Pediatric Pulmonary Vascular Disease

An extreme case of cor triatriatum mimicking hypoplastic left heart syndrome and combined pulmonary vein stenosis

Hee Ju Hong, Hye Won Kwon, Jae Gun Kwak, Sang Yun Lee, Yoon Seong LeeSeoul National University Hospital.South Korea Cardiology in the YoungCardiol Young 2023; DOI: 10.1017/S1047951123003724 AbstractA 65-day-old girl presented to the emergency room with lethargy, requiring emergency venoarterial extracorporeal membrane oxygenation for refractory cardiogenic shock. Initially, hypoplastic left heart syndrome was suspected. However, cor […]

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Patent Ductus Arteriosus and Bronchopulmonary Dysplasia-Associated Pulmonary Hypertension: A Bayesian Meta-Analysis

Eduardo Villamor, Elkevan Westering-Kroon, Gema E. Gonzalez-Luis, František Bartoš, Steven H. Abman, Maurice J. HuizingMosaKids Children’s Hospital and Maastricht University Medical Center. Hospital Universitario Materno-Infantil de Canarias. University of Amsterdam. University of Colorado Anschutz School of Medicine and Children’s Hospital Colorado, Aurora.Netherlands, Spain and United States Journal of the American Medical Association Network OpenJAMA Netw

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In vivo hepatic flow distribution by computational fluid dynamics can predict pulmonary flow distribution in patients with Fontan circulation

Petter Frieberg, Pia Sjöberg, Erik Hedström, Marcus Carlsson, Petru LiubaLund University and Skåne University Hospital.Sweden Scientific ReportsSci Rep 2023; 13:DOI: 10.1038/s41598-023-45396-6 AbstractIn Fontan patients, a lung deprived of hepatic blood may develop pulmonary arterio-venous malformations (PAVMs) resulting in shunting, reduced pulmonary vascular resistance (PVR) and decreased oxygenation. To provide guidance for corrective invasive interventions, we aimed

In vivo hepatic flow distribution by computational fluid dynamics can predict pulmonary flow distribution in patients with Fontan circulation Read More »

Prevalence and Predictors of Hereditary Hemorrhagic Telangiectasia and Capillary-Malformation Arteriovenous Malformation Syndrome Among Children with Neurovascular Malformations

Elissa R. Engel, Katie Wusik, Philip Bright, Sudhakar Vadivelu, J. Michael Taylor, Adrienne HammelUniversity of Cincinnati College of Medicine and Cincinnati Children’s Hospital Medical Center. University of Kentucky College of Medicine.United States Journal of PediatricsJ Pediatr 2023; DOI: 10.1016/j.jpeds.2023.113761 AbstractObjective: To investigate the prevalence and predictors of hereditary hemorrhagic telangiectasia (HHT) and capillary-malformation arteriovenous malformation (CM-AVM) syndrome

Prevalence and Predictors of Hereditary Hemorrhagic Telangiectasia and Capillary-Malformation Arteriovenous Malformation Syndrome Among Children with Neurovascular Malformations Read More »

Longitudinal Assessment of Curaçao Criteria in Children with Hereditary Hemorrhagic Telangiectasia

Mordechai Pollak, Dvir Gatt, Michelle Shaw, Sheryl Hewko, Anthony Lamanna, Sara Santos, Felix RatjenHospital for Sick Children and Ruth Rappaport Children’s Hospital.Canada Journal of PediatricsJ Pediatr 2023; DOI: 10.1016/j.jpeds.2023.113665 AbstractObjective: To assess the utility of the Curaçao criteria by age over time in children with hereditary hemorrhagic telangiectasia (HHT).Study design: This was a single-center, retrospective analysis of patients

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Effective long-term sirolimus treatment in hypoxemia mainly due to intrapulmonary right-to-left shunt in a patient with multiple vascular anomalies

Jinrong Liu, Xiaomin Duan, Jie Yin, Haiming Yang, Ruxuan He, Shunying ZhaoBeijing Children’s Hospital, National Center for Children’s Health and Capital Medical University.China Orphanet Journal of Rare DiseasesOrphanet J Rare Dis 2023; 18:DOI: 10.1186/s13023-023-02732-3 AbstractPulmonary arteriovenous malformations (PAVMs), particularly where feeding artery/arteries to PAVMs ≥ 3 mm can be treated with embolization. The treatment for hypoxemia

Effective long-term sirolimus treatment in hypoxemia mainly due to intrapulmonary right-to-left shunt in a patient with multiple vascular anomalies Read More »

A Review of Serotonin in the Developing Lung and Neonatal Pulmonary Hypertension

Jamie L. Archambault, Cassidy A. DelaneyUniversity of Colorado.United States BiomedicinesBiomedicines 2023; 11: DOI: 10.3390/biomedicines11113049 AbstractSerotonin (5-HT) is a bioamine that has been implicated in the pathogenesis of pulmonary hypertension (PH). The lung serves as an important site of 5-HT synthesis, uptake, and metabolism with signaling primarily regulated by tryptophan hydroxylase (TPH), the 5-HT transporter (SERT), and

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Reassessing the role of milrinone in the treatment of heart failure and pulmonary hypertension in neonates and children: a systematic review and meta-analysis

Felipe Yu Matsushita, Vera Lúcia Jornada Krebs, Carolina Vieira de Campos, Paula Vieira de Vincenzi Gaiolla, Werther Brunow de CarvalhoUniversity of São Paulo. Hospital Samaritano. Brazil European Journal of PediatricsEur J Pediatr 2023; DOI: 10.1007/s00431-023-05342-0 AbstractTo evaluate milrinone’s impact on pediatric cardiac function, focusing on its specific role as an inotrope and lusitrope, while considering its

Reassessing the role of milrinone in the treatment of heart failure and pulmonary hypertension in neonates and children: a systematic review and meta-analysis Read More »

Right lower lung midline herniation as a rare complication in an infant with heart-lung transplantation: A case report

Dohyung Kim, Kwang Ho Choi, Hyungtae Kim, Jae Hong Lee, Younga Kim, Joung-Hee ByunPusan National University Yangsan Hospital and Pusan National University School of Medicine.Republic of Korea Pediatric TransplantationPediatr Transplant 2023; DOI: 10.1111/petr.14656 AbstractBackground: Lung herniation is a rare complication of heart-lung transplantation that can be fatal owing to vascular compromise and airway obstruction. To date, only

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Characterization of the congenital diaphragmatic hernia model in C57BL/6J fetal mice: a step toward lineage tracing experiments

Fabian Doktor, Rebeca Lopes Figueira Kasra Khalaj, Aizah Ijaz, Martin Lacher, Matisse Blundell, Lisa Antounians, Augusto ZaniThe Hospital for Sick Children and University of Toronto. University of Leipzig. Canada and Germany Pediatric Surgery InternationalPediatr Surg Int 2023; 39: DOI: 10.1007/s00383-023-05583-y AbstractPurpose: Lineage tracing is key to study the fate of individual cells and their progeny especially in

Characterization of the congenital diaphragmatic hernia model in C57BL/6J fetal mice: a step toward lineage tracing experiments Read More »

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