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Case report: Progressive pulmonary artery hypertension in a case of megalencephaly-capillary malformation syndrome

Yuri Yoh, Tadashi Shiohama, Tomoko Uchida, Ryota Ebata, Hironobu Kobayashi, Kentaro Okunushi, Mitsuhiro Kato, Kazuki Watanabe, Mitsuko Nakashima, Hirotomo Saitsu, Hiromichi HamadaChiba University Hospital.  Showa University School of Medicine. Hamamatsu University School of Medicine.Japan Frontiers in GeneticsFront Genet 2023; 14DOI: 10.3389/fgene.2023.1221745 AbstractMegalencephaly-capillary malformation syndrome (MCAP, OMIM # 602501) is caused by hyperactivity of the thephosphoinositide-3-kinase (PI3K)-Vakt […]

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Frequency of acute vasodilator response (AVR) in incident and prevalent patients with pulmonary arterial hypertension: Results from the pulmonary vascular disease phenomics study

Mario Naranjo, Erika B. Rosenzweig, Anna B. Hemnes, Miriam Jacob, Ankit Desai, Nicholas S. Hill, A. Brett Larive, J. Emanuel Finet, Jane Leopold, Evelyn Horn, Robert Frantz, Frans Rischard, Serpil Erzurum, Gerald Beck, Stephen C. Mathai, Paul M. HassounJohns Hopkins University. Columbia University. Vanderbilt University Medical Center. Cleveland Clinic. University of Arizona College of Medicine.

Frequency of acute vasodilator response (AVR) in incident and prevalent patients with pulmonary arterial hypertension: Results from the pulmonary vascular disease phenomics study Read More »

Associated radiation exposure from medical imaging and excess lifetime risk of developing cancer in pediatric patients with pulmonary hypertension

Malini Mahendra, Philip Chu, Elena K. Amin, Hythem Nawaytou, James R. Duncan, Jeffrey R. Fineman, Rebecca Smith-BindmanCSF Benioff Children’s Hospital and University of California at San Francisco. Mallinckrodt Institute of Radiology Washington University School of Medicine. United States Pulmonary CirculationPulm Circ 2023; 13DOI: 10.1002/pul2.12282 AbstractPediatric patients with pulmonary hypertension (PH) receive imaging studies that use ionizing

Associated radiation exposure from medical imaging and excess lifetime risk of developing cancer in pediatric patients with pulmonary hypertension Read More »

Evaluation of paediatric pulmonary vein stenosis by cardiac CT angiography: a comparative study with transthoracic echocardiography and catheter angiogram

R. Salman, S. R. More, M. P. Ferreira Botelho, P. M. Ketwaroo, P. M. Masand, S. P. JadhavTexas Children’s Hospital and Baylor College of Medicine. Virtual Radiologic Corporation. United States Clinical RadiologyClin Radiol 2023; DOI: 10.1016/j.crad.2023.06.002 AbstractAim: To compare prospective electrocardiogram (ECG)-gated cardiac computed tomographic angiography (CCTA) with transthoracic echocardiography (TTE) and cardiac catheter angiography (CCA) for

Evaluation of paediatric pulmonary vein stenosis by cardiac CT angiography: a comparative study with transthoracic echocardiography and catheter angiogram Read More »

Outcomes and Risk Factors of Interventions for Pediatric Post-operative Pulmonary Vein Stenosis

Kristin T. Fujita, Michael P. DiLorenzo, Usha Krishnan, Mariel E. Turner, Oliver M. Barry, Alejandro J. Torres, Emile A. Bacha, David Kalfa, Matthew A. CrystalColumbia University Vagelos College of Physicians and Surgeons and New York-Presbyterian. United States Pediatric CardiologyPediatr Cardiol 2023; DOI: 10.1007/s00246-023-03214-w AbstractPulmonary vein stenosis (PVS) in children is a challenging condition with poor outcomes.

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An electrocardiographic score to predict pulmonary hypertension in children with atrial septal defect

Indah K Murni, Taichi Kato, Muhammad Taufik Wirawan, Nadya Arafuri, Kristia Hermawan, Anggoro Budi Hartopo, Dyah Wulan Anggrahini, Sasmito Nugroho, Noormanto Noormanto, Noriaki Emoto, Lucia Kris DinartiUniversitas Gadjah Mada and Dr. Sardjito Hospital. Nagoya University Graduate School of Medicine. Kobe University Graduate School of Medicine. Kobe Pharmaceutical University.Indonesia and Japan BioMed Central PediatricsBMC Pediatr 2023;

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Pulmonary vascular disease as a complication of pediatric congenital heart diseases

Julie Wacker, Raphael Joye, Leon Genecand, Frederic Lador, Maurice BeghettiGeneva University Hospitals. Centre Universitaire Romand de Cardiologie et Chirurgie Cardiaque Pédiatrique.Switzerland Translational PediatricsTransl Pediatr 2023; 12: 1041-1052DOI: 10.21037/tp-23-64 AbstractCongenital and acquired heart diseases can cause pulmonary hypertension (PH) in children, either by increasing pulmonary blood flow (PBF), left atrial pressure (LAp), and/or pulmonary vascular resistance (PVR).

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Cardiopulmonary Phenotypes and Protein Signatures in Children With Down Syndrome

Emily M. DeBoer, Kristine Wolter-Warmerdam, Robin R. Deterding, Juana Marmolejo, Tom Blumenthal, Joaquin M. Espinosa, Francis Hickey, Brandie D. WagnerUniversity of Colorado School of Medicine. United States Clinical PediatricsClin Pediatr 2023; DOI: 10.1177/00099228231179453 AbstractPulmonary disease, lower respiratory tract infection, and pneumonia are the largest causes of morbidity and mortality in individuals with Down syndrome (DS), but

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The role of rhIGF-1/BP3 in the prevention of pulmonary hypertension in bronchopulmonary dysplasia and its underlying mechanism

Sehua Qu, Lianqiang Shan, Xin Chen, Zhen Zhang, Yumeng Wu, Yun Chen, Feixiang Zhuo, Yitong Wang, Huaifu DongThe First Affiliated Hospital of Bengbu Medical College. China BioMed Central Pulmonary MedicineBMC Pulm Med 2023; 23: DOI: 10.1186/s12890-023-02498-1 AbstractBackground: This study aimed to determine whether postnatal treatment with recombinant human IGF-1 (rhIGF-1)/binding peptide 3 (BP3) ameliorates lung injury and

The role of rhIGF-1/BP3 in the prevention of pulmonary hypertension in bronchopulmonary dysplasia and its underlying mechanism Read More »

Quantitative Measures of Right Ventricular Size and Function by Echocardiogram Correlate with Cardiac Catheterization Hemodynamics in Congenital Diaphragmatic Hernia

Catherine M. Avitabile, Sabrina Flohr, Leny Mathew, Yan Wang, Devon Ash, David B. Frank, Jennifer E. Tingo, Natalie E. Rintoul, Holly L. HedrickUniversity of Pennsylvania Perelman School of Medicine and Children’s Hospital of Philadelphia. United States Journal of PediatricsJ Pediatr 2023; 261DOI: 10.1016/j.jpeds.2023.113564 AbstractObjective: To evaluate associations between cardiac catheterization (cath) hemodynamics, quantitative measures of right ventricular

Quantitative Measures of Right Ventricular Size and Function by Echocardiogram Correlate with Cardiac Catheterization Hemodynamics in Congenital Diaphragmatic Hernia Read More »

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