s Hospital and Harvard Medical School.United States ChildrenChildren 2021; 8: DOI: 10.3390/children8020128 AbstractPulmonary vein stenosis (PVS) is a rare, frequently lethal disease with heterogeneous phenotypes and an unclear etiology. Limited studies have

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Pulmonary vein stenosis

Chen-Chih J. Sun, Thomas Doyle, Richard E. RingelUniversity of Maryland.United States Human PathologyHum Pathol 1995; 26: 880-886DOI: 10.1016/0046-8177(95)90011-x AbstractPulmonary vein stenosis (PVS) is a rare disorder. Accurate diagnosis often requires anatomical examination. We report four children with pulmonary vein stenosis. Autopsy showed bilateral lesions in two patients who were thought clinically to have unilateral disease. A diagnosis of PVS was made

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Predictive Factors for Postoperative Intensive Care Unit Admission and Mechanical Ventilation After Cardiac Catheterization for Pediatric Pulmonary Vein Stenosis

Wiriya Maisat, Koichi YukiBoston Children’s Hospital and Harvard Medical School.United States Journal of Cardiothoracic and Vascular AnesthesiaJ Cardiothorac Vasc Anesth 2022; 36: 2500-2508DOI: 10.1053/j.jvca.2022.02.024 AbstractObjective: To investigate the predictive factors for postoperative intensive care unit (ICU) admission and mechanical ventilation (MV) after cardiac catheterization for pediatric pulmonary vein stenosis (PVS).Design: A retrospective observational study.Setting: At a single tertiary academic

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The many faces and outcomes of pulmonary vein stenosis in early childhood

Tilman Humpl, Jeffrey Fineman, Athar M. QureshiUniversity Children’s Hospital Berne. University of California, San Francisco. Texas Children’s Hospital and Baylor College of Medicine.Switzerland and United States Pediatric PulmonologyPediatr Pulmonol 2021; 56: 649-655DOI: 10.1002/ppul.24848 AbstractPulmonary vein stenosis is a rare and poorly understood condition causing obstruction of the large pulmonary veins and of blood flow from the

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Computed tomographic parenchymal lung findings in premature infants with pulmonary vein stenosis

Barry O’Callaghan, Jenny E. Zablah, Jason P. Weinman, Erin K. Englund, Gareth J. Morgan, D. Dunbar Ivy, Benjamin S. Frank, David Andrew Mong, LaDonna J. Malone, Lorna P. BrowneChildren’s Hospital Colorado, Aurora and University of Colorado Medical SchoolUnited States Pediatric RadiologyPediatr Radiol 2023; DOI: 10.1007/s00247-023-05673-y AbstractBackground: Developmental pulmonary vein pulmonary vein stenosis in the setting of prematurity

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Treatment and prognosis of Scimitar syndrome: A retrospective analysis in a single center of East China

Kai Wang, Xinyi Xu, Tingliang Liu, Wei Gao, Ying GuoShanghai Children’s Medical Center and Shanghai Jiao Tong University. The First Affiliated Hospital of Wenzhou Medical University.China Frontiers in Cardiovascular MedicineFront Cardiovasc Med 2022; DOI: 10.3389/fcvm.2022.973796 AbstractBackground: Scimitar syndrome is a rare congenital cardiovascular malformation; its optimal management remains controversial. This study aims to present the clinical experience

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Successful rapid staged hybrid approach for obstructed total anomalous pulmonary venous connection

Sameh M. Said, Elizabeth A. Braunlin, James Berry, Ashley Loomis, Gurumurthy, HiremathMaria Fareri Children’s Hospital and Westchester Medical Center. Masonic Children’s Hospital and University of Minnesota. United States Journal of Cardiac SurgeryJ Card Surg 2022; 37: 5501-5504DOI: 10.1111/jocs.17053 AbstractObstructed total anomalous pulmonary venous connection (TAPVC) represents a true pediatric cardiac emergency. The patient may present in

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Surgical and Cardiac Catheterization Outcomes of Scimitar Syndrome Patients: A Three Decade Single-Center Experience

Emma Seymour, George Mallory, Raysa Morales-DemoriBaylor College of Medicine and Texas Children’s Hospital.United States Pediatric CardiologyPediatr Cardiol 2023; 44: 579-586DOI: 10.1007/s00246-022-02965-2 AbstractScimitar syndrome (SS) is a rare congenital condition which includes partial anomalous pulmonary venous return (PAPVR) and a variable degree of pulmonary hypoplasia. We describe the clinical features, therapeutic approach and outcomes of patients who

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Acute Pulmonary Vasodilator Testing and Long-Term Clinical Course in Segmental Pulmonary Vascular Disease

Liezl Domingo, H. Sonali Magdo, Ronald W. DayUniversity of Utah and Primary Children’s Hospital.United States Pediatric CardiologyPediatr Cardiol 2018; 39: 501-508DOI: 10.1007/s00246-017-1780-9 AbstractResults of acute pulmonary vasodilator testing (AVT) and the outcome of medical therapy have not been described in patients with segmental pulmonary vascular disease (SPVD). We sought to compare the pulmonary vasodilatory effects of

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