Pediatric Pulmonary Vascular Disease

A Congenital Portosystemic Shunt in a Child With Heterotaxy, Situs Inversus, Polysplenia, and Interrupted Inferior Vena Cava With Azygous Continuation

Victoria Carvajal, Saigopala Reddy, Vani Gopalareddy, Adrienne Bean, Gonzalo WallisLevine Children’s Hospital. University of North Carolina Chapel Hill Medical School. United States American College of Gastroenterology Case Reports JournalACG Case Rep J 2023; DOI: 10.14309/crj.0000000000001201 AbstractCongenital portosystemic shunts are rare vascular malformations in which portal venous blood from the intestines and spleen bypasses the liver and […]

A Congenital Portosystemic Shunt in a Child With Heterotaxy, Situs Inversus, Polysplenia, and Interrupted Inferior Vena Cava With Azygous Continuation Read More »

Decreased endothelial micro-RNA-30b-5p impairs angiogenesis in fetal lambs with persistent pulmonary hypertension

Sunil K. Sati, Ujala Rana, Chintamani Joshi, Ru-Jeng Teng, Girija G. KonduriMedical College of Wisconsin.United States Pediatric ResearchPediatr Res 2025; DOI: 10.1038/s41390-025-04098-7 AbstractBackground: Impaired angiogenesis contributes to increased pulmonary vascular resistance in persistent pulmonary hypertension of the newborn (PPHN). Notch signaling, critical to lung angiogenesis, is modulated by micro-RNAs (miR). RNA sequencing of pulmonary arterial endothelial cells

Decreased endothelial micro-RNA-30b-5p impairs angiogenesis in fetal lambs with persistent pulmonary hypertension Read More »

Pulmonary hypertension associated with vein of Galen malformation. Fetal cardiac hemodynamic findings and physiological considerations

Ana Mendez, Elisabeth Codsi, Francisco Gonzalez Barlatay, Anie Lapointe, Marie-Josée RaboissonUniversity of Montreal, Sainte-Justine University Hospital Center. Hospital Virgen del Rocío. Canada and Spain Journal of PerinatologyJ Perinatol 2022; 42: 143-148DOI: 10.1038/s41372-021-01297-y AbstractThe management of newborns with vein of Galen aneurysmal malformation (VGAM) is clinically challenging for neonatologists and cardiologists. Hemodynamic profiles in four fetuses diagnosed

Pulmonary hypertension associated with vein of Galen malformation. Fetal cardiac hemodynamic findings and physiological considerations Read More »

A catheter-based interventional strategy redirects hepatic vein flows after Fontan procedure in left isomerism to treat severe hypoxemia

Kothandam SivakumarMadras Medical Mission.India Annals of Pediatric CardiologyAnn Pediatr Cardiol 2022; 15: 212-215DOI: 10.4103/apc.apc_80_21 AbstractPulmonary arteriovenous malformations after the Kawashima procedure causing severe hypoxemia are treated by Fontan surgery that redirects hepatic venous blood to the pulmonary circulation. Alignment of the hepatic venous conduit toward both pulmonary arteries is crucial for their regression. Persistent hypoxemia due

A catheter-based interventional strategy redirects hepatic vein flows after Fontan procedure in left isomerism to treat severe hypoxemia Read More »

Prominent Intrapulmonary Shunt Vessels and Altered Lung Development in Infants With Sudden Unexplained Infant Death

Csaba Galambos, Douglas Bush, Steven H. Abman, Michael CaplanUniversity of Colorado School of Medicine. Icahn School of Medicine at Mount Sinai. Lake Erie College of Osteopathic Medicine.United States Journal of PediatricsJ Pediatr 2023; DOI: 10.1016/j.jpeds.2022.10.026 AbstractThe purpose of this study was to evaluate intrapulmonary arteriovenous shunts in patients with and without sudden unexplained infant death. We

Prominent Intrapulmonary Shunt Vessels and Altered Lung Development in Infants With Sudden Unexplained Infant Death Read More »

