Pulmonary Arteriovenous Malformations

Abnormalities in the Von Willebrand-Angiopoietin Axis Contribute to Dysregulated Angiogenesis and Angiodysplasia in Children With a Glenn Circulation

Carlo R. Bartoli, Samson Hennessy-Strahs, Robert D. Dowling, J. William Gaynor, Andrew C. GlatzHospital of the University of Pennsylvania, Children’s Hospital of Philadelphia and University of Pennsylvania. Penn State University College of Medicine.United States Journal of the American College of Cardiology Basic Translational ScienceJACC Basic Transl Sci 2021; 6: 222-235DOI: 10.1016/j.jacbts.2020.12.014 AbstractChildren with a bidirectional superior […]

Abnormalities in the Von Willebrand-Angiopoietin Axis Contribute to Dysregulated Angiogenesis and Angiodysplasia in Children With a Glenn Circulation Read More »

Hepatopulmonary Syndrome and Multiple Arteriovenous Fistulas in a Child with Niemann-Pick Disease

Zeynep Reyhan Onay, Tugba Ramasli Gursoy, Ayse Tana Aslan, Tugba Sismanlar Eyuboglu, Koray AkkanGazi University. Turkey Pediatric Allergy Immunology and PulmonologyPediatr Allergy Immunol Pulmonol 2021; 34: 30-32DOI: 10.1089/ped.2020.1244 AbstractBackground: Niemann-Pick disease (NPD) is caused by abnormal storage of sphingomyelin. NPD may affect the pulmonary system and cause hypoxia. In the present case, both hepatopulmonary syndrome (HPS) and

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sVEGFR1 Is Enriched in Hepatic Vein Blood-Evidence for a Provisional Hepatic Factor Candidate?

Andrew D. Spearman, Ankan Gupta, Amy Y. Pan, Todd M. Gudausky, Susan R. Foerster, G. Ganesh Konduri, Ramani RamchandranMedical College of Wisconsin and Children’s Wisconsin. United States Frontiers in PediatricsFront Pediatr 2021; 9: DOI: 10.3389/fped.2021.679572 AbstractBackground: Pulmonary arteriovenous malformations (PAVMs) are common sequelae of palliated univentricular congenital heart disease, yet their pathogenesis remain poorly defined. In this

sVEGFR1 Is Enriched in Hepatic Vein Blood-Evidence for a Provisional Hepatic Factor Candidate? Read More »

Mutational and clinical spectrum of Japanese patients with hereditary hemorrhagic telangiectasia

Kana Kitayama, Tomoya Ishiguro, Masaki Komiyama, Takayuki Morisaki, Hiroko Morisaki, Gaku Minase, Kohei Hamanaka, Satoko Miyatake, Naomichi Matsumoto, Masaru Kato, Toru Takahashi and Tohru YorifujiChildren’s Medical Center and Osaka City General Hospital. The University of Tokyo. National Cerebral and Cardiovascular Center. Sakakibara Heart Institute. Yokohama City University Graduate School of Medicine. Japan BioMed Central Medical

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Pulmonary arteriovenous malformation with unexplained cyanosis as the first presentation of hereditary haemorrhagic telangiectasia, case report, and literature review

Ali Alakhfash, Abdullah Alqwaiee, Abdulrahman Almesned, Zuhair N. Al-HassnanPrince Sultan cardiac Center-Qassim. Sapienza Università di Roma. King Faisal Specialist Hospital & Research Centre. Saudi Arabia and Italy European Heart Journal Case ReportsEur Heart J Case Rep 2021; 22: DOI: 10.1093/ehjcr/ytab261 AbstractBackground: Pulmonary arteriovenous malformations (PAVMs) are rare pulmonary vascular anomalies. They can result in right-to-left shunt and,

Pulmonary arteriovenous malformation with unexplained cyanosis as the first presentation of hereditary haemorrhagic telangiectasia, case report, and literature review Read More »

Pulmonary arterial hypertension associated with pulmonary arteriovenous malformations and pulmonary veno-occlusive disease: A devastating combination

Baukje M. Zaaijera, Nienke Duppena, Brigitte W. M. Willemseb, Martijn V. Verhagenc, Marcus T. R. Roofthoofta, WimT imensd, Rolf M. F. Bergera, Johannes M. DouwesUniversity of Groningen, University Medical Center Groningen, Beatrix Children’s Hospital.Netherlands Respiratory Medicine Case ReportsRespir Med Case Rep 2021; 34: DOI: 10.1016/j.rmcr.2021.101564 AbstractWe describe a case of an adolescent male with the rare

Pulmonary arterial hypertension associated with pulmonary arteriovenous malformations and pulmonary veno-occlusive disease: A devastating combination Read More »

Pulmonary Arteriovenous Malformations Incidentalloma in a 10-Years-Old Child

Daoud Ali Mohamed, Amarkak Waiss, Behyamet Onka, Walid Mohamed, Nazik Allali, Latifa Chat, Siham El HaddadUniversity Hospital of Ibn Sina Rabat. Morroco Global Pediatric HealthGlob Pediatr Health 2021; 3: DOI: 10.1177/2333794X211051186 AbstractPulmonary Arteriovenous Malformations (PAVMs) are structurally abnormal vascular communications between pulmonary arteries and pulmonary veins, which bypass the normal capillary bed and cause a low

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Preservation of Antegrade Pulmonary Blood Flow in Kawashima Procedure With Prior Right Ventricular Outflow Tract Stent

Suneet Bhansali, Puneet Bhatla, Michael Argilla, Sunil Saharan, Ralph Mosca, Tk Susheel KumarLangone Medical Center.United States World Journal of Pediatric and Congenital Heart SurgeryWorld J Pediatr Congenit Heart Surg 2022; 13: 521-523DOI: 10.1177/21501351221080171 AbstractSurgical management of single ventricle with interrupted inferior vena cava and azygos continuation typically requires a Kawashima procedure with subsequent completion of Fontan.

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Pearls & Oy-sters: Cerebral Abscess Secondary to Pulmonary Arteriovenous Malformation in Hereditary Hemorrhagic Telangiectasia

Jodie I. Roberts, Kristine Woodward, Adam Kirton, Michael J. EsserUniversity of Calgary; Alberta Children’s Hospital Research Institute.Canada NeurologyNeurology 2022; 98: 292-295DOI: 10.1212/WNL.0000000000013181 AbstractHereditary hemorrhagic telangiectasia (HHT) is an autosomal dominant condition that is linked to a myriad of neurologic complications arising from vascular malformations of the brain, spinal cord, and lungs. Our case describes a previously

Pearls & Oy-sters: Cerebral Abscess Secondary to Pulmonary Arteriovenous Malformation in Hereditary Hemorrhagic Telangiectasia Read More »

Three-dimensional rotational angiography utility in imaging and intervention in a case of pulmonary arteriovenous malformation

Neeraj Awasthy, Amol GuptaMax Hospital.India Annals of Pediatric CardiologyAnn Pediatr Cardiol 2021; 14: 533-535DOI: 10.4103/apc.APC_111_18 AbstractPulmonary arteriovenous malformation (PAVM) is an abnormal communication between the pulmonary artery and the pulmonary vein. PAVMs are usually congenital in origin; however, they may be acquired. Three-dimensional rotational angiography (3DRA) is a technique used increasingly for imaging in congenital heart

Three-dimensional rotational angiography utility in imaging and intervention in a case of pulmonary arteriovenous malformation Read More »

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