Segmental Pulmonary Venous Disease. Without a Focus on Pulmonary Hypertension Archives

Pulmonary Venous Decompressing Collaterals: Angiographic Characteristics and Impact on Outcomes in Pediatric Pulmonary Vein Stenosis

Ashish Saini, Hui Huang, Andrew Jergel, Rosemary Gray, Dennis W. Kim, James KuoChildren’s Healthcare of Atlanta and Emory University School of Medicine. United States Pediatric CardiologyPediatr Cardiol 2026; DOI: 10.1007/s00246-026-04350-9 AbstractPediatric pulmonary vein stenosis (PVS) is a rare, progressive condition associated with significant morbidity and mortality. While pulmonary venous decompressing collaterals (PVDC) have been described, their […]

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Therapeutic Targets for Pediatric Pulmonary Vein Stenosis: Insights from Animal Models

Siqi She, Debao Li, Qi Sun, Lincai YeShanghai Children’s Medical Center and Shanghai Jiao Tong University School of Medicine. Children’s Hospital of Fudan University and National Children’s Medical Center. China ChildrenChildren 2026; 13: DOI: 10.3390/children13050677 AbstractPulmonary vein stenosis (PVS) is a rare and devastating condition affecting infants and children, characterized by progressive intimal hyperplasia, myofibroblast proliferation,

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Transcatheter Interventional Options in Pulmonary Vein Stenosis: When to Stent?

Heidi Van Christopher J. Petit, Oliver M. BarryColumbia University Vagelos College of Physicians and Surgeons and NewYork-Presbyterian Hospital Morgan Stanley Children’s HospitalUnited States Seminars in Thoracic and Cardiovascular Surgery Pediatric Cardiac Surgery AnnualSemin Thorac Cardiovasc Surg Pediatr Card Surg Ann 2026;DOI: 10.1053/j.pcsu.2026.02.007 AbstractPulmonary vein stenosis (PVS) is a rare and aggressive condition in infants and children,

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Pulmonary Vein Stenosis Medical Therapy: Current and on the Horizon

Mudit Gupta, David B. FrankPerelman School of Medicine at the University of Pennsylvania and Children’s Hospital of PhiladelphiaUnited States Seminars in Thoracic and Cardiovascular Surgery Pediatric Cardiac Surgery AnnualSemin Thorac Cardiovasc Surg Pediatr Card Surg Ann 2026;DOI: 10.1053/j.pcsu.2026.02.006 AbstractPulmonary vein stenosis (PVS) is a severe vascular obstructive lesion historically associated with poor survival. As outcomes have

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Pathogenesis, Evaluation, and Management of Pulmonary Vein Stenosis: JACC Review Topic of the Week

Trevor Simard, Dhruv Sarma, William R. Miranda, Charles Jain, Jason H. Anderson, Jeremy D. Collins, Abdallah El Sabbagh, Aravdeep Jhand, Tobias Peikert, Guy S. Reeder, Thomas M. Munger, Douglas L. Packer, David R. HolmesMayo Clinic.United States Journal of the American College of CardiologyJ Am Coll Cardiol 2023; 81: 2361-2373DOI: 10.1016/j.jacc.2023.04.016 AbstractPulmonary vein stenosis (PVS) can arise

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Catheter and echocardiographic-focused management of primary pulmonary vein stenosis in premature infants: a single center 5-year experience

Keira Nassetta Conor P. O’Halloran, Emily Hoyt, Matthew Cornicelli, Nicolas Porta, Jeremy Fox, Alan W. Nugent, Paul Tannous, Amanda HauckAnn and Robert H. Lurie Children’s Hospital of Chicago.United States Journal of PerinatologyJ Perinatol 2026;DOI: 10.1038/s41372-026-02611-2 AbstractBackground/objectives: We describe the outcomes of pulmonary vein stenosis treatment in a cohort of premature infants using an assertive percutaneous management strategy

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Characteristics and outcomes of preterm infants with pulmonary vein stenosis in the contemporary era: a PHIS database analysis

Mohamed F. Elsisy, Fred Z. Lam, Mark M. Naguib, Mary E. Dees, James C. Gay, George T. NicholsonMonroe Carell Jr. Children’s Hospital at Vanderbilt. United States Journal of PerinatologyJ Perinatol 2026; DOI: 10.1038/s41372-026-02703-z AbstractBackground: Pulmonary vein stenosis (PVS) is increasingly recognized in preterm infants, yet data regarding characteristics and outcomes remain limited.Methods: A review of hospitalizations from 50

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Adams-Oliver syndrome with widespread CMTC and fatal pulmonary vascular disease

Ophelia Entsir Dadzie, Lidia Tyszczuk, Susan E. Holder, Fernanda Teixeira, Aikaterina Charakida, Julia Scarisbrick, Anthony ChuHammersmith Hospital.United Kingdom Pediatric DermatologyPediatr Dermatol 2007; 24: 651-653DOI: 10.1111/j.1525-1470.2007.00556.x AbstractWe report a neonate with cutis marmorata telangiectatica congenita and clinical features of Adams-Oliver syndrome in association with severe pulmonary vascular disease. We provide an overview of cutis marmorata telangiectatica congenita,

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Pediatric Pulmonary Vein Stenosis and Treatment

Joice Prodigios, Stephanie El Omeiri, Marcus Meneses, Bethelhem Belachew, Hansel J. Otero, David M. Biko, Jordan B. RappChildren’s Hospital of Philadelphia and Perelman School of Medicine at The University of Pennsylvania.United States Seminars in RoentenologySemin Roentenol 2025;DOI: 10.1053/j.ro.2025.09.006 AbstractPulmonary vein stenosis (PVS) is an uncommon but often progressive condition in children, associated with high morbidity and

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Surgical and Catheter-Based Intervention in Pediatric Pulmonary Vein Stenosis

Daiji Takajo, Paul J. Critser, Awais Ashfaq, Russel HirschCincinnati Children’s Hospital Medical Center and University of Cincinnati. University of Texas Southwestern Medical Center.United States Pediatric CardiologyPediatr Cardiol 2026;DOI: 10.1007/s00246-026-04266-4 AbstractBackground: Pulmonary vein stenosis (PVS) is a rare but serious condition in children, often requiring surgical or catheter-based interventions. The initial optimal treatment strategy remains unclear due to

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