Pediatric Pulmonary Vascular Disease

Refractory Chylothorax and Ventricular Hypertrophy Treated with Trametinib in a Patient with Noonan Syndrome: 18-Month Follow-Up

Antonia Pascarella, Giuseppe Limongelli, Alessandro De Falco, Elia Marco Paolo Minale, Giangiacomo Di Nardo, Giovanni Maria Di Marco, Geremia Zito Marinosci, Giorgia Olimpico, Paolo Siani, Daniele De BrasiSantobono-Pausilipon Children’s Hospital. University of Campania “Luigi Vanvitelli” and Monaldi Hospital. University “Federico II”. Italy ChildrenChildren 2024; 11: DOI: 10.3390/children11111342 AbstractRASopathies are a group of genetic syndromes caused by […]

Refractory Chylothorax and Ventricular Hypertrophy Treated with Trametinib in a Patient with Noonan Syndrome: 18-Month Follow-Up Read More »

Detection of pulmonary hypertension in preterm infants with bronchopulmonary dysplasia using oxygen saturation data

Pravitha Ramanand, Premananda Indic, Samuel J. Gentle, Namasivayam AmbalavananUniversity of Texas at Tyler. University of Alabama at Birmingham.United States Pediatric ResearchPediatr Res 2025; DOI: 10.1038/s41390-025-03891-8 AbstractBackground: Pulmonary hypertension (PH) complicates the clinical course of bronchopulmonary dysplasia (BPD) in preterm infants, increasing risk of mortality and other morbidities. Early detection of PH may provide the clinical opportunity for

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Infants With a Congenital Diaphragmatic Hernia Had Favourable Pulmonary Hypertension Outcomes at 1 Year of Age

Alice Dirick, Marilyne Levy, Kelly Mellul, Maxime Coignard, Naziha Khen-Dunlop, Alexandre Lapillonne Julien Stirnemann, Elsa Kermorvant-DucheminNecker-Enfants Malades Hospital. France Acta PediatricaActa Pediatr 2025; DOI: 10.1111/apa.70019 AbstractAim: Pulmonary hypertension is frequent in neonates with a congenital diaphragmatic hernia, but long-term data have been scarce. Our aim was to examine its prevalence, evolution and management and identify factors associated

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Continuous positive airway pressure versus conventional oxygen therapy in meconium aspiration syndrome: a randomized controlled trial

Arifa Mustaqeem, Anita Yadav, Jogender Kumar, Pradeep DebataVardhman Mahavir Medical College and Safdarjung Hospital. Post Graduate Institute of Medical Education and Research. India Journal of Tropical PediatricsJ Trop Pediatr 2025; 71: DOI: 10.1093/tropej/fmaf002 AbstractNeonates with meconium aspiration syndrome (MAS) frequently require respiratory support. However, the initial mode of respiratory support in these patients remains unclear. We

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MiR-25-3p regulates pulmonary arteriovenous malformation after Glenn procedure in patients with univentricular heart via the PHLPP2-HIF-1α axis

Junpei Kawamura, Munekazu Yamakuchi, Kentaro Ueno, Teruto Hashiguchi, Yasuhiro OkamotoKagoshima University. Japan Scientific ReportsSci Rep 2025; 15: DOI: 10.1038/s41598-025-88840-5 AbstractThe detailed mechanism of pulmonary arteriovenous malformations after Glenn surgery (G-PAVMs) in cyanotic congenital heart disease (CHD) remains unclear. Microarray in situ hybridization was performed to assess the miRNA (miRNA) profiles of serum from pediatric patients (0-6

MiR-25-3p regulates pulmonary arteriovenous malformation after Glenn procedure in patients with univentricular heart via the PHLPP2-HIF-1α axis Read More »

Unusual presentation of anomalous origin of the right pulmonary artery from the ascending aorta: case report

Mohamed Elhudairy, Naif Alkhushi, Osman Al‑Radi, Khadijah Maghrabi, Gaser AbdelmohsenKing Abdul-Aziz University. Kasr Al Ainy School of Medicine and Cairo University.Saudi Arabia and Egypt Egypt Heart JournalEgypt Heart J 2025; 77: DOI: 10.1186/s43044-025-00614-6 AbstractBackground: Anomalous origin of the right pulmonary artery (AORPA) from the ascending aorta is a rare congenital anomaly, representing approximately 0.12% of all congenital

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Embolotherapy for pulmonary arteriovenous malformations in the pediatric population with hereditary hemorrhagic telangiectasias – a retrospective case series

Haseeb Mukhtar, Vivek Iyer, Nadir Demirel, Emily C. Bendel, Haraldur Bjarnason, Sanjay MisraMayo Clinic.United States Journal of Vascular and Interventional RadiologyJ Vasc Interv Radiol 2025; DOI: 10.1016/j.jvir.2025.01.047 AbstractPurpose: To document the outcomes of embolotherapy for pulmonary arteriovenous malformation (pAVM) management, and investigate factors associated with pAVM persistence after embolotherapy in pediatric patients with hereditary hemorrhagic telangiectasia (HHT).Materials

Embolotherapy for pulmonary arteriovenous malformations in the pediatric population with hereditary hemorrhagic telangiectasias – a retrospective case series Read More »

Characterization of Intracardiac Flow in the Right Ventricle With Pressure and Volume Overload in Children

Yasunobu Hayabuchi, Yukako HommaTokushima University.Japan Cardiology ResearchCardiol Res 2025; 16: 22-32DOI: 10.14740/cr2009 AbstractBackground: Blood flow visualization using vector flow mapping (VFM) holds potential as a novel indicator of right ventricular (RV) function.Methods: This study included 12 patients with atrial septal defect (ASD group, mean (± standard deviation) age: 6.2 ± 1.5 years), six patients with pulmonary hypertension (PH

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Lung ultrasound to evaluate the outcome and prognosis of transient tachypnea of the newborn

Peng Jiang, Jing Wei, Meiying HanLiaocheng People’s Hospital.China Frontiers in PediatricsFront Pediatr 2025; 12:  DOI: 10.3389/fped.2024.1536992 AbstractBackground/objectives: Transient tachypnea of the newborn (TTN) is generally self-limiting. The increasing incidence of severe cases and lack of comprehensive studies on its clinical outcomes and influencing factors highlight the need for improved diagnostic and monitoring tools. This study aimed to

Lung ultrasound to evaluate the outcome and prognosis of transient tachypnea of the newborn Read More »

Comparison of morbidity and mortality outcomes of conventional and sutureless repair techniques in children with isolated total anomalous pulmonary venous drainage

Kübra Gözacik Karakoc, Batuhan Yazici, Hacer Kamali, Okan Yildiz, Gökhan Karakoc, Sertac Haydin, Ismihan Selen OnanIstanbul Mehmet Akif Ersoy Thoracic and Cardiovascular Surgery Training and Research Hospital. Model Statistics CRO and Clinical Trials Center.Turkey Cardiology in the YoungCardiol Young 2025;DOI: 10.1017/S1047951124036679 AbstractObjectives: The sutureless repair technique has been favoured due to its purported reduction in post-operative pulmonary

Comparison of morbidity and mortality outcomes of conventional and sutureless repair techniques in children with isolated total anomalous pulmonary venous drainage Read More »

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