Pulmonary Lymphatic Disorders

Unilateral congenital pulmonary lymphangiectasis presenting with pneumothorax and an NRAS variant

Majid Al Teneiji, Marie-Anne Brundler, Mary Noseworthy, Kyle C. KurekAlberta Children’s Hospital and University of Calgary. Canada Pediatric PulmonologyPediatr Pulmonol 2021; 56: 2374-2376DOI: 10.1002/ppul.25401 AbstractNo Abstract Available CategoryPulmonary Lymphatic DiseaseGenetic Factors Associated with Pulmonary Vascular DiseasePulmonary Vascular Pathology Age Focus: Pediatric Pulmonary Vascular Disease Fresh or Filed Publication: Filed (PHiled). Greater than 1-2 years since publication […]

Unilateral congenital pulmonary lymphangiectasis presenting with pneumothorax and an NRAS variant Read More »

A rare case of pulmonary lymphangiectasia associated with CHD

Claudio Henriques, Ana Lai, Helena Andrade, Raquel Pina, Antonio Marinho-da-Silva, Antonio Pires Paediatric Hospital and University Hospital.Portugal Cardiology in the YoungCardiol Young 2022; 32: 132-134DOI: 10.1017/S1047951121002328 AbstractCHD may, at times, occur in the framework of other rare pathologies. These, having similar clinical manifestations, present a diagnostic dilemma for the clinician.The authors present the case of an infant

A rare case of pulmonary lymphangiectasia associated with CHD Read More »

[Diffuse pulmonary lymphangiomatosis with pleural and pericardial involvement. Pediatric case report]

Rodolfo P. Moreno, Yanina Hernández, Patricia Garrido, Bethy Camargo Vargas, Alberto Hernández, Javier Faín, Cecilia Seligra, Patricia Topp, Alberto Maffey, Gustavo CardigniSanatorio de la Trinidad Palermo. Argintina Archives of Argentina PediatricsArch Argent Pediatr 2021; 119: e264-e268DOI: 10.5546/aap.2021.e264 AbstractDiffuse pulmonary lymphangiomatosis is a rare disease characterized by marked proliferation and dilation of lymphatic vessels in the lungs,

[Diffuse pulmonary lymphangiomatosis with pleural and pericardial involvement. Pediatric case report] Read More »

MR lymphangiography of lymphatic abnormalities in children and adults with Noonan syndrome

C. C. Pieper, J. Wagenpfeil, A. Henkel, S. Geiger, T. Köster, K. Hoss, J. A. Luetkens, C. Hart, U. I. Attenberger, A. MüllerUniversity of Bonn and Children’s Hospital.Germany Scientific ReportsSci Rep 2022; 12: DOI: 10.1038/s41598-022-13806-w AbstractNoonan syndrome is associated with complex lymphatic abnormalities. We report dynamic-contrast enhanced MR lymphangiography (DCMRL) findings in children and adults with

MR lymphangiography of lymphatic abnormalities in children and adults with Noonan syndrome Read More »

Midodrine, an Oral Alpha-1 Adrenoreceptor Agonist, Successfully Treated Refractory Congenital Chylous Pleural Effusion and Ascites in a Neonate

Satoshi Tamaoka, Asami Osada, Takane Kin, Takeshi Arimitsu, Mariko HidaKeio University School of Medicine.Japan ChestChest 2021; 159: e189-e191DOI: 10.1016/j.chest.2020.10.071 AbstractA trisomy 21 neonate presented with congenital chylous pleural effusion and ascites that was refractory to conventional pharmacotherapy. Midodrine, an oral alpha-1-adrenoreceptor agonist, achieved remission of chylous effusion without any adverse effects. To the best of our

Midodrine, an Oral Alpha-1 Adrenoreceptor Agonist, Successfully Treated Refractory Congenital Chylous Pleural Effusion and Ascites in a Neonate Read More »

Non-immune hydrops fetalis secondary to congenital chylothorax with diffuse interstitial lung disease: a diagnostic conundrum

Alvin Jia Hao Ngeow, Mei Yoke Chan, Oon Hoe Teoh, Sarat Kumar Sanamandra, Daisy Kwai Lin ChanSingapore General Hospital. KK Women’s and Children’s Hospital. Singapore British Medical Journals Case ReportsBMJ Case Rep 2021; 14: DOI: 10.1136/bcr-2020-240688 AbstractA Chinese male infant was born at 35 weeks weighing 2935 g to a mother with polyhydramnios and prenatal hydrops

Non-immune hydrops fetalis secondary to congenital chylothorax with diffuse interstitial lung disease: a diagnostic conundrum Read More »

Recurrent prenatal PIEZO1-related lymphatic dysplasia: Expanding molecular and ultrasound findings

Gioia Mastromoro, Daniele Guadagnolo, Antonella Giancotti, Maria Grazia Di Gregorio, Enrica Marchionni, Flaminia Vena, Francesca Romana Lepri, Lavinia Bargiacchi, Flavia Ventriglia, Cira Di Gioia, Antonio Novelli, Antonio PizzutiSapienza University of Rome. Ospedale San Pietro Fatebenefratelli. Bambino Gesù Children’s Hospital. University of Rome.Italy European Journal of Medical Genetics Eur J Med Genet 2021; 64: DOI: 10.1016/j.ejmg.2020.104106 AbstractGeneralized

Recurrent prenatal PIEZO1-related lymphatic dysplasia: Expanding molecular and ultrasound findings Read More »

Thoracic Empyema Secondary to Congenital Chylothorax in a 14-Month-Old Boy with Noonan Syndrome

Takeru Oikawa, Chiharu Ota, Shinya Iwasawa, Takehiko Onoki, Hideyuki Ikeda, Takushi HanitaTohoku University Hospital.Japan Case Reports in PediatricsCase Rep Pediatr 2021; DOI: 10.1155/2021/6620353 AbstractThoracic empyema usually occurs as a complication of bacterial pneumonia, but in rare cases, it is caused by hematogenous dissemination secondary to nonpulmonary diseases. Congenital chylothorax or chylothorax in children is associated with

Thoracic Empyema Secondary to Congenital Chylothorax in a 14-Month-Old Boy with Noonan Syndrome Read More »

Two Cases of Congenital Chylethorax: A Successful Story of Medical Management

I. Kankananarachchi, K. K. S. Priyankara, K. K. K. Lakman, K. Withanaarachchi, P. K. G. GunathilakaUniversity of Ruhuna. Teaching Hospital Karapitiya. Sri Lanka Case Reports in PediatricsCase Rep Pediatr 2021; DOI: 10.1155/2021/6634326 AbstractCongenital chylothorax (CC) is one of the most common causes of pleural effusions in neonates. Associated ipsilateral pulmonary aplasia in CC results in neonatal

Two Cases of Congenital Chylethorax: A Successful Story of Medical Management Read More »

A case of refractory chylothorax treated with Eppikajutsuto

Juma Obayashi, Shigeyuki Furuta, Yukitsugu Nakamura, Kunihide Tanaka, Hiroaki KitagawaSt. Marianna University School of Medicine. Japan Pediatrics InternationalPediatr Int 2022; 64: DOI: 10.1111/ped.14707 AbstractNo Abstract Available CategoryPulmonary Lymphatic DiseaseMedical Therapy. Efficacy or Lack of Efficacy Age Focus: Pediatric Pulmonary Vascular Disease Fresh or Filed Publication: Filed (PHiled). Greater than 1-2 years since publication Article Access Free

A case of refractory chylothorax treated with Eppikajutsuto Read More »

Scroll to Top