Primary Pulmonary Lymphatic Disease Archives - Page 4 of 9

Chylothorax related to acute SARS-CoV-2 infection in a patient with Noonan syndrome with prior uncomplicated cardiac surgeries

Lubaina Ehsan, Jessica A. Thoe, John J. Parent, Joseph D. FakhouryWestern Michigan University Homer Stryker, M.D. School of Medicine and Bronson Children’s Hospital. Indiana University School of Medicine.United States Cardiology in the YoungCardiol Young 2024; 34: 448-451DOI: 10.1017/S1047951123004171 AbstractSARS-CoV-2 is a novel coronavirus that has rarely been associated with chylothorax. Patients with Noonan syndrome are at […]

PKD1L1 Is Involved in Congenital Chylothorax

Jonathan B. Whitchurch, Sophia Schneider, Alina C. Hilger, Ricarda Köllges, Jil D. Stegmann, Lea Waffenschmidt, Laura Dyer, Holger Thiele, Bhanupriya Dhabhai, Tikam Chand Dakal, Andreas Müller, Dominic P. Norris, Heiko M. ReutterHarwell Campus. University Hospital Bonn. University Hospital Erlangen. University of Cologne. Mohanlal Sukhadia University.United Kingdom, Germany and India CellsCells 2024; 13:DOI: 10.3390/cells13020149 AbstractBesides visceral heterotaxia, Pkd1l1 null

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Chylothorax Associated with the Syndrome of Idiopathic Osteolysis Including Gorham-Stout Disease: Spontaneous Remission Without Treatment

Sota Monma, Michihiro Yano, Masazumi Matsuda, Hiroyuki Tsuchie, Naoko MoriAkita University Graduate School of Medicine. Japan Turkish Archives of PediatricsTurk Arch Pediatr 2024; 59: 230-231DOI: 10.5152/TurkArchPediatr.2024.23208 AbstractAbstract Not Available CategoryPrimary Pulmonary Lymphatic DiseaseGenetic Factors Associated with Pulmonary Vascular Disease Age Focus: Pediatric Pulmonary Vascular Disease Fresh or Filed Publication: Filed (PHiled). Greater than 1-2 years since

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Pulmonary vascular changes induced by congenital obstruction of pulmonary venous return

Masato Endo, Shigeo Yamaki, Mikio Ohmi, Koichi TabayashiTohoku University School of Medicine.Japan Annals of Thoracic SurgeryAnn Thorac Surg 2000; 69: 193-197DOI: 10.1016/s0003-4975(99)01079-6 AbstractBackground: Pulmonary venous obstruction (PVO) induces pulmonary arterial hypertension, as well as pulmonary venous hypertension, and jeopardizes the repair of cardiac lesions.Methods: Four cases of congenital mitral stenosis and 4 cases of cor triatriatum (Lucas type

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The Hamman-Rich syndrome in childhood; report of a case with unilateral pulmonary arterial and venous stenosis and atriovenous occlusion

Israel DiamondChildren’s Hospital and University of Louisville School of MedicineUnited States PediatricsPediatrics 1958; 22: 279–288https://doi.org/10.1542/peds.22.2.279 AbstractThe Hamman-Rich syndrome is described in a 4-year-old Negro male. The clinical picture was that of persistent cough and progressive dyspnea beginning at 4 months of age. Diagnosis was made ante mortem by lung biopsy. The fibrotic process and arteriolosclerosis

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Unilateral congenital pulmonary lymphangiectasis presenting with pneumothorax and an NRAS variant

Majid Al Teneiji, Marie-Anne Brundler, Mary Noseworthy, Kyle C. KurekAlberta Children’s Hospital and University of Calgary. Canada Pediatric PulmonologyPediatr Pulmonol 2021; 56: 2374-2376DOI: 10.1002/ppul.25401 AbstractNo Abstract Available CategoryPrimary Pulmonary Lymphatic DiseaseGenetic Factors Associated with Pulmonary Vascular DiseasePulmonary Vascular Pathology Age Focus: Pediatric Pulmonary Vascular Disease Fresh or Filed Publication: Filed (PHiled). Greater than 1-2 years since

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A rare case of pulmonary lymphangiectasia associated with CHD

Claudio Henriques, Ana Lai, Helena Andrade, Raquel Pina, Antonio Marinho-da-Silva, Antonio PiresPaediatric Hospital and University Hospital.Portugal Cardiology in the YoungCardiol Young 2022; 32: 132-134DOI: 10.1017/S1047951121002328 AbstractCHD may, at times, occur in the framework of other rare pathologies. These, having similar clinical manifestations, present a diagnostic dilemma for the clinician.The authors present the case of an infant

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[Diffuse pulmonary lymphangiomatosis with pleural and pericardial involvement. Pediatric case report]

Rodolfo P. Moreno, Yanina Hernández, Patricia Garrido, Bethy Camargo Vargas, Alberto Hernández, Javier Faín, Cecilia Seligra, Patricia Topp, Alberto Maffey, Gustavo CardigniSanatorio de la Trinidad Palermo. Argintina Archives of Argentina PediatricsArch Argent Pediatr 2021; 119: e264-e268DOI: 10.5546/aap.2021.e264 AbstractDiffuse pulmonary lymphangiomatosis is a rare disease characterized by marked proliferation and dilation of lymphatic vessels in the lungs,

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MR lymphangiography of lymphatic abnormalities in children and adults with Noonan syndrome

C. C. Pieper, J. Wagenpfeil, A. Henkel, S. Geiger, T. Köster, K. Hoss, J. A. Luetkens, C. Hart, U. I. Attenberger, A. MüllerUniversity of Bonn and Children’s Hospital.Germany Scientific ReportsSci Rep 2022; 12: DOI: 10.1038/s41598-022-13806-w AbstractNoonan syndrome is associated with complex lymphatic abnormalities. We report dynamic-contrast enhanced MR lymphangiography (DCMRL) findings in children and adults with

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Midodrine, an Oral Alpha-1 Adrenoreceptor Agonist, Successfully Treated Refractory Congenital Chylous Pleural Effusion and Ascites in a Neonate

Satoshi Tamaoka, Asami Osada, Takane Kin, Takeshi Arimitsu, Mariko HidaKeio University School of Medicine.Japan ChestChest 2021; 159: e189-e191DOI: 10.1016/j.chest.2020.10.071 AbstractA trisomy 21 neonate presented with congenital chylous pleural effusion and ascites that was refractory to conventional pharmacotherapy. Midodrine, an oral alpha-1-adrenoreceptor agonist, achieved remission of chylous effusion without any adverse effects. To the best of our

Midodrine, an Oral Alpha-1 Adrenoreceptor Agonist, Successfully Treated Refractory Congenital Chylous Pleural Effusion and Ascites in a Neonate Read More »