Pediatric Pulmonary Vascular Disease

Decreased smooth muscle cells and fibrous thickening of the tunica media in peripheral pulmonary artery stenosis in Alagille syndrome

Yosuke Ogawa, Amane Yamamoto, Sho Yamazawa, Masako Ikemura, Yasutaka Hirata, Ryo InuzukaUniversity of Tokyo Hospital.Japan Cardiovascular PathologyCardiovasc Pathol 2025; DOI: 10.1016/j.carpath.2024.107677 AbstractAlagille syndrome is caused by mutations in genes involved in NOTCH signaling, specifically JAG1 and NOTCH2, and is associated with a high rate of peripheral pulmonary artery stenosis. In this study, we report the case […]

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Chronic cyanosis since infancy: Unveiling a giant right pulmonary arteriovenous malformation

Dian Komalaa, Harry Galuh Nugrahaa, Firman Ramadhana, Rais Khairuddina, Rahmat Budi Kuswiyantob, Putria Rayani ApandiUniversitas Padjadjaran.Indonesia Radiology Case ReportsRadiol Case Rep 2025; 20: 5353-5356DOI: 10.1016/j.radcr.2025.06.084 AbstractGiant pulmonary arteriovenous malformations (PAVMs) are rare vascular anomalies involving direct connections between pulmonary arteries and veins, leading to right-to-left shunting and systemic hypoxemia. While small PAVMs may be asymptomatic, larger

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Early postnatal right-to-left patent ductus arteriosus shunting and severe outcomes in neonates with congenital diaphragmatic hernia: a retrospective cohort study

Jung Il Kwak, Juhee Park, Mi Jin Kim, Kyusang Yoo, Bo Kyeong Jin, Tae-Gyeong Kim, Joo Hyung Roh, Ha Na Lee, Keon Hee Seol, Chae Young Kim, Soo Hyun Kim, Jiyoon Jeong, Byong Sop Lee, Euiseok JungAsan Medical Center Children’s Hospital and University of Ulsan College of Medicine. BioMedical Central PediatricsBMC Pediatr 2025; 25: DOI: 10.1186/s12887-025-05986-x

Early postnatal right-to-left patent ductus arteriosus shunting and severe outcomes in neonates with congenital diaphragmatic hernia: a retrospective cohort study Read More »

General and Emergency Presentations of Children with Congenital Heart Defect and Factors Affecting it as Seen in A Tertiary Health Institution in Enugu

I. O. Arodiwe, I. A. Nwafor, F. A. Ujunwa, B. O. Edulu, J. M. Chinawa, T. A. Oguonu, N. Ezemba, J. C. EzeUniversity of Nigeria, Enugu Campus.Nigeria West Africa Journal of MedicineWest Africa J Med 2025; 42: 202-207DOI: Not Available AbstractBackground and objectives: The pattern of emergency presentations in children with congenital heart disease (CHD) is

General and Emergency Presentations of Children with Congenital Heart Defect and Factors Affecting it as Seen in A Tertiary Health Institution in Enugu Read More »

Inflammatory Markers During Extracorporeal Membrane Oxygenation in Neonates With Congenital Diaphragmatic Hernia

Friederike M. Krechel, Judith Leyens, Eva Schoenenborn, Ramona Dolscheid-Pommerich, Bartolomeo Bo, Tamene Melaku, Christoph Berg, Andreas Mueller, Florian KipfmuellerChildren’s Hospital, University Hospital Bonn and University of Bonn. British Colombia Women’s and Children’s Hospital and University of British Colombia. University Hospital Cologne. University Medical Center Mannheim and University of Heidelberg.Germany and Canada American Society of Artificial

Inflammatory Markers During Extracorporeal Membrane Oxygenation in Neonates With Congenital Diaphragmatic Hernia Read More »

