Primary Pulmonary Lymphatic Disease Archives

Perinatal survival and long-term neurodevelopmental outcomes of congenital chylothorax

Hideyuki Hawaka, Tomoyuki Shimokaze, Jun Shibasaki, Hiromi Nagase, Tomoko Saito, Hiroshi Ishikawa, Katsuaki ToyoshimaKanagawa Children’s Medical Center. Hiroshima City Hiroshima Citizens Hospital. Japan Pediatric ResearchPediatr Res 2026; DOI: 10.1038/s41390-026-05271-2 AbstractBackground: Congenital chylothorax carries a poor prognosis, particularly with delivery at <32 weeks. Survival outcomes under consistent management prioritizing pregnancy prolongation despite worsening hydrops, as well as long-term […]

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Congenital chylothorax in infants: An updated scoping review

A. Alghobaishi, S. I. Albraim, H. I. Albraim, N. S. Gubari, S. Khan, H. I. Thalib, S. AlaghaKing Fahad Armed Forces Hospital. Saudi German Hospital. MyClinic. Batterjee Medical College. Saudi Arabia African Journal of Thoracic and Critical Care MedicineAfr J Thorac Crit Care Med 2026; 32: DOI: 10.7196/AJTCCM.2025.v32i1.2701 AbstractBackground: Chylothorax is a medical condition characterised by the

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Volumetric Capnography for Assessing Pre- and Post-Operative Intrapulmonary Shunt in Congenital Pulmonary Lymphangiectasia: A Case Report

Masashi Zuiki, Norihiro Iwata, Kazunori Watanabe, Akihiro Taniguchi, Maho Inoue, Kiyokazu Kin, Sayaka Yuguchi, Eisuke Ichise, Kanae Hashiguchi, Daisuke Kinoshita, Tatsuji Hasegawa, Shigeru Ono, Tomoko Ieharayoto Prefectural University of MedicineJapan Pediatric PulmonologyPediatr Pulmonol 2026; 61: DOI: 10.1002/ppul.71699 AbstractAbstract Not Available CategoryPrimary Pulmonary Lymphatic DiseaseDiagnostic Testing for Pulmonary Vascular Disease. Non-invasive Testing Age Focus: Pediatric Pulmonary Vascular

Volumetric Capnography for Assessing Pre- and Post-Operative Intrapulmonary Shunt in Congenital Pulmonary Lymphangiectasia: A Case Report Read More »

Bilateral Congenital Chylothorax With Neonatal Ventilator-Associated Pneumonia and Sepsis: Diagnostic and Therapeutic Challenges: A Case Report

Leon B. Hajdari, Melihate Çekaj, Bese R. Morina, Vlere R. MorinaUniversity of Prishtina. University Clinical Center of Kosova.Kosovo American Journal of Case ReportsAm J Case Rep 2026; DOI: 10.12659/AJCR.952519 AbstractBackground: Congenital chylothorax is a rare condition characterized by the accumulation of lymph in the pleural space. It is the most common cause of neonatal pleural effusion,

Bilateral Congenital Chylothorax With Neonatal Ventilator-Associated Pneumonia and Sepsis: Diagnostic and Therapeutic Challenges: A Case Report Read More »

Hypertrophic Cardiomyopathy as a Key Feature of MRAS-Related Noonan Syndrome: New Case and Comprehensive Literature Review

Romain Martineau, Constance Wells, Florent Fuchs, Sophie Collardeau‐Frachon, Valentin Ruault, Sophie Colomb, Jean‐Michel Faure, Caroline Bartholmot, Marie Vincenti, Benjamin Ganne, Marjolaine WillemsUniversity Hospital of Montpellier and Montpellier University. CESP Center for Research in Epidemiology and Population Health. Hospices Civils de Lyon & Université Claude Bernard. France Prenatal DiagnosisPrenat Diagn 2026; DOI: 10.1002/pd.70134 AbstractNoonan syndrome (NS) is

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Case Report: Diffuse pulmonary lymphangiomatosis in a child

Ya-nan Zhang, Zhen Yuan, Jin-chen Du, Bin Liu, Fu Li, Shou-Cai Hu, Qing-Xin Li940th Hospital of Joint Logistics Support Force of Chinese People’s Liberation Army. Gansu University of Traditional Chinese Medicine.China Frontiers in PediatricsFront Pediatr 2026; 13: DOI: 10.3389/fped.2025.1591611 AbstractWe report a rare case of generalized lymphatic anomaly (GLA) in a 12-year-old male, presenting with intermittent

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Echocardiographic diagnosis of pulmonary thromboembolism in a preterm infant presenting with congenital chylothorax

Takao Kobayashi, Sota Iwatani, Seiji YoshimotoKobe Children’s Hospital. Hokkaido University.Japan Pediatrics and NeonatologyPediatr Neonatol 2026; DOI: 10.1016/j.pedneo.2026.01.005 AbstractAbstract Not Available CategoryPrimary Pulmonary Lymphatic DiseaseAcquired Patient Factors Associated with Pulmonary Vascular DiseaseDiagnostic Testing for Pulmonary Vascular Disease. Non-invasive Testing Age Focus: Pediatric Pulmonary Vascular Disease Fresh or Filed Publication: Fresh (PHresh). Less than 1-2 years since publication

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A Rare Phenotype of X-linked Myotubular Myopathy: Hydrops Fetalis and Refractory Congenital Chylothorax with Fatal Outcome

Chousein Amet, Umut Altunoglu, Süleyman Bayraktar, Bilge Bayraktar TanyeriBiruni University. Koç University. Haseki Training and Research Hospital.Turkey Zeitschrift für Geburtshilfe und NeonatologieZ Geburtshilfe Neonatol 2026; DOI: 10.1055/a-2825-7263 AbstractAbstract Not Available CategoryPrimary Pulmonary Lymphatic DiseaseGenetic Factors Associated with Pulmonary Vascular Disease Age Focus: Pediatric Pulmonary Vascular Disease Fresh or Filed Publication: Fresh (PHresh). Less than 1-2 years

A Rare Phenotype of X-linked Myotubular Myopathy: Hydrops Fetalis and Refractory Congenital Chylothorax with Fatal Outcome Read More »

Thoracic Duct Embolization in a Case of Congenital Chylothorax

Esin Gizem Olgun, Seyhan Celik Mertese, Arzu Meltem Demir, Secahattin Bayav, Serpil Ozdemir, Mukaddes Agirtici, Zarife Kuloglu, Semra Kucuk, Ozturk, Ceyda Tuna Kirsaclioglu, Aydan Kansu, Sadik Bilgic, Nazan CobanogluAnkara University Faculty of Medicine. Turkey Pediatric PulmonologyPediatr Pulmonol 2026; 61: DOI: 10.1002/ppul.71516 AbstractAbstract Not Available CategoryPrimary Pulmonary Lymphatic DiseaseSurgical and Catheter-mediated Interventions for Pulmonary Vascular Disease Age

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Causes and risk factors for death in infants with congenital chylothorax

Yuichi Kubo, Satoshi Ibara, Takuya Tokuhisa, Masaya Kibe, Kazuyoshi Sueyoshi, Masato Kamitomo, Motoi KatoShonan Fujisawa Tokushukai Hospital. Kagoshima City Hospital. Imakiire General Hospital. Kagoshima University Hospital.Japan Frontiers in PediatricsFront Pediatr 2025; 13: DOI: 10.3389/fped.2025.1699515 AbstractAim: To identify mortality risk factors in infants with congenital chylothorax (CC) and analyze the causes of death, including pathological examination.Methods: For this single-center

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