Pediatric Pulmonary Vascular Disease

Management of total anomalous pulmonary venous drainage in early infancy

Welton M. Gersony, Frederick O. Bowman Jr, Carl N. Steeg, Constance J. Hayes, Mary Jane Jesse, James R. MalmColumbia University College of Physicians & Surgeons and Presbyterian Hospital.United States CirculationCirculation 1971; 43: I19-I24DOI: 10.1161/01.cir.43.5s1.i-19 AbstractTen consecutive babies ranging in age from two weeks to five months, with total anomalous pulmonary venous drainage and pulmonary artery hypertension, […]

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[Budd-Chiari syndrome with hepatopulmonary syndrome: a case report and literature review]

Tian Fengyan, Dong Xiao, Hou Xiaohan, Yuan Ruyue, Pan Yuanwei, Zhang DaFirst Affiliated Hospital of Zhengzhou University. China Zhonghua Er Ke Za Zhi 2024; 62: 71-75DOI: 10.3760/cma.j.cn112140-20230828-00139 AbstractObjective: To summarize the clinical features and prognosis of Budd-Chiari syndrome with hepatopulmonary syndrome (HPS) in children. Methods: The clinical data of a child who had Budd-Chiari syndrome with HPS treated at the Department of Pediatrics of the

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Epidemiology of neonatal pneumothorax developed spontaneously and during respiratory supports in neonatal intensive care units

N. Y. Boo, E. L. Lee Ang, The Malaysian National Neonatal RegistryUniversiti Tunku Abdul Rahman. Tengku Ampuan Rahimah Hospital.Malaysia Malaysian Journal of PathologyMalays J Pathol 2023; 45: 441-456DOI: Not Available AbstractBackground: Information on incidence and risk factors associated with different types of neonatal pneumothorax were lacking globally.Objectives: To determine incidences of pneumothorax developed spontaneously and during different

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Early Echocardiographic Findings of Pulmonary Hypertension-specific Therapy in Children

Akif Kavgaci, Fatma Sedef Tunaoglu, Serdar Kula, Ayse Deniz Oguz, Semiha Terlemez, Fatma IncedereGazi University Faculty of Medicine.Turkey Medeniyet Medical JournalMedeni Med J 2023; 38: 268-275DOI: 10.4274/MMJ.galenos.2023.06706 AbstractObjective: Echocardiography is a very useful tool for the diagnosis and evaluation of pulmonary hypertension (PH). This study was planned to investigate whether echocardiographic (ECHO) data of patients with PH

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Lung Transplantation for Pulmonary Vascular Disease in Children: A United Network for Organ Sharing Analysis

Hosam F. Ahmed, Amalia Guzman-Gomez, Malika Desai, Alia Dani, David L. S. Morales, Paul J. Critser, Farhan Zafar, Don Hayes JrCincinnati Children’s Hospital Medical Center and University of Cincinnati College of Medicine. United States Pediatric CardiologyPediatr Cardiol 2023;DOI: 10.1007/s00246-023-03356-x AbstractPulmonary vascular disease (PVD) represents an important clinical indication for lung transplant (LTx) in infants, children, and

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Diffuse interstitial lung disease in a male fetus with periventricular nodular heterotopia and filamin A mosaic variant

Beatrice Desnous, Guillaume Carles, Florence Riccardi, Nathalie Stremler, Melissa Baravalle, Fedouah El-Louali, Benoit Testud, Mathieu MilhTimone Enfant, APHM. Sainte Musse Hospital. Aix-Marseille University. France Prenatal DiagnosisPrenat Diagn 2023;DOI: 10.1002/pd.6505 AbstractBackground: Most periventricular nodular heterotopias (PNHs) are associated with a mutation in the filamin A (FLNA) gene in Xq28. This condition is associated with cardiovascular malformations, connective tissue

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Current diagnosis and treatment practice for pulmonary hypertension in bronchopulmonary dysplasia-A survey study in Germany (PUsH BPD)

Friederike Häfner, Caroline Johansson, Larissa Schwarzkopf, Kai Förster, Yvonne Kraus, Andreas W. Flemmer, Georg Hansmann, Hannes Sallmon, Ursula Felderhoff‐Müser, Sabine Witt, Lars Schwettmann, Anne HilgendorffHelmholtz Munich. Dr. von Hauner Children’s Hospital and LMU University Hospital. IFT Institute für Therapieforschung Centre for Mental Health and Addiction Research. Hannover Medical School. Medical University of Graz. University Hospital

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Surgical outcomes of common arterial trunk repair beyond infancy

Chinnaswamy Reddy, Ameya Kaskar, Govardhan Reddy, Niranjan Soundararajan, S. Satheesh, Viralam S. Kiran, Pujar Venkateshauarya SureshNarayana Health. India Indian Journal of Thoracic and Cardiovascular SurgeryIndian J Thorac Cardiovasc Surg 2024; 40: 9-16DOI: 10.1007/s12055-023-01549-w AbstractBackground: The aim of this study is to analyze the clinical outcomes of common arterial trunk repair beyond infancy in terms of both early-

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Factors associated with the response to postnatal dexamethasone use in very low birthweight infants: a nationwide cohort study

Seung Hwan Baek, Jeong Eun Shin, Jungho Han, In Gyu Song, Joonsik Park, Su Min Lee, Sungbo Shim, Ho Seon Eun, Soon Min Lee, Joohee Lim, So Jin Yoon, Wook Chang, Min Soo ParkSeverance Hospital. Gangnam Severance Hospital. Yongin Severance Hospital. Republic of Korea British Medical Journal Paediatrics OpenBMJ Paediatr Open 2023;DOI: 10.1136/bmjpo-2023-002302 AbstractBackground: Dexamethasone is widely

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LRP4 site-specific variants in the third β-propeller domain causes congenital myasthenic syndrome type 17

Tariq Al Jabry, Nadia Al-Hashmi, Basem Abdelhadi, Almundher Al-MaawaliSultan Qaboos University Hospital. Royal Hospital.Oman European Journal of Medical GeneticsEir J Med Genet 2023;DOI: 10.1016/j.ejmg.2023.104903 AbstractLRP4 is expressed in many organs. It mediates SOST-dependent inhibition of bone formation and acts as an inhibitor of WNT signaling. It is also a postsynaptic end plate cell surface receptor at

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