Pediatric Pulmonary Vascular Disease

Progress in Pulmonary Vein Stenosis: Lessons from Success in Treating Pulmonary Arterial Hypertension

Kathy J. Jenkins, Jeffrey R. FinemanBoston Children’s Hospital. University of California, San Francisco.United States ChildrenChildren 2022; 9: DOI: 10.3390/children9060799 AbstractPulmonary vein stenosis (PVS) is a rare and poorly understood condition that can be classified as primary, acquired, status-post surgical repair of PVS, and/or associated with developmental lung disease. Immunohistochemical studies demonstrate that obstruction of the large […]

Progress in Pulmonary Vein Stenosis: Lessons from Success in Treating Pulmonary Arterial Hypertension Read More »

Autologous vascularised pericardial flap tunneling technique in Scimitar syndrome repair with dextrocardia: lessons from the Senning procedure

Alain J. Poncelet, Karlien Carbonez, Jean E. RubayCliniques Universitaires Saint-Luc, Bruxelles.Belgium Cardiology in the YoungCardiol Young 2021; 31: 859-861DOI: 10.1017/S1047951120004928 AbstractScimitar syndrome is a rare variant (5%) of partial abnormal pulmonary venous return. Surgery is required when pulmonary overcirculation is present. Following repair, Scimitar vein stenosis occurs in approximately 20%. We applied a variant of the

Autologous vascularised pericardial flap tunneling technique in Scimitar syndrome repair with dextrocardia: lessons from the Senning procedure Read More »

Longer Exposure to Left-to-Right Shunts Is a Risk Factor for Pulmonary Vein Stenosis in Patients with Trisomy 21

Connie Choi, Kimberlee Gauvreau, Philip Levy, Ryan Callahan, Kathy J. Jenkins, Minghui ChenHarvard Medical School and Boston Children’s Hospital.United States ChildrenChildren 2021; 8: DOI: 10.3390/children8010019 AbstractWe conducted a study to determine whether patients born with Trisomy 21 and left-to-right shunts who develop pulmonary vein stenosis (PVS) have a longer exposure to shunt physiology compared to those

Longer Exposure to Left-to-Right Shunts Is a Risk Factor for Pulmonary Vein Stenosis in Patients with Trisomy 21 Read More »

Effectiveness of posterior aortopexy for the left pulmonary vein obstruction between the left atrium and the descending aorta

Kwang Ho Choi, Hyungtae Kim, Si Chan Sung, Hyoung Doo Lee, Hoon Ko, Joung-Hee ByunPusan National University Yangsan Hospital. Republic of Korea Journal of Cardiac SurgeryJ Card Surg 2021; 36: 2644-2650DOI: 10.1111/jocs.15596 AbstractBackground: Left pulmonary vein (PV) obstruction can occur due to compression between the left atrium (LA) and the descending aorta (DA). One of the effective

Effectiveness of posterior aortopexy for the left pulmonary vein obstruction between the left atrium and the descending aorta Read More »

This and that: management of Tetralogy of Fallot and pulmonary vein stenosis in an infant-a case report

Christopher P. Scott, Kamel Shibbani, Christopher A. Caldarone, Daniel McLennanChildren’s Wisconsin. University of Iowa Stead Family Children’s Hospital. Texas Children’s Hospital.United States European Heart Journal Case ReportsEur Heart J Case Rep 2021; 5: DOI: 10.1093/ehjcr/ytab429 AbstractBackground: Tetralogy of Fallot (TOF) is the most common congenital cyanotic cardiac lesion. Pulmonary vein stenosis occurs much less commonly and remains

This and that: management of Tetralogy of Fallot and pulmonary vein stenosis in an infant-a case report Read More »

Infantile Scimitar Syndrome With Contralateral Pulmonary Vein Stenosis and Refractory Pulmonary Hypertension

Janelle Buysse, Ramya Deepthi Billa, Daniel McLennan, Ravi Ashwath, Aditya Badheka, Madhuradhar ChegondiUniversity of Iowa Stead Family Children’s Hospital.United States CureusCureus 2021; 13: DOI: 10.7759/cureus.17203 AbstractInfantile scimitar syndrome is associated with pulmonary hypertension which can be difficult to manage. We present a three-month-old infant with scimitar syndrome, who eventually developed refractory pulmonary hypertension, posing a significant

Infantile Scimitar Syndrome With Contralateral Pulmonary Vein Stenosis and Refractory Pulmonary Hypertension Read More »

Preliminary findings on the use of intravascular ultrasound in the assessment of pediatric pulmonary vein stenosis

Ryan Callahan, Kathy J. Jenkins, Zachary Gauthier, Kimberlee Gauvreau, Diego PorrasBoston Children’s Hospital and Harvard Medical SchoolUnited States Catheterization and Cardiovascular InterventionsCatheter Cardiovasc Interv 2021; 97: E362-E370DOI: 10.1002/ccd.29264 AbstractObjective: Determine the feasibility of performing intravascular ultrasound (IVUS) in pediatric pulmonary vein stenosis (PVS) and investigate whether IVUS can delineate the mechanism of PVS.Background: The use of IVUS in

Preliminary findings on the use of intravascular ultrasound in the assessment of pediatric pulmonary vein stenosis Read More »

Primary pulmonary vein stenosis among premature infants with single-vessel disease

Eli Zettler, Brian K. Rivera, Corey Stiver, Brian Boe, Clifford Cua, Molly K. Ball, Charles V. Smith, Jonathan L. Slaughter, Bernadette Chen, Ryan Callahan, Carl H. BackesNationwide Children’s Hospital and Ohio State University. University of Washington School of Medicine. Boston Children’s Hospital and Harvard Medical School. United States Journal of PerinatologyJ Perinatol 2021; 41: 1621-1626DOI: 10.1038/s41372-020-00830-9

Primary pulmonary vein stenosis among premature infants with single-vessel disease Read More »

Secondary Pulmonary Vein Stenosis Due to Total Anomalous Pulmonary Venous Connection Repair in Children: Extravascular MDCT Findings

Edward Y. Lee, Sara O. Vargas, Kathy J. Jenkins, Ryan Callahan, Halley J. Park, Zachary Gauthier, Abbey J. WinantBoston Children’s Hospital and Harvard Medical School.United States ChildrenChildren 2021; 8: DOI: 10.3390/children8090726 AbstractPurpose: To evaluate extravascular findings on thoracic MDCT angiography in secondary pulmonary vein stenosis (PVS) due to total anomalous pulmonary venous connection (TAPVC) repair in children.Materials

Secondary Pulmonary Vein Stenosis Due to Total Anomalous Pulmonary Venous Connection Repair in Children: Extravascular MDCT Findings Read More »

Extravascular MDCT Findings of Pulmonary Vein Stenosis in Children with Cardiac Septal Defect

Edward Y. Lee, Ryan Callahan, Sara O. Vargas, Kathy J. Jenkins, Halley J. Park, Zachary Gauthier, Abbey J. WinantBoston Children’s Hospital and Harvard Medical School.United States ChildrenChildren 2021; 8: DOI: 10.3390/children8080667 AbstractPurpose: To retrospectively investigate the extravascular thoracic MDCT angiography findings of pulmonary vein stenosis (PVS) in children with a cardiac septal defect. Materials and Methods: Pediatric patients

Extravascular MDCT Findings of Pulmonary Vein Stenosis in Children with Cardiac Septal Defect Read More »

Scroll to Top