Pediatric Pulmonary Vascular Disease

Resolution of Fenfluramine-associated pulmonary arterial hypertension in Lennox-Gastaut syndrome: A case report and literature review

Rebecca Strafella, Richard Wang, Marissa Petchpradub, Ariel Sacknovitz, Patricia E. McGoldrick, Steven M. WolfNew York Medical College and Westchester Medical Center. Boston Children’s Health.United States Epilepsy and Behavior ReportsEpilepsy Behav Rep 2024; 28: DOI: 10.1016/j.ebr.2024.100730 AbstractFenfluramine is a medication originally approved for weight loss before being withdrawn for an association with the development of pulmonary arterial […]

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Use of Right Ventricular Free-Wall Strain in a Multivariable Estimate of Right Ventricular-Arterial Coupling in Pediatric Pulmonary Arterial Hypertension

Charles T. Simpkin, D. Dunbar Ivy, Mark K. Friedberg, Dale A. BurkettChildren’s Hospital Colorado and University of Colorado – Anschutz Medical Campus. Hospital for Sick Children and University of Toronto.United States and Canada Circulation Cardiovascular ImagingCirc Cardiovasc Imag 2024; DOI: 10.1161/CIRCIMAGING.124.016882 AbstractBackground: Right ventricular-arterial coupling (RVAC) describes the relationship between right ventricular contractility and pulmonary vascular afterload.

Use of Right Ventricular Free-Wall Strain in a Multivariable Estimate of Right Ventricular-Arterial Coupling in Pediatric Pulmonary Arterial Hypertension Read More »

Enhancing the Survival of Congenital Diaphragmatic Hernia: Quality Improvement Initiative With a Multidisciplinary Extracorporeal Membrane Oxygenation Team Approach

Byong Sop Lee Jiyoon Jeong, Euiseok Jung, Ha Na Lee, Heeyoung Kim, Hyunhee Kwon, Soo Hyun Kim, Jung-Man Namgoong, Dae Yeon KimAsan Medical Center, Asan Medical Center Children’s Hospital and University of Ulsan College of Medicine. Republic of Korea Journal of Korean Medical ScienceJ Korean Med Sci 2024; 39: DOI: 10.3346/jkms.2024.39.e300 AbstractBackground: Extracorporeal membrane oxygenation (ECMO) is

Enhancing the Survival of Congenital Diaphragmatic Hernia: Quality Improvement Initiative With a Multidisciplinary Extracorporeal Membrane Oxygenation Team Approach Read More »

Metagenomic Analysis of Gut Microbiome of Persistent Pulmonary Hypertension of the Newborn

Linli Han, Chuyang Lin, Yue Lan, Yimin Hua, Jinlin Wu, Zhenxin Fan, Yifei LiWest China Second University Hospital and Sichuan University. China Cardiovascular ToxicologyCardiovasc Toxicol 2024; DOI: 10.1007/s12012-024-09949-z AbstractPersistent pulmonary hypertension of the newborn (PPHN) is one of the most common diseases in the neonatal intensive care unit which severely affects neonatal survival. Gut microbes play

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Synchrotron-Based Phase-Contrast Micro-CT Combined With Histology to Decipher Differences Between Hereditary and Sporadic Pediatric Pulmonary Veno-Occlusive Disease

Ida Jeremiasen, Niccolò Peruzzi, Elna Lampei, Sofie Meyer, Levent M. Akyürek, Erik Gebre‐Medhin, Ceren Mutgan, Peter Dorfmüller, Lavinia Neubert, Danny Jonigk, Csaba Galambos, Karin Tran‐LundmarkDepartment of Experimental Medical Science and Wallenberg Center for Molecular Medicine Lund University. Skåne University Hospital. Sahlgrenska Academy Hospital. Ludwig Boltzmann Institute for Lung Vascular Research. Universities of Giessen and Marburg

Synchrotron-Based Phase-Contrast Micro-CT Combined With Histology to Decipher Differences Between Hereditary and Sporadic Pediatric Pulmonary Veno-Occlusive Disease Read More »

Radiological evaluation of pulmonary vein obstruction including two examinations by magnetic resonance imaging

W. S. Kim, K. M. Yeon, I. Kim, M. C. Han, J. G. ChiSeoul National University and Children’s Hospital.Repunlic of Korea Pediatric RadiologyPediatr Radiol 1993; 23: 6-11DOI: 10.1007/BF02020210 AbstractCongenital obstruction of the pulmonary vein without anomalous drainage can cause long-standing pulmonary congestion and pulmonary arterial hypertension, and it may include stenosis of individual pulmonary veins and

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Acquired pulmonary vein obstruction after open-heart surgery

Gian Paolo Ussia, Maurizio Marasini, Lucio Zannini, Giacomo PongiglioneGiannina Gaslini Institute, Children’s Hospital.Italy European Journal of Cardiothoracic SurgeryEur J Cardiothorac Surg 2002; 22: 465-467DOI: 10.1016/s1010-7940(02)00350-0 AbstractAcquired pulmonary vein obstruction is an extremely rare complication after open-heart surgery not including pulmonary vein procedures. We report on three cases of this unusual complication presenting peculiar angiographic findings in

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Atresia of right pulmonary veins with intact atrial septum and major aorto-pulmonary collateral treated with percutaneous stent implantation and embolization

Gian Paolo Ussia, Maurizio Marasini, Alesandro Rimini, Giacomo PongiglioneIstituto Giannina Gaslini Children’s Hospital.Italy Journal of Interventional CardiologyJ Interv Cardiol 2004; 17: 183-187DOI: 10.1111/j.1540-8183.2004.09883.x AbstractUnilateral pulmonary vein (PV) atresia is a rare congenital cardiac malformation with evolution toward irreversible pulmonary hypertension. Pneumonectomy or lung transplant is currently the treatment of choice for such a disease. We describe

Atresia of right pulmonary veins with intact atrial septum and major aorto-pulmonary collateral treated with percutaneous stent implantation and embolization Read More »

Recurrent unilateral bacterial pneumonias and interstitial fibrosis associated with pulmonary vein atresia: successful treatment with endovascular stent implantation

O. Sacco, B. Fregonese, L. Fregonese, C. Gambini, G. Pongiglione, G. A. RossiI.R.C.C.S. Giannina Gaslini.Italy Pediatric PulmonologyPediatr Pulmonol 2002; 34: 324-328DOI: 10.1002/ppul.10158 AbstractA variety of pulmonary vascular disorders, such as hemangiomatosis, telangectasia, and veno-occlusive disease, may be involved in the pathogenesis of interstitial lung diseases. We describe the case of a girl with recurrent bacterial pneumonia

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Congenital unilateral pulmonary venous atresia: definitive diagnosis and treatment

K. K. Pourmoghadam, J. W. Moore, M. Khan, E. M. Geary, N. Madan, B. J. Wolfson, J. P. de Chadarevian, D. S. Holsclaw, M. L. JacobsSt Christopher’s Hospital for Children. United States Pediatric CardiologyPediatr Cardiol 2003; 24: 73-79DOI: 10.1007/s00246-002-0220-6 AbstractThree cases of unilateral right-sided pulmonary venous atresia were evaluated over an 18-year period. These bring the

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