Pediatric Pulmonary Vascular Disease

Intra-Amniotic Sildenafil and Rosiglitazone Late in Gestation Ameliorate the Pulmonary Hypertension Phenotype in Congenital Diaphragmatic Hernia

Shino Yoshida, Olivia Eichelberger, Michael Ulis, Alexander M. Kreger, George K. Gittes, Joseph T. ChurchUniversity of Pittsburgh School of Medicine and UPMC Children’s Hospital of Pittsburgh. University of Michigan Medical School.United States Pediatric SurgeryPediatr Surg 2024;DOI: 10.1016/j.jpedsurg.2024.01.010 AbstractBackground: Pulmonary hypertension remains difficult to manage in congenital diaphragmatic hernia (CDH). Prenatal therapy may ameliorate postnatal pulmonary hypertension. We […]

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First locus for primary pulmonary vein stenosis maps to chromosome 2q

Ingrid van de Laar, Marja Wessels, Ingrid Frohn-Mulder, Michiel Dalinghaus, Bianca de Graaf, Marianne van Tienhoven, Paul van der Moer, Margreet Husen-Ebbinge, Maarten Lequin, Dennis Dooijes, Ronald de Krijger, Ben A. Oostra, Aida M. Bertoli-AvellaErasmus Medical Center. Medical Center Rijnmond-Zuid. Netherlands European Heart JournalEur Heart J 2009; 30: 2485–2492DOI: 10.1093/eurheartj/ehp271 AbstractAims: Primary pulmonary vein stenosis (PVS) is

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Younger age at initiation of subcutaneous treprostinil is associated with better response in pediatric Group 1 pulmonary arterial hypertension

Justin J. Kochanski, Jeffrey A. Feinstein, Michelle Ogawa, Victor Ritter, Rachel K. Hopper, Gregory T. AdamsonStanford University School of Medicine.United States Pulmonary CirculationPulm Circ 2024; DOI: 10.1002/pul2.12328 AbstractChildren with severe Group 1 pulmonary arterial hypertension (PAH) have an unpredictable response to subcutaneous treprostinil (TRE) therapy, which may be influenced by age, disease severity, or other unknown

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Novel use of the double kissing crush technique to stent complex pulmonary artery stenosis in a child with Alagille syndrome

Danielle D. Strah, Riley D. Hellinger, Kwan S. Lee, Michael D. SeckelerUniversity of Arizona. Rady Children’s Hospital.United States Annals of Pediatric CardiologyAnn Pediatr Cardiol 2023; 6: 290-292DOI: 10.4103/apc.apc_60_23 AbstractCoronary bifurcation lesions and treatment with two-stent techniques have been developed, including the double kissing (DK) crush technique. The use of this technique in children or noncoronary vessels,

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Successful treatment of pulmonary arterial hypertension in a 2-month-old female infant with incontinentia pigmenti: A case report

Marta Marcia, Paola Coppo, Giuseppe Alberto Annoni, Gaetana Ferraro, Gabriella Agnoletti, Giuseppe Antonio MazzaCity of Health and Science Hospital.Italy Annals of Pediatric CardiologyAnn Pediatr Cardiol 2023; 16: 297-300DOI: 10.4103/apc.apc_75_23 AbstractIncontinentia pigmenti (IP) is a rare X-linked dominant neuroectodermal dysplasia affecting almost exclusively females. It is caused by loss-of-function mutations in the inhibitor of kappa light polypeptide

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Successful hybrid management of hypertensive patent ductus arteriosus with unilateral absence of the right pulmonary artery – A case report

Jayitri Mazumder, Debasree Gangopadhyay, Mahua Roy, Anoop Singh, Somrita Laha, Joyeeta DuttaRabindranath Tagore International Institute of Cardiac Sciences.India Annals of Pediatric CardiologyAnn Pediatr Cardiol 2023; 16: 293-296DOI: 10.4103/apc.apc_54_23 AbstractUnilateral absence of pulmonary artery (UAPA) can be either isolated or associated with other congenital cardiac defects. It is a rare congenital lesion with a diverse clinical presentation.

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Case Records of the Massachusetts General Hospital. Case 23511

Tracy B. MalloryMassachusetts General Hospital.United States New England Journal of MedicineNew Eng J Med 1937; 217: 1045-1049DOI: Not Available AbstractAbstract Not Available CategoryClass II. Pulmonary Hypertension Associated with Pulmonary Vein StenosisSymptoms and Findings Associated with Pulmonary Vascular DiseasePulmonary Vascular Pathology Age Focus: Pediatric Pulmonary Vascular Disease Fresh or Filed Publication: Filed (PHiled). Greater than 1-2

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Transient abnormal myelopoiesis requiring advanced neonatal intensive care treatment

Maria Chalia, Emilie Seager, Anupama Rao, Simon HannamGreat Ormond Street Hospital for Children.United Kingdom Acta PaediatricaActa Paediatr 2024; DOI: 10.1111/apa.17142 AbstractAim: Five to thirty percent of neonates with trisomy 21 develop transient abnormal myelopoiesis (TAM) with a high mortality rate. The aim of the study was to identify contributing factors that determine mortality and need for chemotherapy

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[Clinical and genetic analysis of a patient with HUPRA syndrome due to missense variants of SARS2 gene and literature review]

J. Huang, Q. Y. Li. W. Ji, X.F. Guo, X. H. HuFujian Children’s Hospital. Beijing Anzhen Hospital and Capital Medical University. Shanghai Jiaotong University School of Medicine and Shanghai Children’s Medical Center. Fujian Provincial Maternity and Children’s Hospital. Xinhua Hospital.China Zhonghua Xin Xue Guan Bing Za Zhi 2024; 52: 172-179DOI: 10.3760/cma.j.cn112148-20231009-00268 Abstract (English)Objective: To explore the clinical

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Inhaled Nitric Oxide in Neonatal Pulmonary Hypertension

Michael W. Cookson, John P. KinsellaUniversity of Colorado Anschutz School of Medicine and Children’s Hospital Colorado.United States Clinics in PerinatologyClin Perinatol 2024; 51: 95-111DOI: 10.1016/j.clp.2023.11.001 AbstractPivotal trials investigating the use of inhaled nitric oxide (iNO) in the 1990s led to approval by the Food and Drug Administration in 1999. Inhaled nitric oxide is the only approved

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