Pediatric Pulmonary Vascular Disease

Midodrine, an Oral Alpha-1 Adrenoreceptor Agonist, Successfully Treated Refractory Congenital Chylous Pleural Effusion and Ascites in a Neonate

Satoshi Tamaoka, Asami Osada, Takane Kin, Takeshi Arimitsu, Mariko HidaKeio University School of Medicine.Japan ChestChest 2021; 159: e189-e191DOI: 10.1016/j.chest.2020.10.071 AbstractA trisomy 21 neonate presented with congenital chylous pleural effusion and ascites that was refractory to conventional pharmacotherapy. Midodrine, an oral alpha-1-adrenoreceptor agonist, achieved remission of chylous effusion without any adverse effects. To the best of our […]

Midodrine, an Oral Alpha-1 Adrenoreceptor Agonist, Successfully Treated Refractory Congenital Chylous Pleural Effusion and Ascites in a Neonate Read More »

Non-immune hydrops fetalis secondary to congenital chylothorax with diffuse interstitial lung disease: a diagnostic conundrum

Alvin Jia Hao Ngeow, Mei Yoke Chan, Oon Hoe Teoh, Sarat Kumar Sanamandra, Daisy Kwai Lin ChanSingapore General Hospital. KK Women’s and Children’s Hospital. Singapore British Medical Journals Case ReportsBMJ Case Rep 2021; 14: DOI: 10.1136/bcr-2020-240688 AbstractA Chinese male infant was born at 35 weeks weighing 2935 g to a mother with polyhydramnios and prenatal hydrops

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Recurrent prenatal PIEZO1-related lymphatic dysplasia: Expanding molecular and ultrasound findings

Gioia Mastromoro, Daniele Guadagnolo, Antonella Giancotti, Maria Grazia Di Gregorio, Enrica Marchionni, Flaminia Vena, Francesca Romana Lepri, Lavinia Bargiacchi, Flavia Ventriglia, Cira Di Gioia, Antonio Novelli, Antonio PizzutiSapienza University of Rome. Ospedale San Pietro Fatebenefratelli. Bambino Gesù Children’s Hospital. University of Rome.Italy European Journal of Medical Genetics Eur J Med Genet 2021; 64: DOI: 10.1016/j.ejmg.2020.104106 AbstractGeneralized

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Thoracic Empyema Secondary to Congenital Chylothorax in a 14-Month-Old Boy with Noonan Syndrome

Takeru Oikawa, Chiharu Ota, Shinya Iwasawa, Takehiko Onoki, Hideyuki Ikeda, Takushi HanitaTohoku University Hospital.Japan Case Reports in PediatricsCase Rep Pediatr 2021; DOI: 10.1155/2021/6620353 AbstractThoracic empyema usually occurs as a complication of bacterial pneumonia, but in rare cases, it is caused by hematogenous dissemination secondary to nonpulmonary diseases. Congenital chylothorax or chylothorax in children is associated with

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Two Cases of Congenital Chylethorax: A Successful Story of Medical Management

I. Kankananarachchi, K. K. S. Priyankara, K. K. K. Lakman, K. Withanaarachchi, P. K. G. GunathilakaUniversity of Ruhuna. Teaching Hospital Karapitiya. Sri Lanka Case Reports in PediatricsCase Rep Pediatr 2021; DOI: 10.1155/2021/6634326 AbstractCongenital chylothorax (CC) is one of the most common causes of pleural effusions in neonates. Associated ipsilateral pulmonary aplasia in CC results in neonatal

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A case of refractory chylothorax treated with Eppikajutsuto

Juma Obayashi, Shigeyuki Furuta, Yukitsugu Nakamura, Kunihide Tanaka, Hiroaki KitagawaSt. Marianna University School of Medicine. Japan Pediatrics InternationalPediatr Int 2022; 64: DOI: 10.1111/ped.14707 AbstractNo Abstract Available CategoryPrimary Pulmonary Lymphatic DiseaseGenetic Factors Associated with Pulmonary Vascular DiseaseMedical Therapy. Efficacy or Lack of Efficacy Age Focus: Pediatric Pulmonary Vascular Disease Fresh or Filed Publication: Filed (PHiled). Greater than

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Staged Management of Congenital Chylothorax With Hydrops Fetalis: An Insight Into EXIT Related Procedures

Hung-Lin Tai, Tze Yee Diane Mok, An-Shine Chao, Shih-Ming Chu, Reyin LienSaint Paul’s Hospital. Chang Gung Memorial Hospital. New Taipei Municipal TuCheng Hospital. Chang Gung Medical Center and Chang Gung University.Taiwan Frontiers in PediatricsFront Pediatr 2021; DOI: 10.3389/fped.2021.633051 AbstractBackground: Idiopathic congenital chylothorax is a rare but serious disease. Advancement in perinatal care and the renovated treatment modalities

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Outcomes of neonatal chylous effusions: A 20-year west-Australian tertiary center experience

A. Anvekar, G. Athalye-Jape, H. Panchal, S. Rao, R. KohanFiona Stanley Hospital. King Edward Memorial Hospital. Perth Children Hospital.Australia LymphologyLymphology 2021; 54: 204-213DOI Not Available AbstractNeonatal chylous effusions are rare entity with limited evidence-based management. We conducted a retrospective review of neonates admitted to King Edward Memorial and Princess Margaret/Perth Children’s Hospital over 20 years

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Management of Spontaneous Chylothorax in a Neonate: A Medical Challenge

Irfan Ullah , Shahzad Rauf , Jahanzeb Malik , Kiran Shafiq Khan , Abdul Wali KhanKabir Medical College. Khyber Medical University. Rawalpindi Institute of Cardiology. Dow University of Health Sciences. College of Physician and Surgeons Pakistan. Hayatabad Medical Complex Peshawar. Pakistan CureusCureus 2021; 13: DOI: 10.7759/cureus.12942 AbstractChylothorax or collection of lymphatic fluid in the pleural space

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Use of Propranolol in the Treatment of Chylous Effusions in Infants

Kaitlin Mitchell, Angela Weiner, Patricia Ramsay, Mitali SahniPediatrix Medical Group of Nevada and University of Nevada.United States PediatricsPediatrics 2021; 148: DOI: 10.1542/peds.2020-049699 AbstractChylothorax and chyloperitoneum are rare in infants and challenging to definitively diagnose by using current criteria extrapolated from the adult population. They can be of primary or secondary etiologies, including congenital lymphatic malformations and

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