Pediatric Pulmonary Vascular Disease

High altitude simulation testing in patients with congenital diaphragmatic hernia

Ashlyn E. Whitlock, Catherine A. Sheils, Jill M. Zalieckas, Gary Visner, Mary Mullen, Mollie Studley, Lindsay Lemire, Terry L. BuchmillerBoston Children’s Hospital and Harvard Medical School.United States Journal of Pediatric SurgeryJ Pediatr Surg 2022; 57: 195-198DOI: 10.1016/j.jpedsurg.2021.10.044 AbstractAim of study: Congenital Diaphragmatic Hernia (CDH) is associated with lung hypoplasia and pulmonary hypertension. Many patients receive care in […]

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Chest computed tomography findings of ground-glass nodules with enhancing central vessel/nodule in pediatric patients with BMPR2 mutations and plexogenic arteriopathy

Jason P. Weinman, David A. Mong, LaDonna J. Malone, D. Dunbar Ivy, Robin R. Deterding, Csaba GalambosChildren’s Hospital Colorado.United States Pediatric RadiologyPediatr Radiol 2022; 52: 2549-2556DOI: 10.1007/s00247-022-05413-8 AbstractBackground: Germline mutation in bone morphogenetic protein type II (BMPR2) is the most common cause of idiopathic/heritable pulmonary hypertension in pediatric patients. Despite the discovery of this gene there are

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Use of vasopressin in persistent pulmonary hypertension of the newborn: A case series

Swosti Joshi, Vilmaris Quinones Cardona, Ogechukwu R. MenkitiDrexel University College of Medicine and St. Christopher’s Hospital for Children.United States SAGE Medical Case ReportsSAGE Med Cas Rep 2022; DOI: 10.1177/2050313X221102289 AbstractTreatment of neonates with persistent pulmonary hypertension of newborn includes optimization of ventilatory support, use of pulmonary vasodilators, and/or inotropic support. If refractory to this management, some

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Predictors of Serious Adverse Events and High-Level Cardiorespiratory Support in Patients Undergoing Transcatheter Pulmonary Vein Interventions

Jessica A. Barreto, Kimberlee Gauvreau, Diego Porras, Jesse J. Esch, Nicola Maschietto, Brian Quinn, Lisa Bergersen, Mary Stein, Ryan CallahanHarvard Medical School and Boston Children’s Hospital. University of Pennsylvania Perelman School of Medicine and Children’s Hospital of Philadelphia.United States Pediatric CardiologyPediatr Cardiol 2023; DOI: 10.1007/s00246-023-03129-6 AbstractPatients with pulmonary vein stenosis (PVS) often require frequent transcatheter pulmonary

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Benefit of stereoscopic volume rendering for the identification of pediatric pulmonary vein stenosis from CT angiography

Michelle Noga, Ross Cockburn, Jiali Luan, Deepa Krishnaswamy, Kumaradevan PunithakumarUniversity of Alberta. Mazankowski Alberta Heart Institute. University of Manitoba. Dalhousie University.Canada PLOS Digital HealthPLOS Digit Health 2023; 2: DOI: 10.1371/journal.pdig.0000215 AbstractThe use of three-dimensional (3D) technologies in medical practice is increasing; however, its use is largely untested. One 3D technology, stereoscopic volume-rendered 3D display, can improve

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Acute Pulmonary Vasodilator Testing and Long-Term Clinical Course in Segmental Pulmonary Vascular Disease

Liezl Domingo, H. Sonali Magdo, Ronald W. DayUniversity of Utah and Primary Children’s Hospital.United States Pediatric CardiologyPediatr Cardiol 2018; 39: 501-508DOI: 10.1007/s00246-017-1780-9 AbstractResults of acute pulmonary vasodilator testing (AVT) and the outcome of medical therapy have not been described in patients with segmental pulmonary vascular disease (SPVD). We sought to compare the pulmonary vasodilatory effects of

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Congenital Surfactant C Deficiency with Pulmonary Hypertension – A Case Report

Wei Chard Chua, I-Chen Chen, Yi-Ching Liu, Yen-Hsien Wu, Shih-Hsing Lo, Jong-Hau Hsu, Peir-In Liang, Hsiu-Lin Chen, Zen-Kong DaiKaohsiung Medical University Hospital. Taiwan ChildrenChildren 2022; 9: DOI: 10.3390/children9101435 AbstractInterstitial lung diseases in children are a diverse group in terms of etiology and pathogenesis. With advances in genetic testing, mutations in surfactant protein have now been identified

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Deficiency in DDR1 Induces Pulmonary Hypertension and Impaired Alveolar Development

Quinn A. Bonafiglia, Yu-Qing Zhou, Guangpei Hou, Rhidita Saha, Ying-Han R. Hsu, Jonah Burke-Kleinman, Michelle P. BendeckUniversity of Toronto, Ted Rogers Centre for Heart Research and University Health Network.Canada American Journal of Respiratory Cell and Molecular BiologyAm J Respir Cell Mol Biol 2022; 67: 562-573DOI: 10.1165/rcmb.2022-0124OC AbstractPulmonary hypertension (PH) is a multifaceted condition characterized by elevated

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Long-term outcomes of transcatheter Potts shunt in children with suprasystemic pulmonary arterial hypertension

Raymond N. Haddad, Maryline Levy, Isabelle Szezepanski, Sophie Malekzadeh-Milani, Damien BonnetHôpital Universitaire Necker-Enfants Malades and Université de Paris Cité.France Frontiers in Cardiovascular MedicineFront Cardiovasc Med 2022; 9: DOI: 10.3389/fcvm.2022.1028304 AbstractBackground: Transcatheter Potts shunt (TPS) is a palliation alternative for children with severe pulmonary arterial hypertension (PAH). Debates on the long-term outcomes remain unsolved.Objectives: To evaluate long-term clinical and

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Extremely premature infants born at 23-25 weeks gestation are at substantial risk for pulmonary hypertension

Hannes Sallmon, Martin Koestenberger, Alexander Avian, Friedrich Reiterer, Bernhard Schwaberger, Katharina Meinel, Gerhard Cvirn, Stefan Kurath-Koller, Andreas Gamillscheg, Georg HansmannEuropean Pediatric Pulmonary Vascular Disease Network. Charité-Universitätsmedizin Berlin. Deutsches Herzzentrum Berlin. Medical University Graz. Hannover Medical School. Germany and Austria Journal of PerinatologyJ Perinatol 2022; 42: 781-787DOI: 10.1038/s41372-022-01374-w AbstractObjective: Extremely low gestational age newborns (ELGANs) represent an especially

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