Pediatric Pulmonary Vascular Disease or Adult Pulmonary Vascular Disease

Bioinformatic Analysis and Molecular Docking Identify Isorhamnetin Is a Candidate Compound in the Treatment of Pulmonary Artery Hypertension

Chen Shao, Wei Xia, Yang LiuSecond People’s Hospital of Lianyungang. Qilu Medical University. China Anatolgy Journal of CardiologyAnatol J Cardiol 2024;DOI: 10.14744/AnatolJCardiol.2024.4723 AbstractBackground: The current study aims to identify the key pathways and potential therapeutic targets for pulmonary arterial hypertension (PAH) and to further evaluate the anti-PAH effects of isorhamnetin.Methods: The dataset of gene expression profiling for PAH […]

Bioinformatic Analysis and Molecular Docking Identify Isorhamnetin Is a Candidate Compound in the Treatment of Pulmonary Artery Hypertension Read More »

Case report: A finding of PVOD and PAH in first degree relatives suggests shared heritable risk and overlapping features of both pulmonary vascular diseases

Roger Winters, Lindsay M. Forbes, Dunbar Ivy, Carlyne Cool, Bryan D. Park, Peter Hountras, David Badesch, Sue Gu, Edda Spiekerkoetter, Roham Zamanian, Stacey Leier Gluck, Todd M. BullUniversity of Colorado and University of Colorado Children’s Hospital. Stanford University.United States Respirology Case ReportsRespirol Case Rep 2024; 12: DOI: 10.1002/rcr2.70064 AbstractPulmonary veno-occlusive disease (PVOD) is a rare form

Case report: A finding of PVOD and PAH in first degree relatives suggests shared heritable risk and overlapping features of both pulmonary vascular diseases Read More »

Brain and lung arteriovenous malformation rescreening practices for children and adults with hereditary hemorrhagic telangiectasia

Lauren A. Beslow, Helen Kim, Steven W. Hetts, Felix Ratjen, Marianne S. Clancy, James R. Gossage, Marie E. FaughnanChildren’s Hospital of Philadelphia and Perelman School of Medicine at the University of Pennsylvania. University of California San Francisco. Hospital for Sick Children and University of Toronto. Cure HHT Foundation. Augusta University. St. Michael’s Hospital.United States and

Brain and lung arteriovenous malformation rescreening practices for children and adults with hereditary hemorrhagic telangiectasia Read More »

Trends and patterns in pulmonary arterial hypertension-associated hospital admissions among methamphetamine users: a decade-long study

Amanda Husein, Jolie Boullion, Ismail Hossain, Diensn Xing, Tareq Ferdous Khan, Shenuarin Bhuiyan, Gopi K. Kolluru, Mostafizur Rahman Bhuiyan, Nicholas E. Goeders, Steven A. Conrad, John A. Vanchiere A. Wayne Orr, Christopher G. Kevil, Mohammad Alfrad Nobel BhuiyanLouisiana State University Health Sciences Center at Shreveport. Cleveland State University. Bangabandhu Sheikh Mujib Medical University. United States

Trends and patterns in pulmonary arterial hypertension-associated hospital admissions among methamphetamine users: a decade-long study Read More »

Increased BMP-Responsive Transcription Factors in Distinct Endothelial and Mesenchymal Cells in PAH

Abam Michael Andruska, Rodrigo Cantu Valadez, Kenzo Ichimura, Pauline Chu, Tianyi Zhang, Katharina Schimmel, Lingli Wang, Aiqin Cao, Michaela A. Aldred, Edda SpiekerkoetterStanford University. University of California Berkeley. Indiana University School of Medicine.United States American Journal of Respiratory and Critical MedicineAm J Respir Crit Care Med 2024; DOI: 10.1164/rccm.202405-1039LE AbstractAbstract Not Available CategoryVascular Cell Biology and