Less is More: ECMO Utilization and Outcomes in Congenital Diaphragmatic Hernia

Anastasia M. Kahan, Sommer Glasgow, Bradley A. Yoder, Michelle Yang, Christian C. Yost, Kelsea Peterson, Jack H. Scaife, Christopher E. Clinker, Erica Arnold, Stephen J. Fenton, Zachary J. Kastenberg, Robert A. Swendiman, Scott S. Short, Katie W. RussellUniversity of Utah.United States Journal of Pediatric SurgeryJ Pediatr Surg 2025; DOI: 10.1016/j.jpedsurg.2025.162571 AbstractPurpose: Infants with congenital diaphragmatic hernia (CDH)

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Persistent Pulmonary Hypertension Among Infants Undergoing Therapeutic Hypothermia for Hypoxic Ischemic Encephalopathy: A Systematic Review and Meta-Analysis

Rashida Javed, Tim J. Van Hasselt, Narasimha Rao, Harsha GowdaNorthampton General Hospital. University of Leicester. Madinat Zayed Hospital. University Hospitals Birmingham.United Kingdom and United Arab Emiretes Therapeutic Hypothermia and Temperature ManagementTher Hypothermia Temp Manag 2025; DOI: 10.1177/21537658251370950 AbstractTo perform a systematic review and meta-analysis to examine the association between persistent pulmonary hypertension (PPHN) and receipt of

Persistent Pulmonary Hypertension Among Infants Undergoing Therapeutic Hypothermia for Hypoxic Ischemic Encephalopathy: A Systematic Review and Meta-Analysis Read More »

Clinical and molecular spectrum of patients with methylmalonic acidemia and homocysteinemia complicated by cardiovascular manifestations

Wanqing Zhao, Yanan Zhang, Yalei Pi, Yuqian Li, Huifeng ZhangSecond Hospital of Hebei Medical University. China Orphanet Journal of Rare DiseaseOrphanet J Rare Dis 2025; DOI: 10.1186/s13023-025-03907-w AbstractBackground: To investigate the clinical characteristics, treatment response, and prognosis of patients with methylmalonic acidemia (MMA) and homocysteinemia complicated by cardiovascular manifestations and to raise awareness regarding MMA and homocysteinemia.Methods: A

Clinical and molecular spectrum of patients with methylmalonic acidemia and homocysteinemia complicated by cardiovascular manifestations Read More »

Pulmonary Arterial Hypertension Requiring Medication Is Associated With Higher Prevalence of Thrombocytopenia in Pediatric Patients

Tanya Reyna, Catherine Agarwal, Abrar Mamun, Jessica Dae, Yusuf Ozcan, Michael J. Angtuaco, Taha Bat, Erhan AraratUniversity of Texas Southwestern Medical Center. University of Texas at Dallas. University of Arkansas for Medical Sciences.United States Pediatric PulmonologyPediatr Pulmonol 2025; 60: DOI: 10.1002/ppul.71252 AbstractAbstract Not Available CategoryAcquired Patient Factors Associated with Pulmonary Vascular Disease Age Focus: Pediatric Pulmonary

Pulmonary Arterial Hypertension Requiring Medication Is Associated With Higher Prevalence of Thrombocytopenia in Pediatric Patients Read More »

Left Main Bronchus Stenosis Leading to Bronchiectasis and Pulmonary Hypertension- Relieved by Stent Placement

Patrick Stafler, Nili Schamroth, Arnon Elizur, Dario Prais, Eyal Jacobi, Zvi Bar-Sever, Tamir Dagan, Einat Birk, Elchanan BruckheimerSchneider Children’s Medical Center of Israel. Tel Aviv University. Rabin Medical Center. Yitzhak Shamir Medical Center. Israel Pediatric PulmonologyPediatr Pulmonol 2025; 60: DOI: 10.1002/ppul.71251 AbstractAbstract Not Available CategoryClass III. Pulmonary Hypertension Associated with Airway Disease, Apnea or HypoventilationSurgical and

Left Main Bronchus Stenosis Leading to Bronchiectasis and Pulmonary Hypertension- Relieved by Stent Placement Read More »

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