Management of an asymptomatic pulmonary arteriovenous fistula diagnosed prenatally by detachable balloon embolization: a case report

Wenjuan Li, Pengjun Zhao, Sun Chen Xinhua Hospital, Affiliated to Shanghai Jiao Tong University School of Medicine.China European Heart Journal Case ReportsEur Heart J Case Rep 2025; DOI: 10.1093/ehjcr/ytaf038 AbstractBackground: Pulmonary arteriovenous fistulas (PAVFs) are abnormal vascular malformations that connect pulmonary arteries and pulmonary veins, resulting in a right-to-left shunt. This anatomical shunt leads to a decrease in

Management of an asymptomatic pulmonary arteriovenous fistula diagnosed prenatally by detachable balloon embolization: a case report Read More »

Acquired Pulmonary Arteriovenous Malformation in a Case of a Pediatric Adrenocortical Carcinoma

Rahat-Ul-AinChildren’s Hospital and Institute of Child Health.Pakistan Journal of the College of Physicians and Surgeons PakistanJ Coll Physicians Surg Pak 2021; 31: 119-120DOI: 10.29271/jcpsp.2021.01.119 AbstractAbstract Not Available CategoryPulmonary Arteriovenous Malformations Age Focus: Pediatric Pulmonary Vascular Disease Fresh or Filed Publication: Filed (PHiled). Greater than 1-2 years since publication Article Access Free PDF File or Full Text

Acquired Pulmonary Arteriovenous Malformation in a Case of a Pediatric Adrenocortical Carcinoma Read More »

Determination of the Cause for Persistent Hypoxemia by Transesophageal Echocardiography After a Fontan Completion

Madan Mohan Maddali, Eapen Thomas, Pranav Subbaraya Kandachar, Nishant Ram Arora, Salim Nasser Al-MaskariRoyal Hospital. Oman Journal of Cardiothoracic and Vascular AnesthesiaJ Cardiothorac Vasc Anesth 2021; 35: 3135-3138DOI: 10.1053/j.jvca.2021.01.054 AbstractAbstract Not Available CategoryPulmonary Arteriovenous MalformationsDiagnostic Testing for Pulmonary Vascular Disease. Invasive Testing Age Focus: Pediatric Pulmonary Vascular Disease Fresh or Filed Publication: Filed (PHiled). Greater than

Determination of the Cause for Persistent Hypoxemia by Transesophageal Echocardiography After a Fontan Completion Read More »

Increases in oxygen saturation following discharge from Fontan palliation – an indicator of resolution of pulmonary arteriovenous malformations?

Hannah Van Galder, Amy M. Schaal, Mingen Feng, Amy Y. Pan, Michele A. Frommelt, Salil Ginde, Andrew D. SpearmanMedical College of Wisconsin and Children’s Wisconsin. United States Cardiology in the YoungCardiol Young 2021; 31: 1807-1813DOI: 10.1017/S1047951121000913 AbstractBackground: Pulmonary arteriovenous malformations in single ventricle congenital heart disease are poorly understood. Previous studies investigating pulmonary arteriovenous malformations predominantly focus

Increases in oxygen saturation following discharge from Fontan palliation – an indicator of resolution of pulmonary arteriovenous malformations? Read More »

Persistent pulmonary hypertension of the newborn infant (PPHN) due to premature closure of the ductus arteriosus (DA)

Ayevbekpen Grace Okoye, Adrita Khawash, Mahesh Nanjundappa, Matthew Jones, Anne GreenoughKings College Hospital NHS Foundation Trust. Evelina Children’s Hospital and Guys and St Thomas Hospital. United Kingdom Case Reports in Perinatal MedicineCase Rep Perinat Med 2025; 13: DOI: 10.1515/crpm-2024-0001 AbstractObjectives: To describe the course of an infant with persistent pulmonary hypertension of the newborn (PPHN) secondary to

Persistent pulmonary hypertension of the newborn infant (PPHN) due to premature closure of the ductus arteriosus (DA) Read More »

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