Pediatric Pulmonary Vascular Disease

TGF-β receptor mutations and clinical prognosis in Chinese pediatric patients with idiopathic/hereditary pulmonary arterial hypertension

Xinyu Zhang, Chen Zhang, Qiangqiang, Li, Hong GuBeijing Anzhen Hospital and Capital Medical University.China Pulmonary CirculationPulm Circ 2022; 12: DOI: 10.1002/pul2.12076 AbstractThe relationship between clinical prognosis and transforming growth factor-β (TGF-β) receptor mutations in Chinese pediatric patients with idiopathic/hereditary pulmonary arterial hypertension (IPAH/HPAH) remains unclear. We retrospectively studied the clinical characteristics and outcomes of pediatric patients […]

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Echocardiographic measures of ventricular-vascular interactions in congenital diaphragmatic hernia

Sanjeev Aggarwal, Christina Shanti, Prashant Agarwal, Joseph Lelli, Girija NatarajanCentral Michigan University and Children’s Hospital of Michigan.United States Early Human DevelopmentEarly Hum Dev 2022; 165: DOI: 10.1016/j.earlhumdev.2021.105534 AbstractObjective: To evaluate the utility of echocardiographic measures of ventricular-vascular interactions in predicting death or ECMO in congenital diaphragmatic hernia (CDH).Design: In this single center retrospective study, early (<48 hour age)

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Morbidity in children after fetoscopic endoluminal tracheal occlusion for severe congenital diaphragmatic hernia: Results from a multidisciplinary clinic

Shelby R. Sferra, Melanie K. Nies, Jena L. Miller, Alejandro V. Garcia, Erica I. Hodgman, Annalise B. Penikis, Abigail J. Engwall-Gill, Vera Joanna Burton, Jessica L. Rice, Peter J. Mogayzel, Ahmet A. Baschat, Shaun M. KunisakiJohns Hopkins University School of Medicine. United States Journal of Pediatric SurgeryJ Pediatr Surg 2023; 58: 14-19DOI: 10.1016/j.jpedsurg.2022.09.042 AbstractBackground: Although fetoscopic endoluminal

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Long-term outcomes of congenital diaphragmatic hernia: A single institution experience

Claire D. Gerall, Latoya A. Stewart, Jessica Price, Sandra Kabagambe, Shelby R. Sferra, Rebecca Hernan, Julie Khlevner, Usha S. Krishnan, Alive De, Gudrun Aspelund, Vincent P. DuronColumbia University Vagelos College of Physicians and Surgeons and NewYork-Presbyterian Morgan Stanley Children’s Hospital.United States Journal of Pediatric SurgeryJ Pediatr Surg 2022; 57: 563-569DOI: 10.1016/j.jpedsurg.2021.06.007 AbstractBackground/purpose: As survival rates for patients

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Association between Genotype, Presentation, and Outcome in Childhood Idiopathic and Hereditary Pulmonary Arterial Hypertension

Zhuoyuan Xu, Hongsheng Zhang, Chen Zhang, Qiangqiang Li, Hong GuBeijing Anzhen Hospital and Capital Medical University, No. 2.China Journal of Clinical MedicineJ Clin Med 2022; 11: DOI: 10.3390/jcm11247331 AbstractBackground: Paediatric-onset idiopathic/hereditary pulmonary arterial hypertension (IPAH/HPAH) is partially linked to genetic factors that may also affect treatment response and outcome. The relation between clinical characteristics and pathogenicity of

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An Adolescent Patient With Idiopathic Pulmonary Arterial Hypertension Weaned Off Intravenous Epoprostenol Following Treatment With Selexipag: A Case Report

Ayako Chida-Nagai, Takao Tsujioka, Daisuke Sasaki, Gaku Izumi, Hirokuni Yamazawa, Atsuhito TakedaHokkaido University Hospital.Japan Frontiers in PediatricsFront Pediatr 2022; DOI: 10.3389/fped.2022.909595 AbstractIdiopathic pulmonary arterial hypertension (PAH) is a rare, progressive disease affecting the pulmonary arteries. Epoprostenol, a synthetic prostaglandin analog, is the most potent pharmacological treatment modality used in patients with PAH. However, it requires continuous

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Clinical impact of subcutaneous treprostinil in trisomy 21 patient with pulmonary arterial hypertension associated with CHD

Ryusuke Numata, Kiyohiro Takigiku, Kouta TakeiNagano Children’s HospitalJapan Cardiology in the YoungCardiol Young 2022; DOI: 10.1017/S1047951121005096 AbstractSubcutaneous treprostinil is commonly used to improve idiopathic pulmonary arterial hypertension in children. However, its effectiveness has not been reported in trisomy 21. We report the case of 9-year-old boy in trisomy 21 with CHD-pulmonary artery hypertension after surgical correction

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A Study on the Molecular Mechanism of High Altitude Heart Disease in Children

Qu-Zhen Tashi, Sang-Bu Tsering, Na-Ni Zhou, Yi Zhang, Yu-Juan Huang, Jia Jia, Ting-Jun LiShigatse Peopel’s Hospital. Fujungenetics Technologies Inc. Children’s Hospital of Shanghai.China Pharmacogenomics and Personalized MedicinePharmgenomica Pers Med 2022; 15: 721-731DOI: 10.2147/PGPM.S356206 AbstractObjective: High altitude heart disease (HAHD) is a common pediatric disease in high altitude areas. It usually occurs in people who have lived for

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Seven-day in vivo testing of a novel, low-resistance, pumpless pediatric artificial lung for long-term support

Brian P. Fallon, Alex J. Thompson, Aaron R. Prater, Skylar Buchan, Trevor Alberts, Mark Hoenerhoff, Alvaro Rojas-Pena, Robert H. Bartlett, Ronald B. HirschlUniversity of Michigan Medical School and Michigan Medicine.United States Journal of Pediatric SurgeryJ Pediatr Surg 2022; 57: 614-623DOI: 10.1016/j.jpedsurg.2022.07.006 AbstractIntroduction: For children with end-stage lung disease that cannot wean from extracorporeal life support (ECLS), a

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Quantitative cardiopulmonary magnetic resonance imaging in neonatal congenital diaphragmatic hernia

Jean A. Tkach, Nara S. Higano, Michael D. Taylor, Ryan A. Moore, Monir Hossain, Guixia Huang, David R. Spielberg, Sean B. Fain, Paul S. Kingma, Jason C. WoodsCincinnati Children’s Hospital Medical Center and University of Cincinnati College of Medicine. Texas Children’s Hospital. University of Iowa. University of Wisconsin.United States Pediatric RadiologyPediatr Radiol 2022; 52: 2306-2318DOI: 10.1007/s00247-022-05384-w

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