Pediatric Pulmonary Vascular Disease

A Four-Week-Old Infant With Respiratory Distress: An Emergency Department Case Presentation of Congenital Lobar Emphysema

Kimberly L. Moulton, Andrea FangStanford University.United States CureusCureus 2021; 13: DOI: 10.7759/cureus.13814 AbstractCongenital lobar emphysema (CLE) and congenital pulmonary lymphangiectasis (CPL) are rare conditions that are most often identified with prenatal ultrasonography. Occasionally, this disease process is first identified in the emergency department (ED), where the physician should avoid common pitfalls in order to prevent acute […]

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Case Report: A Relatively Mild Presentation of Unilateral Congenital Pulmonary Lymphangiectasia

Dionne Adair, Raja Rabah, Maria Ladino-Torres, Thomas G. SabaCS Mott Children’s Hospital and Michigan Medicine.United States Frontiers in PediatricsFront Pediatr 2021; 9: DOI: 10.3389/fped.2021.657473 AbstractPulmonary lymphangiectasia (PL) is a rare congenital disorder of pulmonary lymphatic development. Although it was traditionally a fatal disorder of infancy, some cases in later childhood have been reported, suggesting a spectrum

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Severe Lymphatic Disorder and Multifocal Atrial Tachycardia Treated with Trametinib in a Patient with Noonan Syndrome and SOS1 Mutation

Michele Lioncino, Adelaide Fusco, Emanuele Monda, Diego Colonna, Martina Caiazza, Michelina Sibilio, Daniela Magri, Angela Carla Borrelli, Barbara D’Onofrio, Maria Luisa Mazzella, Rossella Colantuono, Maria Rosaria Arienzo, Berardo Sarubbi, Maria Giovanna Russo, Giovanni Chello, Giuseppe LimongelliUniversity of Campania “Luigi Vanvitelli” and Monaldi Hospital. University College of London and St. Bartholomew’s Hospital.Italy and United Kingdom GenesGenes

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Pediatric Pulmonary Hypertension: Guidelines From the American Heart Association and American Thoracic Society

Steven H. Abman, Georg Hansmann, Stephen L. Archer, D. Dunbar Ivy, Ian Adatia, Wendy K. Chung, Brian D. Hanna, Erika B. Rosenzweig, J. Usha Raj, David Cornfield, Kurt R. Stenmark, Robin Steinhorn, Bernard Thébaud, Jeffrey R. Fineman, Titus Kuehne, Jeffrey A. Feinstein, Mark K. Friedberg, Michael Earing, Robyn J. Barst, Roberta L. Keller, John P. Kinsella, Mary Mullen, Robin Deterding, Thomas Kulik, George Mallory, Tilman Humpl, David L. WesselUniversity of Colorado School of Medicine. Hannover Medical School. Queen’s University. University of Alberta. Columbia University. Stanford University. Medical College of Wisconsin. University of California, San Francisco. Hospital for Sick Children.

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Hybrid Interventions for Pulmonary Vein Stenosis: Leveraging Intraoperative Endovascular Adjuncts in Challenging Clinical Scenarios

Alyssa B. Kalustian, Paige E. Brlecic, Srinath T. Gowda, Gary E. Stapleton, Asra Khan, Lindsay F. Eilers, Ravi Birla, Michiaki Imamura, Athar M. Qureshi, Christopher A. Caldarone, Manish BansalTexas Children’s Hospital and Baylor College of Medicine. United States World Journal of Pediatric and Congenital Heart SurgeryWorld J Pediatr Congenit Heart Surg 2024; DOI: 10.1177/21501351241247503 AbstractBackground: Pediatric pulmonary

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Timing of magnetic resonance imaging in pregnancy for outcome prediction in congenital diaphragmatic hernia

Vivien Dütemeyer, Mieke M. Cannie, Thomas Schaible, Meike Weis, Nicola Persico, Irene Borzani, Dominique A. Badr, Jacques C. JaniUniversity Hospital Brugmann, Université Libre de Bruxelles and Vrije Universiteit Brussel. Hannover Medical School. Universitätsklinikum Mannheim and University Medical Center Mannheim. Fondazione IRCCS Ca’ Granda Ospedale Maggiore Policlinico. University of Milan.Brussels, Germany and Italy Archives of Gynecology

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Transitional Hemodynamics in Neonates Born Through Meconium-Stained Amniotic Fluid: A Prospective Observational Study

Kamal Joshi, Mayank Priyadarshi, Yash Shrivastava, Suman Chaurasia, Poonam Signh, Nowneet Kumar Bhat, Sriparna BasuAll India Institute of Medical Sciences. India Pediatric CardiologyPediatr Cardiol 2024; DOI: 10.1007/s00246-024-03521-w AbstractNeonates born through meconium-stained amniotic fluid (MSAF) are at increased risk of altered cardiopulmonary transition at birth. There is a paucity of literature evaluating the transitional hemodynamics in these

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Right Atrial Strain in Pediatric Pulmonary Hypertension-A Prospective Observational Study

Subhrashis Guha Niyogi, Avneet Singh, Bhupesh Kumar, Anand Kumar Mishra, Goverdhan Dutt PuriAll India Institute of Medical Sciences. Government Medical College and Hospital. Post Graduate Institute of Medical Education and Research. India Pediatric CardiologyPediatr Cardiol 2024; DOI: 10.1007/s00246-024-03523-8 AbstractRight ventricular (RV) afterload due to elevated pulmonary arterial (PA) pressure in pulmonary hypertension (PH) causes long-term right

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Expanding the phenotypic spectrum of NOTCH1 variants: clinical manifestations in families with congenital heart disease

Kaitlin J. Stanley, Kelsey J. Kalbfleisch, Olivia M. Moran, Rajiv R. Chaturvedi, Maian Roifman, Xin Chen, Roozbeh Manshaei, Nicole Martin, Simina McDermott, Vanda McNiven, Diane Myles-Reid, Lynne E. Nield, Miriam S. Reuter, Marci L. B. Schwartz, Patrick Shannon, Rachel Silver, Cherith Somerville, Ronni Teitelbaum, Laura Zahavich, Anne S. Bassett, Raymond H. Kim, Seema Mital, David

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Effect of phosphodiesterase type 5 inhibitors on surgical outcome of ventricular septal defect and pulmonary hypertension patients

Khaled Ahmed Shams, Dalia Monir Ellahony, Ahmed Fouad Halima, Rania Salah ElzayatHelwan University. Magdi Yacoub Foundation. Menoufia University.Egypt Egypt Heart JournalEgypt Heart J 2024; 76:DOI: 10.1186/s43044-024-00475-5 AbstractBackground: Children with ventricular septal defect (VSD) and large systemic-to-pulmonary shunts eventually develop pulmonary hypertension (PH). The perioperative management of patients with VSD and PH is quite troublesome and still debatable,

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