Class 2. Pulmonary Hypertension Associated with Pulmonary Vein Stenosis

Unilateral absence or extreme hypoplasia of pulmonary veins

H. M. Kingston, R. G. Patel, G. H. WatsonRoyal Manchester Children’s Hospital.United Kingdom British Heart JournalBrit Heart J 1983; 49: 148-153DOI: 10.1136/hrt.49.2.148 AbstractThree children with recurrent chest symptoms and signs caused by unilateral atresia or absence of the pulmonary veins are described, with a discussion of the seven reported cases of unilateral congenital pulmonary venous obstruction. […]

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Outcomes of surgery for simple total anomalous pulmonary venous drainage in neonates

Matthew S. Yong, Yves d’Udekem, Terry Robertson, Stephen Horton, Mithilesh Dronavalli, Christian Brizard, Robert Weintraub, Frank Shann, Michael Cheung, Igor E. KonstantinovRoyal Children’s Hospital and University of Melbourne.Australia Annals of Thoracic SurgeryAnn Thorac Surg 2011; 91: 1921-1927DOI: 10.1016/j.athoracsur.2010.12.069 AbstractBackground: Repair of total anomalous pulmonary venous drainage (TAPVD) in neonates remains a challenge as it is often associated

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Congenital unilateral pulmonary vein stenosis complicating transposition of the great arteries

Michael Vogel, Judith Ash, Richard D. Rowe, George A. Trusler, Marlene RabinovitchHospital for Sick Children and University of Toronto.Canada American Journal of CardiologyAm J Cardiol 1984; 54: 166-171DOI:https://doi.org/10.1016/0002-9149(84)90323-0 AbstractFour patients with transposition of the great arteries and unilateral pulmonary vein (PV) stenosis, all left-sided, were studied. Two patients had an intact ventricular septum (1 with

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Never Say Never: The Use of Nitric Oxide in Patients With Obstructed Pulmonary Veins: A Case Report

Victoria Sokoliuk, James A. DiNardo, Morgan L. BrownBoston Children’s Hospital.United States A and A PracticeA A Pract 2019; 12: 205-207DOI: 10.1213/XAA.0000000000000885 AbstractPulmonary vein stenosis (PVS) is a progressive disease with pulmonary hypertension (PH) as a major cause of morbidity and mortality. Traditional management of PH with inhaled nitric oxide (iNO) is typically avoided in PVS patients

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The impact of right ventricular pressure and function on survival in patients with pulmonary vein stenosis

Michelle C. Sykes, Christina Ireland, Julia E. McSweeney, Emily Rosenholm, Kristofer G. Andren, Thomas J. KulikBoston Children’s Hospital.United States Pulmonary CirculationPulm Circ 2018;DOI: 10.1177/2045894018776894 AbstractPulmonary vein stenosis (PVS) is associated with pulmonary hypertension (PH), but there is little information regarding the impact of PH on right ventricular (RV) systolic function and survival. We conducted a retrospective

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Pulmonary Vein Stenosis in Neonates with Severe Bronchopulmonary Dysplasia

Natasha L. Swier, Bernadette Richards, Clifford L. Cua, Susan K. Lynch, Han Yin, Leif D. Nelin, Charles V. Smith, Carl H. BackesOhio State University Wexner Medical Center and Nationwide Children’s Hospital. University of Washington School of Medicine.United States American Journal of PerinatologyAm J Perinatol 2016; 33: 671-677DOI: 10.1055/s-0035-1571201 AbstractObjectives: Pulmonary vein stenosis (PVS) is a rare, often lethal anomaly associated with poor outcomes.

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Congenital pulmonary venous stenosis presenting as persistent pulmonary hypertension of the newborn

Robert G. Holcomb, R. Weslie Tyson, D. Dunbar Ivy, Steven H. Abman, John P. KinsellaChildren’s Hospital, Denver.United States Pediatric PulmonologyPediatr Pulmonol 1999; 28: 301-306DOI: 10.1002/(sici)1099-0496(199910)28:4<301::aid-ppul10>3.0.co;2-m AbstractCongenital pulmonary venous stenosis (CPVS) has been previously described in older infants and children, typically manifesting as failure to thrive with congestive heart failure and subsequent respiratory deterioration. We report on

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Use of Metformin in Pulmonary Vein Stenosis after TAPVR Repair

Edward C. Kirkpatrick, Michael E. Mitchell, MD, William G. Thilly, Joseph Cava, Aoy Tomita-Mitchell, Elena V. GostjevaChildren’s Hospital of Wisconsin and Medical College of Wisconsin. Massachusetts Institute of Technology. United States Global Pediatric HealthGlob Pediatr Health 2020;DOI: 10.1177/2333794X20958924 AbstractAbstract Not Available CategoryClass II. Pulmonary Hypertension Associated with Pulmonary Vein StenosisMedical Therapy. Efficacy or Lack of EfficacyMedical Therapy. Adverse Effects or Lack of Adverse Effects Age Focus: Pediatric Pulmonary

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Obstructed Supramitral Inflow: Cor Triatriatum Sinister Presentation in Adulthood

Sara Medellin, Nelson Burbano-Vera, Andrej AlfirevicCleveland Clinic FoundationUnited States Journal of Cardiothoracic and Vascular AnesthesiaJ Cardiothorac Vasc Surg 2023; DOI: 10.1053/j.jvca.2023.11.006 AbstractCor triatriatum is a rare congenital heart defect that occurs when a fibromuscular membrane divides the atrium into two chambers, which may impair blood flow to the ventricle. When it does, the symptoms usually manifest

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Pulmonary vein stenosis: Case report and literature review

Reshma Amin, S. Kwon, Y. Moayedi, Neil SweezeyHospital for Sick Children.Canada Canadian Respiratory JournalCan Respir J 2009; 16: e77-e80DOI: 10.1155/2009/791653 AbstractBackground: Pulmonary vein stenosis is a rare cause of pulmonary hypertension, with variable onset and presentation. One or more of the four pulmonary veins can be primarily or secondarily affected. A five-month-old girl presented with respiratory distress,

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