Pulmonary Vascular Pathology

Incidence of alveolar capillary dysplasia with misalignment of pulmonary veins in infants with unexplained severe pulmonary hypertension: The roles of clinical, pathological, and genetic testing

Tetsuo Onda, Takuma Akimoto, Itaru Hayasaka, Masahiko Ikeda, Yuta Furuse, Akiko Ando, Yuichi Nakamura, Ryota Honjo, Atsushi Manabe, Itsuko Furuta, Kazutoshi ChoHokkaido University Hospital. Japan Early Human DevelopmentEarly Hum Dev 2021; 155:DOI: 10.1016/j.earlhumdev.2021.105323 AbstractBackground: Alveolar capillary dysplasia with misalignment of pulmonary veins (ACDMPV) is a rare and fatal disorder that occurs in the developing fetal lungs; at […]

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Atresia of the common pulmonary vein

Jaya R. Deshpande, Suman G. KinareSeth G.S. Medical College.India International Journal of CardiologyInt J Cardiol 1991; 30: 221-226DOI: 10.1016/0167-5273(91)90099-b AbstractIn our study of 1326 autopsied cases of congenital heart disease, we have encountered 3 cases of atresia of the common pulmonary vein. This is a rare condition of which, to the best part of our knowledge,

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Atresia of the common pulmonary vein–a rare congenital anomaly

Pradeep Vaideeswar, Milind S. Tullu, Pragati A. Sathe, Ruchi NanavatiSeth G.S. Medical College and KEM Hospital.India Congenital Heart DiseaseCongenit Heart Dis 2008; 3: 431-434DOI: 10.1111/j.1747-0803.2008.00225.x AbstractObjectives: Early atresia of the common pulmonary vein (ACPV) leads to total anomalous pulmonary venous drainage, while late atresia or incomplete absorption leads to common pulmonary vein atresia and cor triatriatum sinister

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Pulmonary vasculature development in congenital diaphragmatic hernia: a novel automated quantitative imaging analysis

Emrah Aydin, Furkan Durmus, Nilhan Torlak, Marc Oria, Nilgün Güler Bayazit, Esin Öztürk Isik, Birol Aslanyürek, Jose L. PeiroCincinnati Children’s Hospital Medical Center and University of Cincinnati College of Medicine. Boğaziçi University. Yildiz Technical University.United States and Turkey Pediatric Surgery InternationalPediatr Surg Int 2024; 40:DOI: 10.1007/s00383-024-05643-x AbstractPurpose: Impaired fetal lung vasculature determines the degree of pulmonary hypertension

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Twins with alveolar capillary dysplasia with misalignment of pulmonary veins: Strategies for diagnosis and management

Sinead Brady, Usha Krishnan, Anjali Saqi, Diana VargasNew York Presbyterian-Morgan Stanley Children’s Hospital and Columbia University Irving Medical Center.United States Journal of Neonatal-Perinatal MedicineJ Neonatal Perinatal Med 2024; 17: 147-152DOI: 10.3233/NPM-230085 AbstractWe present a case of dichorionic-diamniotic twin females who developed hypoxemic respiratory failure. They were ultimately diagnosed by lung biopsy with alveolar capillary dysplasia with

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c-Myc Drives inflammation of the maternal-fetal interface, and neonatal lung remodeling induced by intra-amniotic inflammation

April W. Tan, Xiaoying Tong, Silvia Alvarez-Cubela, Pingping Chen, Aline Guimarães Santana, Alejo A. Morales, Runxia Tian, Rae Infante, Vanessa Nunes de Paiva, Shathiyah Kulandavelu, Merline Benny, Juan Dominguez-Bendala, Shu Wu, Karen C. Young, Claudia O. Rodrigues, Augusto F. SchmidtUniversity of Miami Miller School of Medicine and Holtz Children’s Hospital. Florida Atlantic University Charles E.

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Increased Elastase and Matrix Metalloproteinase Levels in the Pulmonary Arteries of Infants With Congenital Diaphragmatic Hernia

Jui-Hsia Hung, Stéphanie Langlois, Meagen Weibe, Benjamin Wild, Jessica Barré-Dunn, Kyle N. CowanUniversity of Ottawa and Children’s Hospital of Eastern Ontario. Canada Journal of Pediatric SurgeryJ Pediatr Surg 2024;DOI: 10.1016/j.jpedsurg.2024.01.028 AbstractBackground: Pulmonary vascular disease (PVD) complicated with pulmonary hypertension (PH) is a leading cause of mortality in congenital diaphragmatic hernia (CDH). Unfortunately, CDH patients are often resistant

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Mechanism of pulmonary vein stenosis in infants with normally connected veins

Iran M. Sadr, Puay E. Tan, Mark W. Kieran, Kathy J. JenkinsChildren’s Hospital, Boston.United States American Journal of CardiologyAm J Cardiol 2000; 86: 577-579DOI: 10.1016/s0002-9149(00)01022-5 AbstractWe used microscopy, immunohistochemistry, and cell culture to identify the mechanism of restenosis in 4 infants with isolated pulmonary vein stenosis. Recurrent obstruction appears to be due to myofibroblastic proliferation in

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Case Records of the Massachusetts General Hospital. Case 23511

Tracy B. MalloryMassachusetts General Hospital.United States New England Journal of MedicineNew Eng J Med 1937; 217: 1045-1049DOI: Not Available AbstractAbstract Not Available CategoryClass II. Pulmonary Hypertension Associated with Pulmonary Vein StenosisSymptoms and Findings Associated with Pulmonary Vascular DiseasePulmonary Vascular Pathology Age Focus: Pediatric Pulmonary Vascular Disease Fresh or Filed Publication: Filed (PHiled). Greater than 1-2

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Pulmonary Hypertension in Developmental Lung Diseases

Olivier Danhaive, Csaba Galambos, Satyan Lakshminrusimha, Steven H. AbmanSaint-Luc University Hospital and University of California San Francisco. University of Colorado Anschutz School of Medicine. University of California, UC Davis Children’s Hospital.Belgium and United States Clinics in PerinatologyClin Perinatol 2024; 51: 217-235DOI: 10.1016/j.clp.2023.12.001 AbstractDiverse genetic developmental lung diseases can present in the neonatal period with hypoxemic respiratory

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