Pediatric Pulmonary Vascular Disease

Pulmonary hypertension in 2025: next steps?

Kinjal ParikhINOVA Children’s Hospital.United States Current Opinion in CardiologyCurr Opin Cardiol 2025;DOI: 10.1097/HCO.0000000000001228 AbstractPurpose of review: To review recent updates in pediatric pulmonary hypertension with a special focus on recent recommendations from the World Symposium of Pulmonary Hypertension (WSPH).Recent findings: The third pediatric specific WSPH report highlights updated recommendations for pediatric pulmonary hypertension classification, risk stratification, and management […]

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Reverse Potts shunt as rescue from venoarterial extracorporeal membrane oxygenation in pulmonary veno-occlusive disease

Emily Davis, Can Yerebakan, John T. BergerUMC Children’s Hospital and University Medical Center of Southern Nevada. Nationwide Children’s Hospital. Children’s National Hospital.United States Cardiology in the YoungCardiol Young 2025; DOI: 10.1017/S1047951125001957 AbstractPulmonary veno-occlusive disease has no definitive cure apart from lung transplant. The reverse Potts shunt can be a palliative bridge to transplant. A post-arrest 14-year-old

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Evaluating the relevance of the 2024 BSR systemic sclerosis guideline to juvenile systemic sclerosis

Clare E. Pain, Hanna Lythgoe, Emily Willins, Sunil Sampath, Samundeeswari Deepak, Kathryn S. Torok, Phuoc H. Duong, Shahin Moledina, Juliana Silva, Clarissa Pilkington, Eslam Al-Abadi, Christopher P. DentonAlder Hey Children’s Hospital. Royal Manchester Children’s Hospital. Great North Children’s Hospital. Nottingham Children’s Hospital. UPMC Children’s Hospital of Pittsburgh. Birmingham Women’s and Children’s Hospital. University College London.

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Efficacy of bubble contrast echocardiography in detecting pulmonary arteriovenous fistulas in children with univentricular heart after total cavopulmonary connection

Dai Asada, Yuma Morishita, Yoko Kawai, Yo Kajiyama, Kazuyuki IkedaKyoto Prefectural University of Medicine.Japan Cardiology in the YoungCardiol Young 2020; 30: 227-230DOI: 10.1017/S104795111900324X AbstractBackground: Development of pulmonary arteriovenous fistulas in patients with cavopulmonary anastomosis may result in a significant morbidity. Although the use of bubble contrast echocardiography with selective injection into both the branch pulmonary arteries in

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Evaluation of Exome and Genome Sequencing for Critically Ill Pediatric Cardiac Patients

Angela C. Onorato, Rachel Gosselin, Bimal P. Chaudhari, Chance Alvarado, Peter White, Vidu Garg, Amee M. BigelowNationwide Children’s Hospital.United States Research SquareRes Sq 2025; DOI: 10.21203/rs.3.rs-6314694/v1 AbstractGenetic testing guidelines for children in cardiac intensive care units (CICUs) are lacking despite a high prevalence of genetic diseases among this population. Advances in next-generation sequencing (NGS) technologies, especially

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[Pulmonary arteriovenous fistulas in a pediatric patient: a case report]

Yuli T. Samboni, Liliana P. Tordecilla, Gilberto Acuña, Ana L. MuñozUniversidad Antonio Nariño.Columbia Archivos Argentinos de PediatriaArch Argent Pediatr 2020; 118: e170-e173DOI: 10.5546/aap.2020.e170 AbstractPulmonary arteriovenous fistulas are congenital malformations due to anomalous direct communication between arteries and veins; the incidence is 2-3:100,000 inhabitants. This condition is usually asymptomatic and incidentally appearing in adult imaging findings. Transcutaneous

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Postrepair Pulmonary Vein Stenosis: Addressing Anatomic and Patient Risk Factors to Improve Outcomes

Alessia Di Nardo, Elizabeth D. Persaud, Rachel D. VanderlaanUniversity of Toronto and Hospital for Sick Children.Canada Seminars in Thoracic and Cardiovascular Surgery Pediatric Cardiac Surgery AnnualSemin Thorac Cardiovasc Surg Pediatr Card Surg Annu 2025; 28: 107-116DOI: 10.1053/j.pcsu.2025.02.008 AbstractSurgical results for correction of total anomalous pulmonary venous connection (TAPVC) have improved in the current era. Postrepair pulmonary

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[Cyanosis for more than 4 years in a girl aged 4 years and 3 months]

Mao-Lan Wu, Xiang-Rong Zheng, Yan-Tong Zhu, Guo-Yuan Zhang, Chen-Tao Liu, Xia Wang, Yong-Jun TangXiangya Hospital and Central South University.China Chinese Journal of Contemporary PediatricsZhongguo Dang Dai Er Ke Za Zhi 2020; 22: 387-390DOI: 10.7499/j.issn.1008-8830.1910147 AbstractA girl, aged 4 years and 3 months, presented with cyanosis of the lips shortly after birth. She then experienced shortness of

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Hereditary hemorrhagic telangiectasia and pulmonary arteriovenous malformations

Saniye Girit, Ebru Senol, Özge Karatas, Ayse Inci YıldırımIstanbul Medeniyet University. Göztepe Training and Research Hospital. University of Health Sciences Medical School Dr. Lutfi Kırdar Kartal Educational and Research Hospital. University of Health Sciences Medical School Kartal Kosuyolu High Speciality Educational and Research Hospital.Turkey Respiratory Medicine Case ReportsRespir Med Case Rep 2020; 30: DOI: 10.1016/j.rmcr.2020.101137 AbstractPulmonary

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Homozygous GDF2-Related Hereditary Hemorrhagic Telangiectasia in a Chinese Family

Jinrong Liu, Jigang Yang, Xiaolei Tang, Huimin Li, Yuelin Shen, Weiyue Gu, Shunying ZhaoBeijing Children’s Hospital, National Center for Children’s Health and Capital Medical University. Beijing Friendship Hospital. Beijing Chigene Translational Medicine Research Center.China PediatricsPediatrics 2020; DOI: 10.1542/peds.2019-1970 AbstractHereditary hemorrhagic telangiectasia (HHT) can be clinically diagnosed, but children often lack characteristic features. We report a family

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