Class 2. Pulmonary Hypertension Associated with Pulmonary Vein Stenosis

Mutations in VCP cause Adams-Oliver syndrome with or without pulmonary hypertension

Anna Lehman, Sana Ahmed, Arezoo Mohajeri, Alison M. Berezuk, Dhiraj Mannar, Spencer Cholak, Katharine S. Tuttle, James T. Bennett, Jeanine Aparecida Magno, Mark Hannibal, Gordana Kovacevik, Vladimir Kuburovic, M.E. Suzanne Lewis, Oana Moldovan, Zoe Nelson, Salmo Raskin, Anthony M. Vandersteen, Jared C. Roach, Sriram Subramaniam, Millan S. PatelUniversity of British Columbia. University of Washington School […]

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Case Report: Cor triatriatum sinister presenting as acute decompensated heart failure in an adolescent

ZainEdeen Zyadah, Joyce Morcos, Alaa Alresheq, Salem K. Qupp, Ahmad Fatayer, Jahed BushnaqAl-Quds University. Palestine Medical Complex. Washington University of Health and Science.Palestine and Belize Frontiers in Cardiovascular MedicineFront Cardiovasc Med 2026; 13: DOI: 10.3389/fcvm.2026.1785372 AbstractBackground: Cor Triatriatum sinister (CTS) is a rare congenital cardiac anomaly caused by a fibromuscular membrane subdividing the left atrium, potentially leading

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Scimitar syndrome presenting in infancy

Charles B. Huddleston, Vernat Exil, Charles E. Canter, Eric N. MendeloffWashington University School of Medicine and St. Louis Children’s Hospital.United States Annals of Thoracic SurgeryAnn Thorac Surg 1999; 67: 154-159DOI: 10.1016/s0003-4975(98)01227-2 AbstractBackground: Scimitar syndrome has a variable presentation based on the age at which the diagnosis is made. In general, infants presenting in heart failure have a

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A Novel Rat Model for Group 2 Pulmonary Hypertension by Total Pulmonary Vein Banding: Multi-Omics Insights into Pathophysiological Mechanisms

Jin Shentu, Wenxuan Dai, Chang Chen, Jiawei Huang, Lijun Chen, Yi Yan, Han Zhang, Zhongqun Zhu, Guocheng Shi, Huiwen ChenShanghai Children’s Medical Center and Shanghai Jiao Tong University School of Medicine. China Journal of Thoracic and Cardiovascular SurgeryJ Thorac Cardiovasc Surg 2026; DOI: 10.1016/j.jtcvs.2026.01.017 AbstractObjectives: Group 2 pulmonary hypertension (PH) remains a highly morbid disease, yet no

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Secondary pulmonary hypertension in an adult patient with Ebstein anomaly post-atrial septal defect closure; can it be reversible? A case report

Ahmed Kheiwa, Vandad Saadat, Joseph Chung, Stephen Nageotte, Anees RazzoukLoma Linda University Medical Center. European Heart Journal Case ReportsEur Heart J Case Rep 2025; 9: DOI: 10.1093/ehjcr/ytaf527 AbstractBackground: Pulmonary hypertension is often a difficult to diagnose condition, in particular in younger population of patients. Early diagnosis and treatment of this condition is crucial to prevent further morbidity

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Pulmonary Hemodynamics and Long-Term Outcomes in Children with Pulmonary Hypertension-Associated Bronchopulmonary Dysplasia

Eric D. Austin, Mary P. Mullen, Catherine M. Avitabile, Usha S. Krishnan, Erika B. Rosenzweig, Roberta L. Keller, John P. Kinsella, Delphine Yung, Lea Steffes, Angela Bates, Eleni G. Elia, Lewis H. Romer, Sharon McGrath-Morrow, Meghan L. Bernier, Kenneth D. Mandl, J.Usha Raj, Lynn A. Sleeper, Steven H. AbmanVanderbilt University Medical Center. Boston Children’s Hospital

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Congenital unilateral pulmonary venous atresia with pulmonary veno-occlusive disease in contralateral lung: an unusual association

Savitri Shrivastava, James H . Moller, Jesse E . EdwardsUniversity of Minnesota.United States Pediatric CardiologyPediatr Cardiol 1986; 7: 213-219DOI: 10.1007/BF02093183 AbstractA patient presenting with the rare association of congenital unilateral pulmonary venous atresia in one lung and pulmonary veno-occlusive disease in the other is described. The patient first presented at the age of 3 1/2 years

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Congenital atresia of unilateral pulmonary veins associated with a single ventricle: a rare case report and literature review

Hsing-Yuan Lee, Betau Hwang, Pi-Chang Lee, Sheng-Ling Jan, C.C. Laura MengTaoyuan Armed Force General Hospital.Taiwan Circulation JournalCirc J 2008; 72: 1544-1546DOI: 10.1253/circj.cj-07-0516 AbstractCongenital atresia or extreme hypoplasia of individual pulmonary veins is a rare condition that is usually asymptomatic if it only involves 1 or 2 segments of the lungs. It may be fatal if it

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Unilateral pulmonary vein atresia

Y. Wang, Y. Tang, L. Sun, X. Zhang, Y. Liu, S. Xu, Y. Su, L. Zhang, X. Tang, H. Yang, Yuelin ShenHenan Children’s Hospital, Zhengzhou Children’s Hospital and Zhengzhou University. Capital Medical University and National Center for Children’s Health. Children’s Hospital of Xinjang Uygur Autonomous Region, Xinjiang Hospital of Beijing Children’s Hospital and Seventh People’s

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Management of Obstructed Complete Left Partial Anomalous Pulmonary Venous Return in a Preterm Infant

Timothy R. Harris, Joiliana Lecointe, Thomas P. Doyle, Nhue L. Do, Dana R. Janssen, Garrett N. CoyanVanderbilt University Medical Center. University of Arizona. Meharry Medical College.United States Annals of Thoracic Surgery Short ReportsAnn Thorac Surg Short Rep 2025; 3: 106-108DOI: 10.1016/j.atssr.2024.09.006 AbstractA 25-week preterm neonate was born with complete left-sided partial anomalous pulmonary venous drainage with

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