Segmental Pulmonary Venous Disease. Without a Focus on Pulmonary Hypertension

Systemic Sirolimus to Prevent In-Stent Stenosis in Pediatric Pulmonary Vein Stenosis

Ryan Callahan, Jesse J. Esch, Grace Wang, Christina M. Ireland, Kimberlee Gauvreau, Kathy J. JenkinsBoston Children’s Hospital and Harvard Medical School.United States Pediatric CardiologyPediatr Cardiol 2020; 41: 282-289DOI: 10.1007/s00246-019-02253-6 AbstractEvaluate the efficacy of systemic sirolimus (rapamycin) in preventing in-stent stenosis (ISS) in pediatric intraluminal pulmonary vein stenosis (PVS). Report the adverse events related to sirolimus therapy. […]

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Progress in Pulmonary Vein Stenosis: Lessons from Success in Treating Pulmonary Arterial Hypertension

Kathy J. Jenkins, Jeffrey R. FinemanBoston Children’s Hospital. University of California, San Francisco.United States ChildrenChildren 2022; 9: DOI: 10.3390/children9060799 AbstractPulmonary vein stenosis (PVS) is a rare and poorly understood condition that can be classified as primary, acquired, status-post surgical repair of PVS, and/or associated with developmental lung disease. Immunohistochemical studies demonstrate that obstruction of the large

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Treatment of Congenital and Acquired Pulmonary Vein Stenosis

Patcharapong Suntharos, Lourdes R. PrietoNicklaus Children’s Hospital.United States Current Cardiology ReportsCurr Cardiol Rep 2020; 22: DOI: 10.1007/s11886-020-01395-x AbstractPurpose of review: Pulmonary vein stenosis (PVS) is a rare entity that until the last 2 decades was seen primarily in infants and children. Percutaneous and surgical interventions have limited success due to relentless restenosis, and mortality remains high. In

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Autologous vascularised pericardial flap tunneling technique in Scimitar syndrome repair with dextrocardia: lessons from the Senning procedure

Alain J. Poncelet, Karlien Carbonez, Jean E. RubayCliniques Universitaires Saint-Luc, Bruxelles.Belgium Cardiology in the YoungCardiol Young 2021; 31: 859-861DOI: 10.1017/S1047951120004928 AbstractScimitar syndrome is a rare variant (5%) of partial abnormal pulmonary venous return. Surgery is required when pulmonary overcirculation is present. Following repair, Scimitar vein stenosis occurs in approximately 20%. We applied a variant of the

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Longer Exposure to Left-to-Right Shunts Is a Risk Factor for Pulmonary Vein Stenosis in Patients with Trisomy 21

Connie Choi, Kimberlee Gauvreau, Philip Levy, Ryan Callahan, Kathy J. Jenkins, Minghui ChenHarvard Medical School and Boston Children’s Hospital.United States ChildrenChildren 2021; 8: DOI: 10.3390/children8010019 AbstractWe conducted a study to determine whether patients born with Trisomy 21 and left-to-right shunts who develop pulmonary vein stenosis (PVS) have a longer exposure to shunt physiology compared to those

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Effectiveness of posterior aortopexy for the left pulmonary vein obstruction between the left atrium and the descending aorta

Kwang Ho Choi, Hyungtae Kim, Si Chan Sung, Hyoung Doo Lee, Hoon Ko, Joung-Hee ByunPusan National University Yangsan Hospital. Republic of Korea Journal of Cardiac SurgeryJ Card Surg 2021; 36: 2644-2650DOI: 10.1111/jocs.15596 AbstractBackground: Left pulmonary vein (PV) obstruction can occur due to compression between the left atrium (LA) and the descending aorta (DA). One of the effective

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This and that: management of Tetralogy of Fallot and pulmonary vein stenosis in an infant-a case report

Christopher P. Scott, Kamel Shibbani, Christopher A. Caldarone, Daniel McLennanChildren’s Wisconsin. University of Iowa Stead Family Children’s Hospital. Texas Children’s Hospital.United States European Heart Journal Case ReportsEur Heart J Case Rep 2021; 5: DOI: 10.1093/ehjcr/ytab429 AbstractBackground: Tetralogy of Fallot (TOF) is the most common congenital cyanotic cardiac lesion. Pulmonary vein stenosis occurs much less commonly and remains

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Intravascular Ultrasound for Pulmonary Vein Stenosis Interventions in Congenital Heart Disease

Samantha A. Kops, Danielle Strah, Kwan S. Lee, Michael D. SeckelerUniversity of Arizona.United States Journal of Invasive CardiologyJ Invasive Cardiol 2021; 33: E259-E262DOI: Not Available AbstractObjective: Pulmonary vein stenosis (PVS) is aggressive, with high morbidity and mortality. Surgical and catheter interventions yield modest success, at best. Refinements in catheter interventions could potentially improve outcomes in this

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Preliminary findings on the use of intravascular ultrasound in the assessment of pediatric pulmonary vein stenosis

Ryan Callahan, Kathy J. Jenkins, Zachary Gauthier, Kimberlee Gauvreau, Diego PorrasBoston Children’s Hospital and Harvard Medical SchoolUnited States Catheterization and Cardiovascular InterventionsCatheter Cardiovasc Interv 2021; 97: E362-E370DOI: 10.1002/ccd.29264 AbstractObjective: Determine the feasibility of performing intravascular ultrasound (IVUS) in pediatric pulmonary vein stenosis (PVS) and investigate whether IVUS can delineate the mechanism of PVS.Background: The use of IVUS in

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Secondary Pulmonary Vein Stenosis Due to Total Anomalous Pulmonary Venous Connection Repair in Children: Extravascular MDCT Findings

Edward Y. Lee, Sara O. Vargas, Kathy J. Jenkins, Ryan Callahan, Halley J. Park, Zachary Gauthier, Abbey J. WinantBoston Children’s Hospital and Harvard Medical School.United States ChildrenChildren 2021; 8: DOI: 10.3390/children8090726 AbstractPurpose: To evaluate extravascular findings on thoracic MDCT angiography in secondary pulmonary vein stenosis (PVS) due to total anomalous pulmonary venous connection (TAPVC) repair in children.Materials

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