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Mitral Valve Intervention, Pulmonary Hypertension, and Survival in 219 Shone’s Syndrome Patients

Dominique L. Tucker, Sohini Gupta, Amol Pande, Rashed Mahboubi, Miza Salim Hammoud, Munir Ahmad, Hani Najm, Tara Karamlou, Shone’s Syndrome Working GroupCleveland Clinic, Cleveland and Case Western Reserve University School of Medicine. United States Annals of Thoracic SurgeryAnn Thorac Surg 2024; DOI: 10.1016/j.athoracsur.2023.10.023 AbstractBackground: Relationships between pulmonary hypertension (PHTN), mitral valve intervention (MVI), and death among patients

Mitral Valve Intervention, Pulmonary Hypertension, and Survival in 219 Shone’s Syndrome Patients Read More »

A novel frameshift TBX4 variant in a family with ischio-coxo-podo-patellar syndrome and variable severity

Giada Moresco, Ornella Rondinone, Alessia Mauri, Rita Gorgoglione, Daniela Maria Grazia Graziani, Michal Dziuback, Monica Rosa Miozzo, Silvia Maria Sirchia, Luca Pietrogrande, Angela Peron, Laura FontanaUniversità degli Studi di Milano/University of Milan. ondazione IRCCS Ca Granda Ospedale Maggiore Policlinico. ASST Santi Paolo e Carlo. Meyer Children’s Hospital IRCCS. Università degli Studi di Firenze.Italy Genes and

A novel frameshift TBX4 variant in a family with ischio-coxo-podo-patellar syndrome and variable severity Read More »

Panorama of artery endothelial cell dysfunction in pulmonary arterial hypertension

Ying-Huizi Shen, Dong Ding, Tian-Yu Lian, Bao-Chen Qui, Yi Yan, Pei-Wen Wang, Wei-Hua Zhang, Zhi-Cheng JingFirst Hospital of Jilin University. Union Medical College Hospital, Chinese Academy of Medical Sciences and Peking Union Medical College. Guangdong Provincial People’s Hospital and Guangdong Academy of Medical Sciences, Southern Medical University. Shanghai Children’s Medical Center, National Children’s Medical Center

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Arterial-Lymphatic-Like Endothelial Cells Appear in Hereditary Hemorrhagic Telangiectasia 2 and Contribute to Vascular Leakage and Arteriovenous Malformations

Yang Yang, Xiuju Wu, Yan Zhao, Daoqin Zhang, Li Zhang, Xinjiang Cai, Jaden Ji, Zheng Jing, Kristina I. Boström, Yucheng YaoDavid Geffen School of Medicine and University of California. Stanford University.United States CirculationCirculation 2024; DOI: 10.1161/CIRCULATIONAHA.124.070925 AbstractBackground: Arteriovenous malformations (AVMs) are characteristic of hereditary hemorrhagic telangiectasia. Loss-of-function mutations in the activin receptor-like kinase 1 (Alk1) are linked

Arterial-Lymphatic-Like Endothelial Cells Appear in Hereditary Hemorrhagic Telangiectasia 2 and Contribute to Vascular Leakage and Arteriovenous Malformations Read More »

Survival, morbidity, and quality of life in pulmonary arterial hypertension patients: a systematic review of outcomes reported by population-based observational studies

Stefan Reinders, Eva‑Maria Didden, Rose OngActelion Pharmaceuticals and Johnson and Johnson.Peru and Switzerland Respiratory ResearchRespir Res 2024; 25: DOI: 10.1186/s12931-024-02994-w AbstractBackground: Comprehensive summaries on real-world outcomes in pulmonary arterial hypertension (PAH)-a rare, incurable condition, are lacking. We conducted a systematic literature review to describe current survival, morbidity, and quality of life (QoL) outcomes in adult and pediatric

Survival, morbidity, and quality of life in pulmonary arterial hypertension patients: a systematic review of outcomes reported by population-based observational studies Read More »

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