Vascular Cell Biology and Mechanisms of Pulmonary Vascular Disease

Novel KCNK3 variant in a child with pulmonary arterial hypertension

Yi-ming Zheng, Jia-qi Jiang, Xuan Li, Hong-biao Huang, Wen-yu Zhuo, Xuan Tang, Ying Liu, Hai-tao LvChildren’s Hospital of Soochow University. Fujian Provincial Hospital and Fujian Provincial Clinical College of Fujian Medical University. People’s Hospital of Qianxinan Buyi and Miao Minority Autonomous Prefecture. Jiangyin People’s Hospital. China HereditasHereditas 2026; DOI: 10.1186/s41065-026-00680-z AbstractBackground: Pathogenic variants in KCNK3 have […]

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Hsa_circ_0005372 function as both sponging miR-877-3p and interacting with RNA binding proteins DNMT1 to promote proliferation of human pulmonary smooth muscle cells

Danyan Su, Yuqin Huang, Bingbing Ye, Yanyun Huang, Yusheng PangFirst Affiliated Hospital of Guangxi Medical University.China Translational PediatricsTransl Pediatr 2026; 15: DOI: 10.21037/tp-2025-1-886 AbstractBackground: Circular RNAs (circRNAs) may affect pulmonary artery hypertension (PAH) by regulating the proliferation of pulmonary artery smooth muscle cells (PASMCs), but the specific mechanism has not been fully elucidated. This study aimed to

Hsa_circ_0005372 function as both sponging miR-877-3p and interacting with RNA binding proteins DNMT1 to promote proliferation of human pulmonary smooth muscle cells Read More »

Emerging significance of E3 ubiquitin ligases and Deubiquitinases in pulmonary hypertension

Chao-Wei Ding, Jia-Yong Qiu, Hui Shen, Yi Yan, Ze-Xin Liu, Shen-Shen Huang, Yue-Jiao Ma, Zhi-Cheng JingXiamen Humanity Hospital of Fujian Medical University. Second Hospital of Hebei Medical University. Guangdong Provincial People’s Hospital, Guangdong Academy of Medical Sciences and Southern Medical University. First Affiliated Hospital and College of Clinical Medicine of Henan University of Science and

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Subamnex Ameliorates Hypoxia-Induced Pulmonary Arterial Hypertension through Modulation of the STAT3/p-STAT3 Pathway

Rui-Xiang Ge, Jun-Zhuo Shi, Bin-Hao Guo, Meng-Jie Zhang, Min Zeng, Xiao-Rui An, Jing-Song Ye, Guo Cheng, Xin Fan, Meng-Wei Wang, Yun-Feng Zhou, Xi Li, Xiao-Bin Pang, Xin-Mei Xie, Hong-Da Zhang, Lu-Ling Zhao, Yang-Yang He, Jie-Jian Kou, Jing Ma, Yi YanHuaihe Hospital and Henan University. Fuwai Hospital and National Center for Cardiovascular Diseases. Shanghai Children’s Medical

Subamnex Ameliorates Hypoxia-Induced Pulmonary Arterial Hypertension through Modulation of the STAT3/p-STAT3 Pathway Read More »

An overview of the placenta’s role in the development of congenital diaphragmatic hernia

Nilhan Torlak, Marc Oria, Braxton Forde, Jose L. Peiro, Emrah AydinNew York University Grossman School of Medicine. Cincinnati Children’s Hospital Medical Center. University of Cincinnati College of Medicine. Koç University. University of Miami Miller School of Medicine.United States and Poland Frontiers in PediatricsFront Pediatr 2026; 14: DOI: 10.3389/fped.2026.1783068 AbstractCongenital diaphragmatic hernia (CDH) is a severe congenital

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Adventitial Niches, Complement and Inflammation in Pulmonary Vascular Disease: Current Status and Future Directions

Hui Zhang, Ram Raj Prasad, Sushil Kumar, Min Li, Dallas Jones, Cheng-Jun Hu, Claudia Mickael, Yen-Rei Yu, Rubin M. Tuder, Kurt R. StenmarkUniversity of Colorado Anschutz Medical Campus.United States Comprehensive PhysiologyCompre Physiol 2026; 16: DOI: 10.1002/cph4.70133 AbstractThere is strong evidence supporting inflammatory and autoimmune processes in the pathogenesis of pulmonary arterial hypertension (PAH), although the initiating

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Mitochondria-derived peptide MOTS-c alleviates hyperoxia-induced bronchopulmonary dysplasia in neonatal mice by activating Nrf2 pathway

Dan Chen, Mei-hui Zhou, Wei-ying Zhu, Zhi-xuan Xing, Sheng-peng Li, Ya-xian Wu, Xiao-lin Sun, Ping Sun, Qing-feng PangWuxi School of Medicine, Jiangnan University Medical Center and Jiangnan University. Maternity and Child Health Care Affiliated Hospital, Jiaxing University. Linyi Maternal and Child Health Hospital. China European Journal of PharmacologyEur J Pharmacol 2026; DOI: 10.1016/j.ejphar.2026.178726 AbstractOxidative stress play

Mitochondria-derived peptide MOTS-c alleviates hyperoxia-induced bronchopulmonary dysplasia in neonatal mice by activating Nrf2 pathway Read More »

The emerging role of integrin signaling in pulmonary vascular disease

Annika S. Bai, Grith Lykke Sørensen, Aparna B. Sundaram, Wenhan Chang, Rubin M. Tuder, Brian B. Graham Michael H. LeeUniversity of California Santa Barbara. University of California San Francisco. Zuckerberg San Francisco General Hospital. University of Southern Denmark. University of Colorado School of Medicine. United States and Denmark American Journal of Physiology Lung Cellular and

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Alternative Polyadenylation Signatures Distinguish Maladaptive Right Ventricular Remodeling in Pulmonary Hypertension: Implications for RNA-Based Diagnostics and Therapeutics

Janani Subramaniam, Venkata Jonnakuti, Scott D. Collum, Sandra Martineau, Kai-Lieh Huang, Sandra Breuils-Bonnet, Andrea L. Frump, Bindu H. Akkanti, Jayeshkumar A. Patel, Manish K. Patel, Ismael Salas de Armas, Isabella N. Lefebvre, Rajko Radovancevic, Elvin Blanco, Eric J. Wagner, Igor Gregoric, Sriram Nathan, Biswajit Kar, Steeve Provencher, Sebastien Bonnet, François Potus, Hari Krishna Yalamanchili, Harry

Alternative Polyadenylation Signatures Distinguish Maladaptive Right Ventricular Remodeling in Pulmonary Hypertension: Implications for RNA-Based Diagnostics and Therapeutics Read More »

A circulating MicroRNA signature for the diagnosis of pulmonary arterial hypertension and functional characterization of candidate miR-3168

Mauro Lago-Docampo, Ainhoa Iglesias-López, Carlos Vilariño, Adolfo Baloira, Joan Albert Barberá, Isabel Blanco, Diana ValverdeUniversidade de Vigo. Galicia Sur Health Research Institute. Hospital Povisa. Complejo Hospitalario Universitario de Pontevedra. University of Barcelona. Stanford University School of Medicine.Spain and United States Scientific ReportsSci Rep 2026; DOI: 10.1038/s41598-026-42550-8 AbstractPulmonary Arterial Hypertension (PAH) is a rare, progressive disorder characterized

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