Pediatric Pulmonary Vascular Disease or Adult Pulmonary Vascular Disease

Contemporary treatment of right ventricular failure

Bibhuti B. Das, Shashi RajUniversity of Mississippi Medical Center. Narayana Health.United States and India Journal of Heart and Lung Transplantation OpenJHLT Open 2025; 7: DOI: 10.1016/j.jhlto.2024.100203 AbstractRight ventricular failure (RVF) is a clinical syndrome resulting from structural and functional changes in the right ventricle (RV), leading to inadequate blood flow to the pulmonary circulation and elevated

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High Altitude May Protect Against the Early Development of Irreversible Pulmonary Hypertension in Patients With Congenital Heart Disease

Inge von Alvensleben, Brian B. Graham, Gustavo A. Balanza, Carlos Brockmann, Ericka C. Pérez, Ximena Y. Vicente, Carla Arteaga, Claudia Scherer, Franz P. Freudenthal, Rubin M. Tuder, Alexandra HeathKardiozentrum. University of Colorado. University of California San Francisco. Massachusetts General Hospital and Harvard Medical School. Hospital Belga.Bolivia and United States Pulmonary CirculationPulm Circ 2025; 15: DOI: 10.1002/pul2.70049

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Familial Alveolar Capillary Dysplasia With Misalignment of Pulmonary Veins Caused by Paternal FOXF1 Upstream Enhancer Deletion: A Case Report

Hidenori Kawasaki, Kazuhiko Nakabayashi, Masahiko Ikeda, Tetsuo Onda, Seiichi Tomotaki, Masako Torishima, Akiko Saito, Hirofumi Ohashi, Sachiko Minamiguchi, Kenichiro Hata, Masahiro Hayakawa, Masahiko Kawai, Kazutoshi Cho, Shinji Kosugi, akahiro YamadaKyoto University School of Public Health, Kyoto University Hospital and Kyoto University. National Center for Child Health and Development. Hokkaido University Hospital. Nagoya University Hospital. Saitama

Familial Alveolar Capillary Dysplasia With Misalignment of Pulmonary Veins Caused by Paternal FOXF1 Upstream Enhancer Deletion: A Case Report Read More »

Differences in Pulmonary Artery Stiffness Measured by CMR in Preterm-Born Young Adults With and Without Bronchopulmonary Dysplasia

Wouter J. van Genuchten, Jarno J. Steenhorst, Gabrielle M. J. W. van Tussenbroek, Nikki van der Velde, Lieke S. Kamphuis, Irwin K. M. Reiss, Daphne Merkus, Willem A. Helbing, Alexander HirschErasmus MC. University Hospital Munich.Netherlands and Germany Circulation Cardiovascular ImagingCirc Cardiovasc Imaging 2025; DOI: 10.1161/CIRCIMAGING.124.017791 AbstractBackground: Very preterm-born infants are at risk for developing bronchopulmonary dysplasia (BPD), a chronic lung disease. Nowadays, the majority of these infants reach adulthood.

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Surgical resection of diffuse pulmonary arteriovenous malformations (PAVMs)

Aden R. Falk, Lindsay J. Nitsche, Colleen E. Bontrager, Sarah Bond, Lauren A. Beslow, Alexandra J. Borst, Jennifer Pogoriler, Paul J. Devlin, Elizabeth Goldmuntz, Sunil Singhal, Scott O. Trerotola, Stephanie M. FullerChildren’s Hospital of Philadelphia and Perelman School of Medicine at the University of Pennsylvania. University of North Carolina. United States Journal of Thoracic and

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Reverse Potts shunt in severe pulmonary hypertension: A 20-year retrospective review

Wei Jiang, Zhongshi Wu, Can Huang, Ting Lu, Haoyong Yuan, Yuhong Liu, Tao QianSecond Xiangya Hospital of Central South University.China International Journal of CardiologyInt J Cardiol 2025; DOI: 10.1016/j.ijcard.2025.133129 AbstractPulmonary arterial hypertension (PAH) is a multifactorial heterogeneous condition characterized by elevated pulmonary artery pressure, leading to increased right ventricular afterload and ultimately resulting in right heart

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Successful control of recurrent MAS by canakinumab in a Sjogren syndrome patient with homozygous MEFV P369S variants, and review of literatures

Noboyuki Ono, Motoki Yoshimura, Toshiya Nishida, Yusuke Yamauchi, Goro Doi, Yoko Fuyuno, Motoshi Sonoda, Hiroaki NiiroFukuoka City Hospital, Kyushu University Hospital, Beppu Hospital, and Kyushu University. Iizuka Hospital. Japan Modern Rheumatology Case ReportsMod Rheumatol Case Rep 2025; DOI: 10.1093/mrcr/rxaf016 AbstractMacrophage activation syndrome (MAS) is an autoinflammatory condition, which severely complicates autoimmune diseases, such as SJIA, AOSD

Successful control of recurrent MAS by canakinumab in a Sjogren syndrome patient with homozygous MEFV P369S variants, and review of literatures Read More »

Long-term survival of shunt closure in atrial septal defects with pulmonary arterial hypertension

Wenjie Chen, Jingyuan Chen, Min Peng, Jun Luo, Haihua Qiu, Yusi Chen, Jiang LiSecond Xiangya Hospital of Central South University. China International Journal of CardiologyInt J Cardiol 2025; DOI: 10.1016/j.ijcard.2025.133094 AbstractObjective: This study aims to refine closure indications and assess long-term outcomes in pulmonary arterial hypertension associated with atrial septal defect (PAH-ASD).Methods: We enrolled 197 PAH-ASD patients classified

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Genetic Variants and Clinical Features of Patients With Glycogen Storage Disease Type Ib

Yu Xia, Yu Sun, Taozi Du, Chengkai Sun, Ying Xu, Wensong Ge, Lili Liang, Ruifang Wang, Manqing Sun, Bing Xiao, Wenjuan QiuXinhua Hospital, Ruijin Hospital and Shanghai Jiao Tong University. China Journal of the American Medical Association Network OpenJAMA Netw Open 2025; 8: DOI: 10.1001/jamanetworkopen.2024.61888 AbstractImportance: Glycogen storage disease type Ib (GSDIb) is a rare metabolic disorder

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Growing Up with Developmental Lung Diseases: A Review for the Adult Pulmonologist

Yadira Rivera-Sanchez, Zachary W. Blair, Tyler J. Wall, Kara N. GossUniversity of Texas Southwestern Medical Center.United States ChestChest 2025; DOI: 10.1016/j.chest.2025.02.014 AbstractTopic importance: Improved childhood management strategies have decreased the early life morbidity and mortality of severe developmental lung disorders, such that an increasing number of individuals ultimately transition care to adult pulmonologists for management. Alternatively, individuals

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